A structure-based analysis of huntingtin mutant polyglutamine aggregation and toxicity: evidence for a compact beta-sheet structurePOIRIER, Michelle A; HAIBING JIANG; ROSS, Christopher A et al.Human molecular genetics (Print). 2005, Vol 14, Num 6, pp 765-774, issn 0964-6906, 10 p.Article

ATF3 plays a protective role against toxicity by N-terminal fragment of mutant huntingtin in stable PC12 cell lineYIDENG LIANG; HAIBING JIANG; ROSS, Christopher A et al.Brain research. 2009, Vol 1286, pp 221-229, issn 0006-8993, 9 p.Article

Beyond disgust : impaired recognition of negative emotions prior to diagnosis in Huntington's diseaseJOHNSON, Shannon A; STOUT, Julie C; HAYDEN, Michael R et al.Brain. 2007, Vol 130, pp 1732-1744, issn 0006-8950, 13 p., 7Article

Bioactivity profiling with parallel mass spectrometry reveals an assemblage of green tea metabolites affording protection against human huntingtin and α-synuclein toxicityWILLIAMS, Russell B; GUTEKUNST, Will R; MATTHEW JOYNER, P et al.Journal of agricultural and food chemistry (Print). 2007, Vol 55, Num 23, pp 9450-9456, issn 0021-8561, 7 p.Article

Identification and functional characterization of a novel R621C mutation in the synphilin-1 gene in Parkinson's diseaseMARX, Frank P; HOLZMANN, Carsten; ENGELENDER, Simone et al.Human molecular genetics (Print). 2003, Vol 12, Num 11, pp 1223-1231, issn 0964-6906, 9 p.Article

A genome scan for modifiers of age at onset in huntington disease: The HD MAPS StudyLI, Jian-Liang; HAYDEN, Michael R; ROSENBLATT, Adam et al.American journal of human genetics. 2003, Vol 73, Num 3, pp 682-687, issn 0002-9297, 6 p.Article

Immunocytochemical localization of synphilin-1, an α-synuclein-associated protein, in neurodegenerative disordersWAKABAYASHI, Koichi; ENGELENDER, Simone; TANAKA, Yuji et al.Acta neuropathologica. 2002, Vol 103, Num 3, pp 209-214, issn 0001-6322Article

Psychopathology in patients with degenerative cerebellar diseases: A comparison to Huntington's diseaseLEROI, Iracema; O'HEARN, Elizabeth; MARSH, Laura et al.The American journal of psychiatry. 2002, Vol 159, Num 8, pp 1306-1314, issn 0002-953XArticle

Dichloroacetate exerts therapeutic effects in transgenic mouse models of Huntington's diseaseANDREASSEN, Ole A; FERRANTE, Robert J; BEAL, M. Flint et al.Annals of neurology. 2001, Vol 50, Num 1, pp 112-117, issn 0364-5134Article

Widespread occurrence of intranuclear atrophin-1 accumulation in the central nervous system neurons of patients with dentatorubral-pallidoluysian atrophyYAMADA, Mitsunori; WOOD, Jonathan D; SHIMOHATA, Takayoshi et al.Annals of neurology. 2001, Vol 49, Num 1, pp 14-23, issn 0364-5134Article

Prefrontal executive function associated coupling relates to Huntington's disease stageUNSCHULD, Paul G; XINYANG LIU; READING, Sarah A et al.Cortex (Testo stampato). 2013, Vol 49, Num 10, pp 2661-2673, issn 0010-9452, 13 p.Article

Striatal Neuronal Loss Correlates With Clinical Motor Impairment in Huntington's DiseaseZHIHONG GUO; RUDOW, Gay; TRONCOSO, Juan C et al.Movement disorders. 2012, Vol 27, Num 11, pp 1379-1386, issn 0885-3185, 8 p.Article

Motor Abnormalities in Premanifest Persons with Huntington's Disease: The PREDICT-HD StudyBIGLAN, Kevin M; ROSS, Christopher A; LANGBEHN, Douglas R et al.Movement disorders. 2009, Vol 24, Num 12, pp 1763-1772, issn 0885-3185, 10 p.Article

The antidepressant sertraline improves the phenotype, promotes neurogenesis and increases BDNF levels in the R6/2 Huntington's disease mouse modelQI PENG; MASUDA, Naoki; MALI JIANG et al.Experimental neurology (Print). 2008, Vol 210, Num 1, pp 154-163, issn 0014-4886, 10 p.Article

Characterization of huntingtin pathologic fragments in human huntington disease, transgenic mice, and cell modelsSCHILLING, Gabriele; KLEVYTSKA, Alexandra; TEBBENKAMP, Andrew T. N et al.Journal of neuropathology and experimental neurology. 2007, Vol 66, Num 4, pp 313-320, issn 0022-3069, 8 p.Article

Effects of CAG repeat length, HTT protein length and protein context on cerebral metabolism measured using magnetic resonance spectroscopy in transgenic mouse models of Huntington's diseaseJENKINS, Bruce G; ANDREASSEN, Ole A; DEDEOGLU, Alpaslan et al.Journal of neurochemistry. 2005, Vol 95, Num 2, pp 553-562, issn 0022-3042, 10 p.Article

Autophagosome-like vacuole formation in Huntington's disease lymphoblastsNAGATA, Eiichiro; SAWA, Akira; ROSS, Christopher A et al.Neuroreport (Oxford). 2004, Vol 15, Num 8, pp 1325-1328, issn 0959-4965, 4 p.Article

Inducible PC12 cell model of huntington's disease shows toxicity and decreased histone acetylationIGARASHI, Shuichi; MORITA, Hokuto; BENNETT, Kyla M et al.Neuroreport (Oxford). 2003, Vol 14, Num 4, pp 565-568, issn 0959-4965, 4 p.Article

Inducible expression of mutant α-synuclein decreases proteasome activity and increases sensitivity to mitochondria-dependent apoptosisTANAKA, Yuji; ENGELENDER, Simone; IGARASHI, Shuichi et al.Human molecular genetics (Print). 2001, Vol 10, Num 9, pp 919-926, issn 0964-6906Article

Common SNP-Based Haplotype Analysis of the 4p16.3 Huntington Disease Gene RegionLEE, Jong-Min; GILLIS, Tammy; SQUITIERI, Ferdinando et al.American journal of human genetics. 2012, Vol 90, Num 3, pp 434-444, issn 0002-9297, 11 p.Article

Smaller intracranial volume in prodromal Huntington's disease: evidence for abnormal neurodevelopmentNOPOULOS, Peggy C; AYLWARD, Elizabeth H; BARKER, Roger A et al.Brain. 2011, Vol 134, pp 137-142, issn 0006-8950, 6 p., 1Article

Prenatal Interaction of Mutant DISC1 and Immune Activation Produces Adult PsychopathologyABAZYAN, Bagrat; NOMURA, Jun; CADET, Jean Lud et al.Biological psychiatry (1969). 2010, Vol 68, Num 12, pp 1172-1181, issn 0006-3223, 10 p.Article

Huntington's disease-like 2 is associated with CUG repeat-containing RNA fociRUDNICKI, Dobrila D; HOLMES, Susan E; LIN, Mark W et al.Annals of neurology. 2007, Vol 61, Num 3, pp 272-282, issn 0364-5134, 11 p.Article

Predictors of neuropathological severity in 100 patients with Huntington's DiseaseROSENBLATT, Adam; ABBOTT, Margaret H; GOURLEY, Lisa M et al.Annals of neurology. 2003, Vol 54, Num 4, pp 488-493, issn 0364-5134, 6 p.Article

Polyglutamine and transcription: gene expression changes shared by DRPLA and Huntington's disease mouse models reveal context-independent effectsLUTHI-CARTER, Ruth; STRAND, Andrew D; OLSON, James M et al.Human molecular genetics (Print). 2002, Vol 11, Num 17, pp 1927-1937, issn 0964-6906Article