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MYOSTATIN BLOCKADE IMPROVES FUNCTION BUT NOT HISTOPATHOLOGY IN A MURINE MODEL OF LIMB-GIRDLE MUSCULAR DYSTROPHY 2C

Author
BOGDANOVICH, Sasha1 ; MCNALLY, Elizabeth M2 ; KHURANA MD, Tejvir S1
[1] Department of Physiology and Pennsylvania Muscle Institute, University of Pennsylvania School of Medicine, 3700 Hamilton Walk, Philadelphia, Pennsylvania 19104-6085, United States
[2] Section of Cardiology, Department of Medicine and Department of Human Genetics, University of Chicago, Chicago, Illinois, United States
Source

Muscle & nerve. 2008, Vol 37, Num 3, pp 308-316, 9 p ; ref : 39 ref

CODEN
MUNEDE
ISSN
0148-639X
Scientific domain
Neurology; Physiology, morphology
Publisher
Wiley, New York, NY
Publication country
United States
Document type
Article
Language
English
Author keyword
dystroglycan/sarcoglycan complex limb-girdle muscular dystrophy myostatin sarcoglycan
Keyword (fr)
Dystrophie musculaire progressive des ceintures Dystrophie musculaire Fibre musculaire Force Homme Masse musculaire Modèle animal Muscle strié Mutation Souris Stratégie Sarcoglycane γ-sarcoglycane δ-sarcoglycane Maladie héréditaire Mammalia Pathologie du système nerveux Pathologie neuromusculaire Rodentia Vertebrata
Keyword (en)
Limb girdle muscular dystrophy Muscular dystrophy Muscular fiber Force Human Muscle mass Animal model Striated muscle Mutation Mouse Strategy Sarcoglycan γ-sarcoglycan δ-sarcoglycan Genetic disease Mammalia Nervous system diseases Neuromuscular diseases Rodentia Vertebrata
Keyword (es)
Distrofia muscular progresiva cinturones Distrofia muscular Fibra muscular Fuerza Hombre Masa muscular Modelo animal Músculo estriado Mutación Ratón Estrategia γ-sarcoglicano δ-sarcoglicano Enfermedad hereditaria Mammalia Sistema nervioso patología Neuromuscular patología Rodentia Vertebrata
Classification
Pascal
002 Biological and medical sciences / 002A Fundamental and applied biological sciences. Psychology / 002A23 Vertebrates: osteoarticular system, musculoskeletal system / 002A23B Striated muscle. Tendons

Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B17 Neurology / 002B17H Diseases of striated muscles. Neuromuscular diseases

Discipline
Neurology Vertebrates : osteoarticular system, musculoskeletal system
Origin
Inist-CNRS
Database
PASCAL
INIST identifier
20139473

Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS

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