Effects of enzyme replacement therapy on the cardiomyopathy of Anderson-Fabry disease : a randomised, double-blind, placebo-controlled clinical trial of agalsidase alfa
- Author
- HUGHES, D. A1 ; ELLIOTT, P. M2 ; SHAH, J2 ; ZUCKERMAN, J3 ; COGHLAN, G4 ; BROOKES, J5 ; MEHTA, A. B1
[1] Department of Haematology, Royal Free Hospital and University College Medical School, London, United Kingdom
[2] The Heart Hospital, London, United Kingdom
[3] Clinical Trials Centre, Royal Free Hospital and University College Medical School, London, United Kingdom
[4] Department of Cardiology, Royal Free Hospital and University College Medical School, London, United Kingdom
[5] Cardiovascular Magnetic Resonance Unit, The Middlesex Hospital, London, United Kingdom - Source
Heart (London 1996). 2008, Vol 94, Num 2, pp 153-158, 6 p ; ref : 17 ref
- ISSN
- 1355-6037
- Scientific domain
- Cardiology, blood circulation, phlebology
- Publisher
- BMJ, London
- Publication country
- United Kingdom
- Document type
- Article
- Language
- English
- Keyword (fr)
- Agalsidase alfa Appareil circulatoire Cardiologie Cardiomyopathie Enzyme Etude double insu Lipide Sphingolipidose héréditaire de Fabry Traitement substitutif Cardiopathie Enzymopathie Lipoïdose Maladie héréditaire Maladie métabolique Pathologie de l'appareil circulatoire Pathologie des vaisseaux sanguins Pathologie du myocarde Pathologie du système nerveux
- Keyword (en)
- Agalsidase alfa Circulatory system Cardiology Cardiomyopathy Enzyme Double blind study Lipids Fabry disease Replacement therapy Heart disease Enzymopathy Lipoidosis Genetic disease Metabolic diseases Cardiovascular disease Vascular disease Myocardial disease Nervous system diseases
- Keyword (es)
- Agalsidasa alfa Aparato circulatorio Cardiología Cardiomiopatía Enzima Estudio doble ciego Lípido Esfingolipidosis hereditaria Fabry Tratamiento sustitutivo Cardiopatía Enzimopatía Lipoidosis Enfermedad hereditaria Metabolismo patología Aparato circulatorio patología Vaso sanguíneo patología Miocardio patología Sistema nervioso patología
- Classification
- Pascal
- 002 Biological and medical sciences / 002B Medical sciences / 002B12 Cardiology. Vascular system / 002B12A Heart / 002B12A05 Myocarditis. Cardiomyopathies
- Pascal
- 002 Biological and medical sciences / 002B Medical sciences / 002B22 Metabolic diseases / 002B22D Errors of metabolism / 002B22D02 Lipids (lysosomal enzyme disorders, storage diseases)
- Discipline
- Cardiology. Circulatory system Metabolic diseases
- Origin
- Inist-CNRS
- Database
- PASCAL
- INIST identifier
- 19961692
Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS
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DOI
10.1136/hrt.2006.104026 
https://dx.doi.org/10.1136/hrt.2006.104026
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