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Early angiotensin-converting enzyme inhibition in Alport syndrome delays renal failure and improves life expectancy

Author
GROSS, Oliver1 ; LICHT, Christoph2 ; KONRAD, Martin8 ; RASCHER, Wolfgang9 ; DÖTSCH, Jorg4 ; MÜLLER-WIEFEL, Dirk E10 ; HOYER, Peter11 ; KNEBELMANN, Bertrand12 ; PIRSON, Yves13 ; GRUNFELD, Jean-Pierre12 ; NIAUDET, Patrick14 ; COCHAT, Pierre15 ; ANDERS, Hans J3 ; HEIDET, Laurence16 ; LEBBAH, Said16 ; TORRA, Roser17 ; FRIEDE, Tim18 ; LANGE, Katharina18 ; MÜLLER, Gerhard A1 ; WEBER, Manfred19 ; HOPPE, Bernd4 ; BECK, Bodo4 ; TONSHOFF, Burkhard5 ; HÖCKER, Britta5 ; WYGODA, Simone6 ; EHRICH, Jochen H. H7 ; PAPE, Lars7
[1] Department of Nephrology and Rheumatology, University Medical Center Göttingen, Göttingen, Germany
[2] Division of Nephrology, The Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada
[3] Department of Nephrology, University of Munich, Medizinische Poliklinik, Munich, Germany
[4] Department of Pediatrics, University Hospital Cologne, Cologne, Germany
[5] University Children's Hospital Heidelberg, Heidelberg, Germany
[6] Clinic for Children and Adolescents, Hospital St Georg, Leipzig, Germany
[7] Department of Pediatric Kidney, Liver and Metabolic Diseases, Hannover Medical School, Hannover, Germany
[8] KfH-Nierenzentrum für Kinder und Jugendliche, University Hospital of Muenster, Muenster, Germany
[9] Department of Pediatrics and Adolescent Medicine, University of Erlangen-Nuremberg, Erlangen, Germany
[10] Children's Hospital University Medical Center Hamburg-Eppendorf, Hamburg, Germany
[11] Pediatric Nephrology, Endocrinology, Gastroenterology and Transplant Medicine, Children's Hospital, University Clinic Essen, Essen, Germany
[12] Division de Néphrologie, Hôpital Necker, Assistance Publique-Hôpitaux de Paris, and Université Paris Descartes, Paris, France
[13] Cliniques Universitaires UCL de Saint Luc (UCL-St-Luc), Brussels, Belgium
[14] Pediatric Nephrology, Hôpital Necker-Enfants Malades, Université Paris Descartes, Paris, France
[15] Centre de Reference des Maladies Rénales Rares, Hospices Civils de Lyon and Université de Lyon, Lyon, France
[16] Centre de Reference des Maladies Rénales Héréditaires de l'Enfant et de l'Adulte (MARHEA), Service de Néphrologie Pédiatrique, Clinique Maurice Lamy, Hôpital Necker-Enfants Malades, Paris, France
[17] Division of Nephrology, Fundacio Puigvert, Barcelona, Spain
[18] Department of Medical Statistics, University Medical Center Göttingen, Göttingen, Germany
[19] University Witten-Herdecke, Cologne General Hospital, Cologne, Germany
Source

Kidney international. 2012, Vol 81, Num 5, pp 494-501, 8 p ; ref : 31 ref

CODEN
KDYIA5
ISSN
0085-2538
Scientific domain
Urology, nephrology
Publisher
Nature Publishing Group, Basingstoke
Publication country
United Kingdom
Document type
Article
Language
English
Keyword (fr)
Espérance de vie Inhibiteur Inhibition Insuffisance rénale Néphrologie Peptidyl-dipeptidase A Précoce Retard Syndrome d'Alport Urologie Angiotensin converting enzyme Enzyme Hydrolases Maladie héréditaire Néphropathie glomérulaire Pathologie de l'appareil urinaire Pathologie du rein Peptidases Peptidyl-dipeptidases
Keyword (en)
Life expectancy Inhibitor Inhibition Renal failure Nephrology Peptidyl-dipeptidase A Early Delay Alport syndrome Urology Enzyme Hydrolases Genetic disease Glomerulonephritis Urinary system disease Kidney disease Peptidases Peptidyl-dipeptidases
Keyword (es)
Esperanza de vida Inhibidor Inhibición Insuficiencia renal Nefrología Peptidyl-dipeptidase A Precoz Retraso Alport síndrome Urología Enzima Hydrolases Enfermedad hereditaria Nefropatía glomerular Aparato urinario patología Riñón patología Peptidases Peptidyl-dipeptidases
Classification
Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B14 Nephrology. Urinary tract diseases / 002B14A Nephropathies. Renovascular diseases. Renal failure / 002B14A01 Glomerulonephritis

Pascal
002 Biological and medical sciences / 002B Medical sciences / 002B14 Nephrology. Urinary tract diseases / 002B14A Nephropathies. Renovascular diseases. Renal failure / 002B14A05 Renal failure

Discipline
Nephrology. Urinary tract diseases
Origin
Inist-CNRS
Database
PASCAL
INIST identifier
25544018

Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS

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