Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and α-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease
- Author
- GÖRTZ, Philipp1 ; KOLLER, Hubertus1 ; SCHWAHN, Bernd2 ; WENDEL, Udo2 ; SIEBLER, Mario1
[1] Department of Neurology, Heinrich-Heine-University, Düsseldorf, Germany
[2] Department of Pediatrics, Heinrich-Heine-University, Düsseldorf, Germany - Source
Pediatric research. 2003, Vol 53, Num 2, pp 320-324, 5 p ; ref : 20 ref
- CODEN
- PEREBL
- ISSN
- 0031-3998
- Scientific domain
- Genetics; Pediatrics
- Publisher
- Lippincott Williams & Wilkins, Hagerstown, MD
- Publication country
- United States
- Document type
- Article
- Language
- English
- Keyword (fr)
- Activité biologique Aminoacide Animal Concentration Culture cellulaire Dépolarisation Encéphalopathie Enzymopathie GABA In vitro Leucine Leucinose Neurone Pathogénie Physiopathologie Potentiel action Rat Ratio Synapse Aminoacidopathie Maladie héréditaire Mammalia Métabolisme pathologie Neurotransmetteur Rodentia Système nerveux pathologie Vertebrata
- Keyword (en)
- Biological activity Aminoacid Animal Concentration Cell culture Depolarization Encephalopathy Enzymopathy GABA In vitro Leucine Leucinosis Neuron Pathogenesis Pathophysiology Action potential Rat Ratio Synapse Aminoacid disorder Genetic disease Mammalia Metabolic diseases Neurotransmitter Rodentia Nervous system diseases Vertebrata
- Keyword (es)
- Actividad biológica Aminoácido Animal Concentración Cultivo celular Despolarización Encefalopatía Enzimopatía GABA In vitro Leucina Leucinosis Neurona Patogenia Fisiopatología Potencial acción Rata Ratio Sinapsis Aminoacido alteración Enfermedad hereditaria Mammalia Metabolismo patología Neurotransmisor Rodentia Sistema nervioso patología Vertebrata
- Classification
- Pascal
- 002 Biological and medical sciences / 002B Medical sciences / 002B22 Metabolic diseases / 002B22D Errors of metabolism / 002B22D01 Aminoacid disorders
- Discipline
- Metabolic diseases
- Origin
- Inist-CNRS
- Database
- PASCAL
- INIST identifier
- 14497664
Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS
Access to the document
Install on your browser
DOI
10.1203/01.PDR.0000047521.50656.16 
https://dx.doi.org/10.1203/01.PDR.0000047521.50656.16
"O:13:\"PanistOpenUrl\":36:{s:10:\"\u0000*\u0000openUrl\";N;s:6:\"\u0000*\u0000idc\";N;s:6:\"\u0000*\u0000fmt\";s:7:\"journal\";s:6:\"\u0000*\u0000doi\";s:34:\"10.1203\/01.PDR.0000047521.50656.16\";s:6:\"\u0000*\u0000pii\";s:0:\"\";s:7:\"\u0000*\u0000pmid\";s:0:\"\";s:9:\"\u0000*\u0000atitle\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:9:\"\u0000*\u0000jtitle\";s:18:\"Pediatric research\";s:9:\"\u0000*\u0000stitle\";s:12:\"Pediatr. res\";s:7:\"\u0000*\u0000date\";s:4:\"2003\";s:9:\"\u0000*\u0000volume\";s:2:\"53\";s:8:\"\u0000*\u0000issue\";s:1:\"2\";s:8:\"\u0000*\u0000spage\";s:3:\"320\";s:8:\"\u0000*\u0000epage\";s:3:\"324\";s:8:\"\u0000*\u0000pages\";s:0:\"\";s:7:\"\u0000*\u0000issn\";s:9:\"0031-3998\";s:8:\"\u0000*\u0000eissn\";s:0:\"\";s:9:\"\u0000*\u0000aulast\";s:6:\"G\u00d6RTZ\";s:10:\"\u0000*\u0000aufirst\";s:7:\"Philipp\";s:9:\"\u0000*\u0000auinit\";s:0:\"\";s:10:\"\u0000*\u0000auinitm\";s:0:\"\";s:5:\"\u0000*\u0000au\";a:4:{i:0;s:16:\"KOLLER, Hubertus\";i:1;s:14:\"SCHWAHN, Bernd\";i:2;s:11:\"WENDEL, Udo\";i:3;s:14:\"SIEBLER, Mario\";}s:9:\"\u0000*\u0000aucorp\";s:0:\"\";s:7:\"\u0000*\u0000isbn\";s:0:\"\";s:8:\"\u0000*\u0000coden\";s:6:\"PEREBL\";s:8:\"\u0000*\u0000genre\";s:7:\"article\";s:7:\"\u0000*\u0000part\";s:0:\"\";s:9:\"\u0000*\u0000btitle\";s:0:\"\";s:8:\"\u0000*\u0000title\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:8:\"\u0000*\u0000place\";s:14:\"Hagerstown, MD\";s:6:\"\u0000*\u0000pub\";s:29:\"Lippincott Williams & Wilkins\";s:10:\"\u0000*\u0000edition\";s:0:\"\";s:9:\"\u0000*\u0000tpages\";s:1:\"5\";s:9:\"\u0000*\u0000series\";s:0:\"\";s:8:\"\u0000*\u0000proxy\";s:30:\"http:\/\/proxyout.inist.fr:8080\/\";s:12:\"\u0000*\u0000integrite\";b:1;}"
Panist access
"O:12:\"IstexOpenUrl\":35:{s:10:\"\u0000*\u0000openUrl\";N;s:6:\"\u0000*\u0000fmt\";s:7:\"journal\";s:6:\"\u0000*\u0000doi\";s:34:\"10.1203\/01.PDR.0000047521.50656.16\";s:6:\"\u0000*\u0000pii\";s:0:\"\";s:7:\"\u0000*\u0000pmid\";s:0:\"\";s:9:\"\u0000*\u0000atitle\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:9:\"\u0000*\u0000jtitle\";s:18:\"Pediatric research\";s:9:\"\u0000*\u0000stitle\";s:12:\"Pediatr. res\";s:7:\"\u0000*\u0000date\";s:4:\"2003\";s:9:\"\u0000*\u0000volume\";s:2:\"53\";s:8:\"\u0000*\u0000issue\";s:1:\"2\";s:8:\"\u0000*\u0000spage\";s:3:\"320\";s:8:\"\u0000*\u0000epage\";s:3:\"324\";s:8:\"\u0000*\u0000pages\";s:0:\"\";s:7:\"\u0000*\u0000issn\";s:9:\"0031-3998\";s:8:\"\u0000*\u0000eissn\";s:0:\"\";s:9:\"\u0000*\u0000aulast\";s:6:\"G\u00d6RTZ\";s:10:\"\u0000*\u0000aufirst\";s:7:\"Philipp\";s:9:\"\u0000*\u0000auinit\";s:0:\"\";s:10:\"\u0000*\u0000auinitm\";s:0:\"\";s:5:\"\u0000*\u0000au\";a:4:{i:0;s:16:\"KOLLER, Hubertus\";i:1;s:14:\"SCHWAHN, Bernd\";i:2;s:11:\"WENDEL, Udo\";i:3;s:14:\"SIEBLER, Mario\";}s:9:\"\u0000*\u0000aucorp\";s:0:\"\";s:7:\"\u0000*\u0000isbn\";s:0:\"\";s:8:\"\u0000*\u0000coden\";s:6:\"PEREBL\";s:8:\"\u0000*\u0000genre\";s:7:\"article\";s:7:\"\u0000*\u0000part\";s:0:\"\";s:9:\"\u0000*\u0000btitle\";s:0:\"\";s:8:\"\u0000*\u0000title\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:8:\"\u0000*\u0000place\";s:14:\"Hagerstown, MD\";s:6:\"\u0000*\u0000pub\";s:29:\"Lippincott Williams & Wilkins\";s:10:\"\u0000*\u0000edition\";s:0:\"\";s:9:\"\u0000*\u0000tpages\";s:1:\"5\";s:9:\"\u0000*\u0000series\";s:0:\"\";s:8:\"\u0000*\u0000proxy\";s:30:\"http:\/\/proxyout.inist.fr:8080\/\";s:12:\"\u0000*\u0000integrite\";b:1;}"
Istex access
"O:16:\"UnpaywallOpenUrl\":35:{s:8:\"\u0000*\u0000email\";s:27:\"assistance-portail@inist.fr\";s:6:\"\u0000*\u0000fmt\";N;s:6:\"\u0000*\u0000doi\";s:34:\"10.1203\/01.PDR.0000047521.50656.16\";s:6:\"\u0000*\u0000pii\";N;s:7:\"\u0000*\u0000pmid\";N;s:9:\"\u0000*\u0000atitle\";N;s:9:\"\u0000*\u0000jtitle\";N;s:9:\"\u0000*\u0000stitle\";N;s:7:\"\u0000*\u0000date\";N;s:9:\"\u0000*\u0000volume\";N;s:8:\"\u0000*\u0000issue\";N;s:8:\"\u0000*\u0000spage\";N;s:8:\"\u0000*\u0000epage\";N;s:8:\"\u0000*\u0000pages\";N;s:7:\"\u0000*\u0000issn\";N;s:8:\"\u0000*\u0000eissn\";N;s:9:\"\u0000*\u0000aulast\";N;s:10:\"\u0000*\u0000aufirst\";N;s:9:\"\u0000*\u0000auinit\";N;s:10:\"\u0000*\u0000auinitm\";N;s:5:\"\u0000*\u0000au\";N;s:9:\"\u0000*\u0000aucorp\";N;s:7:\"\u0000*\u0000isbn\";N;s:8:\"\u0000*\u0000coden\";N;s:8:\"\u0000*\u0000genre\";N;s:7:\"\u0000*\u0000part\";N;s:9:\"\u0000*\u0000btitle\";N;s:8:\"\u0000*\u0000title\";N;s:8:\"\u0000*\u0000place\";N;s:6:\"\u0000*\u0000pub\";N;s:10:\"\u0000*\u0000edition\";N;s:9:\"\u0000*\u0000tpages\";N;s:9:\"\u0000*\u0000series\";N;s:8:\"\u0000*\u0000proxy\";s:30:\"http:\/\/proxyout.inist.fr:8080\/\";s:12:\"\u0000*\u0000integrite\";N;}"
Unpaywall access
"O:16:\"EuropePMCOpenUrl\":35:{s:10:\"\u0000*\u0000openUrl\";N;s:6:\"\u0000*\u0000fmt\";s:7:\"journal\";s:6:\"\u0000*\u0000doi\";s:34:\"10.1203\/01.PDR.0000047521.50656.16\";s:6:\"\u0000*\u0000pii\";s:0:\"\";s:7:\"\u0000*\u0000pmid\";s:0:\"\";s:9:\"\u0000*\u0000atitle\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:9:\"\u0000*\u0000jtitle\";s:18:\"Pediatric research\";s:9:\"\u0000*\u0000stitle\";s:12:\"Pediatr. res\";s:7:\"\u0000*\u0000date\";s:4:\"2003\";s:9:\"\u0000*\u0000volume\";s:2:\"53\";s:8:\"\u0000*\u0000issue\";s:1:\"2\";s:8:\"\u0000*\u0000spage\";s:3:\"320\";s:8:\"\u0000*\u0000epage\";s:3:\"324\";s:8:\"\u0000*\u0000pages\";s:0:\"\";s:7:\"\u0000*\u0000issn\";s:9:\"0031-3998\";s:8:\"\u0000*\u0000eissn\";s:0:\"\";s:9:\"\u0000*\u0000aulast\";s:6:\"G\u00d6RTZ\";s:10:\"\u0000*\u0000aufirst\";s:7:\"Philipp\";s:9:\"\u0000*\u0000auinit\";s:0:\"\";s:10:\"\u0000*\u0000auinitm\";s:0:\"\";s:5:\"\u0000*\u0000au\";a:4:{i:0;s:16:\"KOLLER, Hubertus\";i:1;s:14:\"SCHWAHN, Bernd\";i:2;s:11:\"WENDEL, Udo\";i:3;s:14:\"SIEBLER, Mario\";}s:9:\"\u0000*\u0000aucorp\";s:0:\"\";s:7:\"\u0000*\u0000isbn\";s:0:\"\";s:8:\"\u0000*\u0000coden\";s:6:\"PEREBL\";s:8:\"\u0000*\u0000genre\";s:7:\"article\";s:7:\"\u0000*\u0000part\";s:0:\"\";s:9:\"\u0000*\u0000btitle\";s:0:\"\";s:8:\"\u0000*\u0000title\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:8:\"\u0000*\u0000place\";s:14:\"Hagerstown, MD\";s:6:\"\u0000*\u0000pub\";s:29:\"Lippincott Williams & Wilkins\";s:10:\"\u0000*\u0000edition\";s:0:\"\";s:9:\"\u0000*\u0000tpages\";s:1:\"5\";s:9:\"\u0000*\u0000series\";s:0:\"\";s:8:\"\u0000*\u0000proxy\";s:30:\"http:\/\/proxyout.inist.fr:8080\/\";s:12:\"\u0000*\u0000integrite\";b:1;}"
Europe PubMed Central access
"O:11:\"BaseOpenUrl\":35:{s:10:\"\u0000*\u0000openUrl\";N;s:6:\"\u0000*\u0000fmt\";s:7:\"journal\";s:6:\"\u0000*\u0000doi\";s:34:\"10.1203\/01.PDR.0000047521.50656.16\";s:6:\"\u0000*\u0000pii\";s:0:\"\";s:7:\"\u0000*\u0000pmid\";s:0:\"\";s:9:\"\u0000*\u0000atitle\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:9:\"\u0000*\u0000jtitle\";s:18:\"Pediatric research\";s:9:\"\u0000*\u0000stitle\";s:12:\"Pediatr. res\";s:7:\"\u0000*\u0000date\";s:4:\"2003\";s:9:\"\u0000*\u0000volume\";s:2:\"53\";s:8:\"\u0000*\u0000issue\";s:1:\"2\";s:8:\"\u0000*\u0000spage\";s:3:\"320\";s:8:\"\u0000*\u0000epage\";s:3:\"324\";s:8:\"\u0000*\u0000pages\";s:0:\"\";s:7:\"\u0000*\u0000issn\";s:9:\"0031-3998\";s:8:\"\u0000*\u0000eissn\";s:0:\"\";s:9:\"\u0000*\u0000aulast\";s:6:\"G\u00d6RTZ\";s:10:\"\u0000*\u0000aufirst\";s:7:\"Philipp\";s:9:\"\u0000*\u0000auinit\";s:0:\"\";s:10:\"\u0000*\u0000auinitm\";s:0:\"\";s:5:\"\u0000*\u0000au\";a:4:{i:0;s:16:\"KOLLER, Hubertus\";i:1;s:14:\"SCHWAHN, Bernd\";i:2;s:11:\"WENDEL, Udo\";i:3;s:14:\"SIEBLER, Mario\";}s:9:\"\u0000*\u0000aucorp\";s:0:\"\";s:7:\"\u0000*\u0000isbn\";s:0:\"\";s:8:\"\u0000*\u0000coden\";s:6:\"PEREBL\";s:8:\"\u0000*\u0000genre\";s:7:\"article\";s:7:\"\u0000*\u0000part\";s:0:\"\";s:9:\"\u0000*\u0000btitle\";s:0:\"\";s:8:\"\u0000*\u0000title\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:8:\"\u0000*\u0000place\";s:14:\"Hagerstown, MD\";s:6:\"\u0000*\u0000pub\";s:29:\"Lippincott Williams & Wilkins\";s:10:\"\u0000*\u0000edition\";s:0:\"\";s:9:\"\u0000*\u0000tpages\";s:1:\"5\";s:9:\"\u0000*\u0000series\";s:0:\"\";s:8:\"\u0000*\u0000proxy\";s:30:\"http:\/\/proxyout.inist.fr:8080\/\";s:12:\"\u0000*\u0000integrite\";b:1;}"
Base Search access
"O:12:\"ArXivOpenUrl\":35:{s:10:\"\u0000*\u0000openUrl\";N;s:6:\"\u0000*\u0000fmt\";s:7:\"journal\";s:6:\"\u0000*\u0000doi\";s:34:\"10.1203\/01.PDR.0000047521.50656.16\";s:6:\"\u0000*\u0000pii\";s:0:\"\";s:7:\"\u0000*\u0000pmid\";s:0:\"\";s:9:\"\u0000*\u0000atitle\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:9:\"\u0000*\u0000jtitle\";s:18:\"Pediatric research\";s:9:\"\u0000*\u0000stitle\";s:12:\"Pediatr. res\";s:7:\"\u0000*\u0000date\";s:4:\"2003\";s:9:\"\u0000*\u0000volume\";s:2:\"53\";s:8:\"\u0000*\u0000issue\";s:1:\"2\";s:8:\"\u0000*\u0000spage\";s:3:\"320\";s:8:\"\u0000*\u0000epage\";s:3:\"324\";s:8:\"\u0000*\u0000pages\";s:0:\"\";s:7:\"\u0000*\u0000issn\";s:9:\"0031-3998\";s:8:\"\u0000*\u0000eissn\";s:0:\"\";s:9:\"\u0000*\u0000aulast\";s:6:\"G\u00d6RTZ\";s:10:\"\u0000*\u0000aufirst\";s:7:\"Philipp\";s:9:\"\u0000*\u0000auinit\";s:0:\"\";s:10:\"\u0000*\u0000auinitm\";s:0:\"\";s:5:\"\u0000*\u0000au\";a:4:{i:0;s:16:\"KOLLER, Hubertus\";i:1;s:14:\"SCHWAHN, Bernd\";i:2;s:11:\"WENDEL, Udo\";i:3;s:14:\"SIEBLER, Mario\";}s:9:\"\u0000*\u0000aucorp\";s:0:\"\";s:7:\"\u0000*\u0000isbn\";s:0:\"\";s:8:\"\u0000*\u0000coden\";s:6:\"PEREBL\";s:8:\"\u0000*\u0000genre\";s:7:\"article\";s:7:\"\u0000*\u0000part\";s:0:\"\";s:9:\"\u0000*\u0000btitle\";s:0:\"\";s:8:\"\u0000*\u0000title\";s:189:\"Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and \u03b1-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease\";s:8:\"\u0000*\u0000place\";s:14:\"Hagerstown, MD\";s:6:\"\u0000*\u0000pub\";s:29:\"Lippincott Williams & Wilkins\";s:10:\"\u0000*\u0000edition\";s:0:\"\";s:9:\"\u0000*\u0000tpages\";s:1:\"5\";s:9:\"\u0000*\u0000series\";s:0:\"\";s:8:\"\u0000*\u0000proxy\";s:30:\"http:\/\/proxyout.inist.fr:8080\/\";s:12:\"\u0000*\u0000integrite\";b:1;}"
arXiv access
