Long-Term Effects of Enzyme Replacement Therapy on Fabry Cardiomyopathy : Evidence for a Better Outcome With Early Treatment
- Author
- WEIDEMANN, Frank1 ; NIEMANN, Markus1 ; BREUNIG, Frank1 ; HERRMANN, Sebastian1 ; BEER, Meinrad2 ; STORK, Stefan1 ; VOELKER, Wolfram1 ; ERTI, Georg1 ; WANNER, Christoph1 ; STROTMANN, Jörg1
[1] Department of Medicine, Divisions of Cardiology and Nephrology, University Hospital, Wuerzburg, Germany
[2] Department of Radiology, University Hospital, Wuerzburg, Germany - Source
Circulation (New York, N.Y.). 2009, Vol 119, Num 4, pp 524-529, 6 p ; ref : 15 ref
- CODEN
- CIRCAZ
- ISSN
- 0009-7322
- Scientific domain
- Cardiology, blood circulation, phlebology
- Publisher
- Lippincott Williams & Wilkins, Hagerstown, MD
- Publication country
- United States
- Document type
- Article
- Language
- English
- Author keyword
- Fabry disease cardiomyopathy echocardiography hypertrophy treatment
- Keyword (fr)
- Cardiomyopathie Echocardiographie Lipide Pathologie de l'appareil circulatoire Pronostic Sphingolipidose héréditaire de Fabry Traitement substitutif Cardiopathie Enzymopathie Lipoïdose Maladie héréditaire Maladie métabolique Pathologie des vaisseaux sanguins Pathologie du myocarde Pathologie du système nerveux
- Keyword (en)
- Cardiomyopathy Echocardiography Lipids Cardiovascular disease Prognosis Fabry disease Replacement therapy Heart disease Enzymopathy Lipoidosis Genetic disease Metabolic diseases Vascular disease Myocardial disease Nervous system diseases
- Keyword (es)
- Cardiomiopatía Ecocardiografía Lípido Aparato circulatorio patología Pronóstico Esfingolipidosis hereditaria Fabry Tratamiento sustitutivo Cardiopatía Enzimopatía Lipoidosis Enfermedad hereditaria Metabolismo patología Vaso sanguíneo patología Miocardio patología Sistema nervioso patología
- Classification
- Pascal
- 002 Biological and medical sciences / 002B Medical sciences / 002B02 Pharmacology. Drug treatments / 002B02G Blood. Blood coagulation. Reticuloendothelial system
- Pascal
- 002 Biological and medical sciences / 002B Medical sciences / 002B12 Cardiology. Vascular system / 002B12B Blood and lymphatic vessels / 002B12B03 Diseases of the peripheral vessels. Diseases of the vena cava. Miscellaneous
- Discipline
- Cardiology. Circulatory system Pharmacological treatments
- Origin
- Inist-CNRS
- Database
- PASCAL
- INIST identifier
- 21121159
Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS
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DOI
10.1161/CIRCULATIONAHA.108.794529 
https://dx.doi.org/10.1161/CIRCULATIONAHA.108.794529
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