Antioxidants Halt Axonal Degeneration in a Mouse Model of X-Adrenoleukodystrophy

Author

LOPEZ-ERAUSKIN, Jone^{1 2} ; FOURCADE, Stephane^{1 2} ; PUJOL, Aurora^{1 2 4 6} ; GALINO, Jorge^{1 2} ; RUIZ, Montserrat^{1 2} ; SCHLÜTER, Agatha^{1 2} ; NAUDI, Alba³ ; JOVE, Mariona³ ; PORTERO-OTIN, Manuel³ ; PAMPLONA, Reinald³ ; FERRER, Isidre^{4 5}
[1] Neurometabolic Diseases Laboratory, The Bellvitge Institute of Biomedical Research (IDIBELL), Hospitalet de Liobregat, Barcelona, Spain
[2] The Centre Biomedical Network Research on Rare Diseases (CIBERER), The Spanish Institute for Health Carlos III (ISCIII), Barcelona, Spain
[3] Experimental Medicine Department, University of Lieida-IRB-LLEIDA Biomedical Research Institute of Lieida, Lieida, Spain
[4] Neuropathology Institute, University Hospital of Bellvitge, University of Barcelona, Barcelona, Spain
[5] The Centre for Biomedical Network Research on Neurodegenerative Diseases (CIBERNED), The Spanish Institute for Health Carlos III ISCIII, Barcelona, Spain
[6] Catalan Institution of Research and Advanced Studies, Barcelona, Spain

Source

Annals of neurology. 2011, Vol 70, Num 1, pp 84-92, 9 p ; ref : 56 ref

CODEN

ANNED3

ISSN

0364-5134

Scientific domain

Neurology

Publisher

Wiley-Liss, Hoboken, NJ

Publication country

United States

Document type

Article

Language

English

Keyword (fr)

Adrénoleucodystrophie Antioxydant Caractère lié au sexe Dégénérescence Lipide Modèle animal Pathologie du système nerveux Endocrinopathie Enzymopathie Insuffisance surrénalienne Leucodystrophie Lipoïdose Maladie dégénérative Maladie héréditaire Maladie métabolique Pathologie de l'encéphale Pathologie des surrénales Pathologie du système nerveux central Sphingolipidose

Keyword (en)

Adrenoleukodystrophy Antioxidant Sex linked character Degeneration Lipids Animal model Nervous system diseases Endocrinopathy Enzymopathy Adrenal insufficiency Leukodystrophy Lipoidosis Degenerative disease Genetic disease Metabolic diseases Cerebral disorder Adrenal gland diseases Central nervous system disease Sphingolipidosis

Keyword (es)

Adrenoleucodistrofia Antioxidante Carácter ligado al sexo Degeneración Lípido Modelo animal Sistema nervioso patología Endocrinopatía Enzimopatía Insuficiencia suprarrenal Leucodistrofia Lipoidosis Enfermedad degenerativa Enfermedad hereditaria Metabolismo patología Encéfalo patología Suprarrenal patología Sistema nervosio central patología Esfingolipidosis

Classification

Pascal

002 Biological and medical sciences / 002B Medical sciences / 002B17 Neurology / 002B17G Degenerative and inherited degenerative diseases of the nervous system. Leukodystrophies. Prion diseases

Discipline

Neurology

Origin

Inist-CNRS

Database

PASCAL

INIST identifier

24407060

Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS