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Fibroblast Growth Factor 10 Plays a Causative Role in the Tracheal Cartilage Defects in a Mouse Model of Apert Syndrome

Author
TIOZZO, Caterina1 ; DE LANGHE, Stijn2 ; CARRARO, Gianni3 ; AL ALAM, Denise3 ; NAGY, Andre3 ; WIGFALL, Clarence3 ; HAJIHOSSEINI, Mohammad K4 ; WARBURTON, David3 ; MINOO, Parviz1 ; BELLUSCI, Saverio3
[1] Department of Pediatrics, Women's and Children's Hospital, University of Southern California Keck School of Medicine, Los Angeles, California 90033, United States
[2] Department of Pediatrics, National Jewish Health, Denver, Colorado 80238, United States
[3] Department of Surgery, Developmental Biology Program, Saban Research Institute of Children's Hospital Los Angeles, Los Angeles, California 90027, United States
[4] School of Biological Sciences, University of East Anglia (UEA), Norwich, Norfolk, NR4 7TJ, United Kingdom
Source

Pediatric research. 2009, Vol 66, Num 4, pp 386-390, 5 p ; ref : 33 ref

CODEN
PEREBL
ISSN
0031-3998
Scientific domain
Genetics; Pediatrics
Publisher
Lippincott Williams & Wilkins, Hagerstown, MD
Publication country
United States
Document type
Article
Language
English
Keyword (fr)
Acrocéphalosyndactylie d'Apert Cartilage Défaut Facteur croissance fibroblaste Jeu rôle Membre inférieur Membre supérieur Modèle animal Pédiatrie Souris Trachée Appareil respiratoire Dysostose Maladie congénitale Malformation Mammalia Pathologie du crâne Pathologie du système ostéoarticulaire Rodentia Vertebrata Voie respiratoire
Keyword (en)
Apert syndrome Cartilage Defect Fibroblast growth factor Role playing Lower limb Upper limb Animal model Pediatrics Mouse Trachea Respiratory system Dysostosis Congenital disease Malformation Mammalia Skull disease Diseases of the osteoarticular system Rodentia Vertebrata Respiratory tract
Keyword (es)
Apert síndrome Cartílago Defecto Factor crecimiento fibroblasto Juego de funciones Miembro inferior Miembro superior Modelo animal Pediatría Ratón Tráquea Aparato respiratorio Disostosis Enfermedad congénita Malformación Mammalia Cráneo patología Sistema osteoarticular patología Rodentia Vertebrata Vía respiratoria
Classification
Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B01 General aspects

Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B15 Diseases of the osteoarticular system / 002B15H Malformations and congenital and or hereditary diseases involving bones. Joint deformations

Discipline
Generalities in medical sciences Osteoarticular pathology
Origin
Inist-CNRS
Database
PASCAL
INIST identifier
21959639

Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS

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