Temporal Neuropathologic and Behavioral Phenotype of 6neo/6neo Pompe Disease Mice
- Author
- SIDMAN, Richard L; TAKSIR, Tatyana1 ; FIDLER, Jonathan1 ; ZHAO, Michael1 ; DODGE, James C1 ; PASSINI, Marco A1 ; RABEN, Nina2 ; THURBERG, Beth L1 ; CHENG, Seng H1 ; SHIHABUDDIN, Lamya S1
[1] Beth Israel Deaconess Medical Center and Harvard Medical School, Boston, United States
[2] National Institutes of Health, NIAMS, Bethesda, Maryland, United States
[3] Genzyme Corporation, Framingham, Massachusetts, United States - Source
Journal of neuropathology and experimental neurology. 2008, Vol 67, Num 8, pp 803-818, 16 p ; ref : 61 ref
- Publisher
- Lippincott Williams & Wilkins, Hagerstown, MD
- Publication country
- United States
- Document type
- Article
- Language
- English
- Author keyword
- Axon terminal degeneration Genetic disease Glycogen storage in CNS Lysosomal storage diseases Neurobiology
- Keyword (fr)
- Animal Axone Comportement Dégénérescence Glucide Glycogène Glycogénose de Pompe Maladie héréditaire Pathologie des lysosomes Pathologie du système nerveux Phénotype Souris Stockage Système nerveux central Enzymopathie Maladie métabolique Mammalia Rodentia Vertebrata
- Keyword (en)
- Animal Axon Behavior Degeneration Carbohydrate Glycogen Glycogenosis II Pompe Genetic disease Lysosomal storage disease Nervous system diseases Phenotype Mouse Storage Central nervous system Enzymopathy Metabolic diseases Mammalia Rodentia Vertebrata
- Keyword (es)
- Animal Axón Conducta Degeneración Glúcido Glicógeno Glicogenosis II Pompe Enfermedad hereditaria Lisosoma patología Sistema nervioso patología Fenotipo Ratón Almacenamiento Sistema nervioso central Enzimopatía Metabolismo patología Mammalia Rodentia Vertebrata
- Classification
- Pascal
- 002 Biological and medical sciences / 002B Medical sciences / 002B17 Neurology / 002B17G Degenerative and inherited degenerative diseases of the nervous system. Leukodystrophies. Prion diseases
- Discipline
- Neurology
- Origin
- Inist-CNRS
- Database
- PASCAL
- INIST identifier
- 20552228
Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS
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DOI
10.1097/NEN.0b013e3181815994 
https://dx.doi.org/10.1097/NEN.0b013e3181815994
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