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A DEFECT IN THE STRUCTURE OF TYPE I PROCOLLAGEN IN A PATIENT WHO HAD OSTEOGENESIS IMPERFECTA: EXCESS MANNOSE IN THE COOH-TERMINAL PROPEPTIDE

Author
PELTONEN L; PALOTIE A; PROCKOP DJ
NEW JERSEY-RUTGERS MED. SCH./PISCATAWAY NJ 08854/USA
Source
PROC. NATL. ACAD. SCI. U.S.A., BIOL. SCI.; USA; DA. 1980; VOL. 77; NO 10; PP. 6179-6183; BIBL. 29 REF.
Document type
Article
Language
English
Keyword (fr)
OSTEOGENESE IMPARFAITE PROCOLLAGENE ANOMALIE COMPOSITION CHIMIQUE ETIOPATHOGENIE OSTEOPATHIE HEREDITAIRE HOMME PATHOLOGIE OSTEOARTICULAIRE
Keyword (en)
OSTEOGENESIS IMPERFECTA PROCOLLAGEN ANOMALIES CHEMICAL COMPOSITION ETIOPATHOGENESIS BONE DISEASE HEREDITARY HUMAN BONE AND JOINT DISEASES
Keyword (es)
OSTEO ATICULAR PATOLOGIA
Classification
Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B15 Diseases of the osteoarticular system

Discipline
Osteoarticular pathology
Origin
Inist-CNRS
Database
PASCAL
INIST identifier
PASCAL8110394968

Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS

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