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Clinical features and prognoses of 23 patients with chronic granulomatous disease followed for 21 years by a single hospital in Japan

Author
KOBAYASHI, Shinichi1 ; MURAYAMA, Shizuko1 ; DEGUCHI, Yasushi1 ; HIGUCHI, Kaoru1 ; WAKASUGI, Hiroaki1 ; SATO, Tatsuya1 ; WADA, Yasuyuki1 ; NAGATA, Masato1 ; OKABE, Nobuhiko1 ; TATSUZAWA, Osamu1 ; TAKANASHI, Sayaka1 ; TAKAHASHI, Kumiko1 ; MIYATSUKA, Sachiko1 ; FUJITA, Tomoko1 ; ICHINOHE, Sadato1 ; KOIKE, Yuichi1 ; KOHAGIZAWA, Toshitaka1 ; MORI, Hirosumi1
[1] National Center for Child Health and Development, Division of Rheumatology and Infectious Diseases, 2-10-1, Ookura, Setagaya-ku Tokyo, Japan
Source

European journal of pediatrics. 2008, Vol 167, Num 12, pp 1389-1394, 6 p ; ref : 20 ref

CODEN
EJPEDT
ISSN
0340-6199
Scientific domain
Genetics; Pediatrics
Publisher
Springer, Berlin / Springer, Heidelberg
Publication country
Germany
Document type
Article
Language
English
Author keyword
Antifungal prophylaxis Colitis Hematopoietic stem cell transplantation Interferon-gamma Survival rate . Severe infection
Keyword (fr)
Cellule hématopoïétique Cellule souche Chimioprophylaxie Colite Forme clinique Granulomatose chronique Grave Homme Hôpital Infection Interféron gamma Malade Milieu hospitalier Pédiatrie Survie Symptomatologie Taux Forme grave Granulomatose chronique familiale Greffe cellules souches Japon Hémopathie Immunodéficit Immunopathologie Maladie des leucocytes Maladie héréditaire Pathologie de l'appareil digestif Pathologie de l'intestin Asie
Keyword (en)
Hematopoietic cell Stem cell Chemoprophylaxis Colitis Clinical form Chronic granulomatous disease Severe Human Hospital Infection Gamma interferon Patient Hospital environment Pediatrics Survival Symptomatology Rate Chronic granulomatous disease Stem cell transplantation Japan Hemopathy Immune deficiency Immunopathology Leukocyte disease Genetic disease Digestive diseases Intestinal disease Asia
Keyword (es)
Célula hematopoyética Célula primitiva Quimioprofilaxis Colitis Forma clínica Enfermedad granulomatosa crónica Grave Hombre Hospital Infección Interferón gamma Enfermo Medio hospitalario Pediatría Sobrevivencia Sintomatología Tasa Japón Hemopatía Inmunodeficiencia Inmunopatología Leucocito enfermedad Enfermedad hereditaria Aparato digestivo patología Intestino patología Asia
Classification
Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B01 General aspects

Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B06 Immunopathology / 002B06D Immunodeficiencies. Immunoglobulinopathies / 002B06D01 Immunodeficiencies

Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B19 Hematologic and hematopoietic diseases / 002B19D Other diseases. Hematologic involvement in other diseases

Discipline
Blood diseases Generalities in medical sciences Immunopathology
Origin
Inist-CNRS
Database
PASCAL
INIST identifier
20818218

Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS

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