Processing of CFTR : Traversing the cellular maze-how much CFTR needs to go through to avoid cystic fibrosis?
- Author
- AMARAL, Margarida D1
[1] Department of Chemistry and Biochemistry, Faculty of Sciences, University of Lisbon, and Centre of Human Genetics, National Institute of Health Dr. Ricardo Jorge, Lisbon, Portugal - Source
Pediatric pulmonology. 2005, Vol 39, Num 6, pp 479-491, 13 p ; ref : 107 ref
- CODEN
- PEPUES
- ISSN
- 8755-6863
- Scientific domain
- Pediatrics; Pneumology
- Publisher
- Wiley-Liss, New York, NY
- Publication country
- United States
- Document type
- Article
- Language
- English
- Author keyword
- CFTR-interacting proteins F508del cystic fibrosis transmembrane conductance regulator endoplasmic reticulum maturation processing traffic
- Keyword (fr)
- Appareil respiratoire pathologie Besoin Cellule Mucoviscidose Protéine Pédiatrie Régulateur conductance transmembranaire mucoviscidose Appareil digestif pathologie Maladie héréditaire Métabolisme pathologie Pancréas pathologie
- Keyword (en)
- Respiratory disease Need Cell Cystic fibrosis Protein Pediatrics Cystic fibrosis transmembrane conductance regulator Digestive diseases Genetic disease Metabolic diseases Pancreatic disease
- Keyword (es)
- Aparato respiratorio patología Necesidad Célula Mucoviscidosis Proteína Pediatría Regulator conductancia transmembrana mucoviscidosis Aparato digestivo patología Enfermedad hereditaria Metabolismo patología Páncreas patología
- Classification
- Pascal
- 002 Biological and medical sciences / 002B Medical sciences / 002B13 Gastroenterology. Liver. Pancreas. Abdomen / 002B13C Liver. Biliary tract. Portal circulation. Exocrine pancreas / 002B13C03 Other diseases. Semiology
- Discipline
- Gastroenterology. Liver. Pancreas. Abdomen Pulmonology
- Origin
- Inist-CNRS
- Database
- PASCAL
- INIST identifier
- 16792122
Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS
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DOI
10.1002/ppul.20168 
https://dx.doi.org/10.1002/ppul.20168
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