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Similar hypercoagulable state and thrombosis risk in type I and type III protein S-deficient individuals from families with mixed type I/III protein S deficiency

Author
CASTOLDI, Elisabetta1 ; MAURISSEN, Lisbeth F. A1 ; TORMENE, Daniela2 ; SPIEZIA, Luca2 ; GAVASSO, Sabrina2 ; RADU, Claudia2 ; HACKENG, Tilman M1 ; ROSING, Jan1 ; SIMIONI, Paolo2
[1] Department of Biochemistry, Cardiovascular Research Institute Maastricht (CARIM), Maastricht University, Maastricht, Netherlands
[2] Department of Cardiologic, Thoracic and Vascular Sciences, 2nd Chair of Internal Medicine, University of Padua Medical School, Padua, Italy
Source

Haematologica (Roma). 2010, Vol 95, Num 9, pp 1563-1571, 9 p ; ref : 46 ref

ISSN
0390-6078
Scientific domain
Hematology
Publisher
Ferrata Storti Foundation, Pavia
Publication country
Italy
Document type
Article
Language
English
Author keyword
Kaplan-Meier analysis activated protein C protein S thrombin generation tissue factor pathway inhibitor
Keyword (fr)
Déficit en protéine S Etude familiale Facteur risque Forme clinique Homme Hypercoagulabilité Hématologie Inhibiteur Kunitz Protein C (activated) Thrombinogenèse Thrombophilie Thrombose veineuse Inhibiteur TFPI Coagulopathie Enzyme Hydrolases Hémopathie Maladie héréditaire Pathologie de l'appareil circulatoire Pathologie des vaisseaux sanguins Pathologie des veines Peptidases Serine endopeptidases
Keyword (en)
Protein S deficiency Family study Risk factor Clinical form Human Hypercoagulability Hematology Kunitz inhibitor Protein C (activated) Thrombinogenesis Thrombophilia Venous thrombosis Tissue factor pathway inhibitor Coagulopathy Enzyme Hydrolases Hemopathy Genetic disease Cardiovascular disease Vascular disease Venous disease Peptidases Serine endopeptidases
Keyword (es)
Deficiencia de proteína S Estudio familiar Factor riesgo Forma clínica Hombre Hipercoagulabilidad Hematología Inhibidor Kunitz Protein C (activated) Trombinogénesis Trombofilia Trombosis venosa Coagulopatía Enzima Hydrolases Hemopatía Enfermedad hereditaria Aparato circulatorio patología Vaso sanguíneo patología Vena patología Peptidases Serine endopeptidases
Classification
Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B12 Cardiology. Vascular system / 002B12B Blood and lymphatic vessels / 002B12B03 Diseases of the peripheral vessels. Diseases of the vena cava. Miscellaneous

Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B19 Hematologic and hematopoietic diseases / 002B19C Platelet diseases and coagulopathies

Discipline
Blood diseases Cardiology. Circulatory system
Origin
Inist-CNRS
Database
PASCAL
INIST identifier
23260777

Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS

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