Temporal Neuropathologic and Behavioral Phenotype of 6neo/6neo Pompe Disease Mice
- Auteur
- SIDMAN, Richard L; TAKSIR, Tatyana1 ; FIDLER, Jonathan1 ; ZHAO, Michael1 ; DODGE, James C1 ; PASSINI, Marco A1 ; RABEN, Nina2 ; THURBERG, Beth L1 ; CHENG, Seng H1 ; SHIHABUDDIN, Lamya S1
[1] Beth Israel Deaconess Medical Center and Harvard Medical School, Boston, United States
[2] National Institutes of Health, NIAMS, Bethesda, Maryland, United States
[3] Genzyme Corporation, Framingham, Massachusetts, United States - Source
Journal of neuropathology and experimental neurology. 2008, Vol 67, Num 8, pp 803-818, 16 p ; ref : 61 ref
- Editeur
- Lippincott Williams & Wilkins, Hagerstown, MD
- Pays de publication
- United States
- Type de document
- Article
- Langue
- English
- Mot clé auteur
- Axon terminal degeneration Genetic disease Glycogen storage in CNS Lysosomal storage diseases Neurobiology
- Mot clé (fr)
- Animal Axone Comportement Dégénérescence Glucide Glycogène Glycogénose de Pompe Maladie héréditaire Pathologie des lysosomes Pathologie du système nerveux Phénotype Souris Stockage Système nerveux central Enzymopathie Maladie métabolique Mammalia Rodentia Vertebrata
- Mot clé (en)
- Animal Axon Behavior Degeneration Carbohydrate Glycogen Glycogenosis II Pompe Genetic disease Lysosomal storage disease Nervous system diseases Phenotype Mouse Storage Central nervous system Enzymopathy Metabolic diseases Mammalia Rodentia Vertebrata
- Mot clé (es)
- Animal Axón Conducta Degeneración Glúcido Glicógeno Glicogenosis II Pompe Enfermedad hereditaria Lisosoma patología Sistema nervioso patología Fenotipo Ratón Almacenamiento Sistema nervioso central Enzimopatía Metabolismo patología Mammalia Rodentia Vertebrata
- Classification
- Pascal
- 002 Sciences biologiques et medicales / 002B Sciences medicales / 002B17 Neurologie / 002B17G Maladies dégénératives et hérédodégénératives du système nerveux. Leucodystrophies. Maladies à prions
- Discipline
- Neurology
- Provenance
- Inist-CNRS
- Base de données
- PASCAL
- Identifiant INIST
- 20552228
Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS
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DOI
10.1097/NEN.0b013e3181815994 
https://dx.doi.org/10.1097/NEN.0b013e3181815994
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