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Syndrome hémolytique et urémique atypique: aspects génétiques et physiopathologique : MICROANGIOPATHIE THROMBOTIQUE ET TRANSPLANTATION D'ORGANE SOLIDE = Genetics and pathophysiological mechanisms of haemolytic uremic syndromeCHAUVET, Sophie; FREMEAUX-BACCHI, Véronique.Le Courrier de la transplantation. 2012, Vol 12, Num 3, pp 122-127, issn 1628-8319, 6 p.Article

Hemolytic uremic syndrome recurrence after renal transplantationLOIRAT, Chantal; FREMEAUX-BACCHI, Véronique.Pediatric transplantation. 2008, Vol 12, Num 6, pp 619-629, issn 1397-3142, 11 p.Article

Hereditary and acquired complement dysregulation in membranoproliferative glomerulonephritisLICHT, Christoph; FREMEAUX-BACCHI, Veronique.Thrombosis and haemostasis. 2009, Vol 101, Num 2, pp 271-278, issn 0340-6245, 8 p.Conference Paper

Successful plasma therapy in hemolytic uremic syndrome with factor H deficiencyNATHANSON, Sylvie; FREMEAUX-BACCHI, Véronique; DESCHENES, Georges et al.Pediatric nephrology (Berlin, West). 2001, Vol 16, Num 7, pp 554-556, issn 0931-041XArticle

Déficits en protéines du complément en pathologie humaine : Déficits immunitaires primitifs de l'adulte. Un diagnostic à ne pas méconnaître = Complément component deficiencies in human diseaseDRAGON-DUREY, Marie-Agnès; FREMEAUX-BACCHI, Véronique.La Presse médicale (1983). 2006, Vol 35, Num 5, pp 861-870, issn 0755-4982, 10 p., CAH2Article

Syndrome hémolytique et urémique : quel est le mécanisme?FREMEAUX-BACCHI, Véronique; FAKHOURI, Fadi; LOIRAT, Chantal et al.La Revue du praticien (Paris). 2008, Vol 58, Num 19, pp 2093-2096, issn 0035-2640, 4 p.Article

Glomérulopathies à C3 = C3 glomerulopathyCHAUVET, Sophie; SERVAIS, Aude; FREMEAUX-BACCHI, Véronique et al.Néphrologie & thérapeutique. 2014, Vol 10, Num 2, pp 78-85, issn 1769-7255, 8 p.Article

CARACTERISATION ET ROLE FONCTIONNEL DE LA FORME SOLUBLE DU RECEPTEUR CD21 = CHARACTERIZATION AND FUNCTIONAL PROPERTIES OF SOLUBLE CD21Fremeaux Bacchi, Véronique; Kazatchkine, Michel.1999, 204 p.Thesis

Atypical haemolytic uraemic syndrome and mutations in complement regulator genesDRAGON-DUREY, Marie-Agnès; FREMEAUX-BACCHI, Véronique.Springer seminars in immunopathology. 2005, Vol 27, Num 3, pp 359-374, issn 0344-4325, 16 p.Article

No lupus nephritis in the absence of antiC1q autoantibodies?FREMEAUX-BACCHI, Veronique; NOËL, Laure Hélène; SCHIFFERLI, Jürg A et al.Nephrology, dialysis, transplantation (Print). 2002, Vol 17, Num 12, pp 2041-2043, issn 0931-0509, 3 p.Article

Le complément en Médecine Interne = Investigation of the complement system in clinical practiceFREMEAUX-BACCHI, Véronique; DRAGON-DUREY, Marie-Agnès; BLOUIN, Jacques et al.Annales de médecine interne (Paris). 2003, Vol 154, Num 8, pp 529-540, issn 0003-410X, 12 p.Article

Atypical Hemolytic Uremic Syndrome Associated with Mutations in Complement Regulator GenesLE QUINTREC, Moglie; ROUMENINA, Lubka; NORIS, Marina et al.Seminars in thrombosis and hemostasis. 2010, Vol 36, Num 6, pp 641-652, issn 0094-6176, 12 p.Article

Autoantibodies in haemolytic uraemic syndrome (HUS)SKERKA, Christine; JOZSI, Mihaly; ZIPFEL, Peter F et al.Thrombosis and haemostasis. 2009, Vol 101, Num 2, pp 227-232, issn 0340-6245, 6 p.Conference Paper

Varicella as a trigger of atypical haemolytic uraemic syndrome associated with complement dysfunction: two casesKWON, Theresa; BELOT, Alexandre; RANCHIN, Bruno et al.Nephrology, dialysis, transplantation (Print). 2009, Vol 24, Num 9, pp 2752-2754, issn 0931-0509, 3 p.Article

Déficits en protéines du complément et pathologies humaines = Complement deficiencies and human diseasesROSAIN, Jérémiei; NGO, Stéphanie; BORDEREAU, Pauline et al.Annales de biologie clinique (Paris). 2014, Vol 72, Num 3, pp 271-280, issn 0003-3898, 10 p.Article

Pulse Cyclophosphamide Therapy and Clinical Remission in Atypical Hemolytic Uremic Syndrome With Anti-Complement Factor H AutoantibodiesBOYER, Olivia; BALZAMO, Eve; CHARBIT, Marina et al.American journal of kidney diseases. 2010, Vol 55, Num 5, pp 923-927, issn 0272-6386, 5 p.Article

Complement alternative pathway acts as a positive feedback amplification of neutrophil activationCAMOUS, Laurent; ROUMENINA, Lubka; BIGOT, Sylvain et al.Blood. 2011, Vol 117, Num 4, pp 1340-1349, issn 0006-4971, 10 p.Article

Complement Factor H Deficiency and Posttransplantation Glomerulonephritis With Isolated C3 DepositsBOYER, Olivia; NOËL, Laure-Hélène; BALZAMO, Eve et al.American journal of kidney diseases. 2008, Vol 51, Num 4, pp 671-677, issn 0272-6386, 7 p.Article

Late-onset thrombocytic microangiopathy caused by cblC disease: Association with a factor H mutationGUIGONIS, Vincent; FREMEAUX-BACCHI, Véronique; GIRAUDIER, Stéphane et al.American journal of kidney diseases. 2005, Vol 45, Num 3, pp 588-595, issn 0272-6386, 8 p.Article

Physiopathologie des microangiopathies thrombotiques = Pathophysiology of thrombotic microangiopathies: current understandingCOPPO, Paul; VEYRADIER, Agnès; DUREY, Marie-Agnès et al.Annales de médecine interne (Paris). 2002, Vol 153, Num 3, pp 153-166, issn 0003-410XArticle

Successful use of eculizumab in a patient with post-transplant thrombotic microangiopathyDE LATOUR, Regis Peffault; XHAARD, Alienor; FREMEAUX-BACCHI, Veronique et al.British journal of haematology. 2013, Vol 161, Num 2, pp 279-280, issn 0007-1048, 2 p.Article

Thrombotic microangiopathy mimicking membranoproliferative glomerulonephritisBRACKMAN, Damien; SARTZ, Lisa; LEH, Sabine et al.Nephrology, dialysis, transplantation (Print). 2011, Vol 26, Num 10, pp 3399-3403, issn 0931-0509, 5 p.Article

Myocardial infarction is a complication of factor H-associated atypical HUSSALLEE, Marion; DANIEL, Laurent; PIERCECCHI, Marie-Dominique et al.Nephrology, dialysis, transplantation (Print). 2010, Vol 25, Num 6, pp 2028-2032, issn 0931-0509, 5 p.Article

Successful pre-transplant management of a patient with anti-factor H autoantibodies-associated haemolytic uraemic syndromeKWON, Theresa; DRAGON-DUREY, Marie-Agnes; MACHER, Marie-Alice et al.Nephrology, dialysis, transplantation (Print). 2008, Vol 23, Num 6, pp 2088-2090, issn 0931-0509, 3 p.Article

Membrane cofactor protein mutations in atypical hemolytic uremic syndrome (aHUS), fatal Stx-HUS, C3 glomerulonephritis, and the HELLP syndromeFANG, Celia J; FREMEAUX-BACCHI, Veronique; LISZEWSKI, M. Kathryn et al.Blood. 2008, Vol 111, Num 2, pp 624-632, issn 0006-4971, 9 p.Article

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