Safety and efficacy of recombinant Alpha1-antitrypsin therapy in cystic fibrosis
- Author
- MARTIN, S. Lorraine1 ; DOWNEY, Damian2 ; BILTON, Diana3 ; KEOGAN, Mary T3 ; EDGAR, Julia4 ; ELBORN, J. Stuart2
[1] School of Pharmacy, Queen's University Belfast, Belfast, Northern Ireland, United Kingdom
[2] Northern Ireland Regional Adult Cystic Fibrosis Centre, Belfast City Hospital, Belfast, Northern Ireland, United Kingdom
[3] Adult Cystic Fibrosis Centre, Papworth Hospital, Cambridge, United Kingdom
[4] PPL Therapeutics, Plc., Roslin, Edinburgh, Scotland, United Kingdom
Recombinant AAT CF Study Team, United Kingdom - Source
Pediatric pulmonology. 2006, Vol 41, Num 2, pp 177-183, 7 p ; ref : 29 ref
- CODEN
- PEPUES
- ISSN
- 8755-6863
- Scientific domain
- Pediatrics; Pneumology
- Publisher
- Wiley-Liss, New York, NY
- Publication country
- United States
- Document type
- Article
- Language
- English
- Author keyword
- alpha1-antitrypsin cystic fibrosis inflammation neutrophil elastase
- Keyword (fr)
- Appareil respiratoire pathologie Efficacité Mucoviscidose Pédiatrie Sécurité Toxicité Traitement Appareil digestif pathologie Maladie héréditaire Métabolisme pathologie Pancréas pathologie
- Keyword (en)
- Respiratory disease Efficiency Cystic fibrosis Pediatrics Safety Toxicity Treatment Digestive diseases Genetic disease Metabolic diseases Pancreatic disease
- Keyword (es)
- Aparato respiratorio patología Eficacia Mucoviscidosis Pediatría Seguridad Toxicidad Tratamiento Aparato digestivo patología Enfermedad hereditaria Metabolismo patología Páncreas patología
- Classification
- Pascal
- 002 Biological and medical sciences / 002B Medical sciences / 002B22 Metabolic diseases / 002B22D Errors of metabolism / 002B22D05 Miscellaneous hereditary metabolic disorders
- Discipline
- Metabolic diseases Pulmonology
- Origin
- Inist-CNRS
- Database
- PASCAL
- INIST identifier
- 17536686
Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS
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DOI
10.1002/ppul.20345 
https://dx.doi.org/10.1002/ppul.20345
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