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Pyogenic Bacterial Infections in Humans with MyD88 Deficiency

Author
VON BERNUTH, Horst1 2 ; PICARD, Capucine1 2 3 ; VASCONCELOS, Julia10 ; SIRVENT, Nicolas11 ; GUEDES, Margarida10 ; BONITO VITOR, Artur12 ; HERRERO-MATA, Maria José13 ; IGNACIO AROSTEGUI, Juan14 ; RODRIGO, Carlos15 ; ALSINA, Laia16 ; RUIZ-ORTIZ, Estibaliz13 ; JUAN, Manel14 ; ZHONGBO JIN4 5 ; FORTUNY, Claudia16 ; YAGÜE, Jordi14 ; ANTON, Jordi16 ; PASCAL, Mariona14 ; CHANG, Huey-Hsuan17 ; JANNIERE, Lucile1 2 ; ROSE, Yoann1 2 ; GARTY, Ben-Zion18 ; CHAPEL, Helen19 ; ISSEKUTZ, Andrew20 ; PANKLA, Rungnapa4 6 ; MARODI, Laszlo21 ; RODRIGUEZ-GALLEGO, Carlos22 ; BANCHEREAU, Jacques4 ; ABEL, Laurent1 2 ; XIAOXIA LI7 ; CHAUSSABEL, Damien4 ; PUEL, Anne1 2 ; CASANOVA, Jean-Laurent1 2 23 ; HUI XIAO7 ; KU, Cheng-Lung1 2 ; CHRABIEH, Maya1 2 ; BEN MUSTAPHA, Imen1 2 8 ; GHANDIL, Pegah1 2 ; CAMCIOGLU, Yildiz9
[1] Human Genetics of Infectious Diseases, INSERM U550, Paris, France
[2] Paris Descartes University, France
[3] Study Center of Primary Immunodeficiencies, Assistance Publique Hôpitaux de Paris, Necker Hospital, Paris, France
[4] Baylor Institute for Immunology Research, Dallas, TX 75204, United States
[5] Baylor University, Waco, TX 76798, United States
[6] Khon Kaen University, Thailand
[7] Cleveland Clinic Foundation, OH 44195, United States
[8] Pasteur Institute of Tunis, Tunisia
[9] Cerrahpasa Medical School, Istanbul University, Turkey
[10] General Hospital of Santo António, Porto, Portugal
[11] University Hospital Archet 2, Nice, France
[12] Hospital S.joão, Porto, Portugal
[13] LIRAD-Banco de Sangre y Tejidos, Instituto de Investigacidn Germans Trias i Pujol, Badalona, Barcelona, Spain
[14] Immunology Department, Hospital Clinic, IDIBAPS, Barcelona, Spain
[15] Germans Trias i Pujol Hospital, Barcelona Autonomous University, Spain
[16] Sant Joan de Déu Hospital, Barcelona University, Spain
[17] Dendritic Cell Immunobiology, Institut Pasteur and INSERM U818, Paris, France
[18] Schneider Children's Medical Center, Petah Tiqva, Israel
[19] University of Oxford and Oxford Radcliffe Hospital, Oxford, United Kingdom
[20] Dalhousie University, Halifax, Nova Scotia, Canada
[21] Debrecen University, Hungary
[22] Gran Canaria Dr Negrin Hospital, Las Palmas de Gran Canaria, Spain
[23] Pediatric Hematology-Immunology Unit, Necker Hospital, Paris, France
Source

Science (Washington, D.C.). 2008, Vol 321, Num 5889, pp 691-696, 6 p ; ref : 31 ref

CODEN
SCIEAS
ISSN
0036-8075
Scientific domain
Multidisciplinary
Publisher
American Association for the Advancement of Science, Washington, DC
Publication country
United States
Document type
Article
Language
English
Keyword (fr)
Bactériose Déficit Homme Immunité naturelle Mutation Pyogène Récepteur TLR Gène MYD88 Infection
Keyword (en)
Bacteriosis Deficiency Human Natural immunity Mutation Pyogenic Toll like receptor Infection
Keyword (es)
Bacteriosis Déficiencia Hombre Inmunidad natural Mutación Piógeno Receptor Toll-like Infección
Classification
Pascal
002 Biological and medical sciences / 002A Fundamental and applied biological sciences. Psychology / 002A06 Fundamental immunology / 002A06C Immunobiology / 002A06C06 Genetics of the immune response

Discipline
Fundamental immunology
Origin
Inist-CNRS
Database
PASCAL
INIST identifier
20569060

Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS

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