BIOCHEMIE DER SPHINGOLIPIDSPEICHERKRANKHEITEN. = BIOCHIMIE DES SPHINGOLIPIDOSESSANDHOFF K.1977; ANGEW. CHEM.; DTSCH.; DA. 1977; VOL. 89; NO 5; PP. 283-295; BIBL. 2 P. 1/2Article

LIPID-PROTEIN-WECHSELWIRKUNGEN. MECHANISMEN DES ENZYMATISCHEN GLYKOLIPID-ABBAUS UND SEINE GENETISCH BEDINGTEN ENTGLEISUNGEN = INTERACTIONS LIPIDES PROTEINES. MECANISMES DE LA DEGRADATION ENZYMATIQUE DES GLYCOLIPIDES ET SES ECARTS DETERMINES GENETIQUEMENTSANDHOFF K.1980; NATURWISSENSCHAFTEN; ISSN 0028-1042; DEU; DA. 1980; VOL. 67; NO 9; PP. 431-441; ABS. ENG; BIBL. 37 REF.Article

BIOCHEMIE DER ERBKRANKHEITEN. = BIOCHIMIE DES MALADIES HEREDITAIRESSANDHOFF K.1977; CHEM. UNSER. ZEIT; DTSCH.; DA. 1977; VOL. 11; NO 1; PP. 1-13; BIBL. 14 REF.Article

AB VARIANT OF INFANTILE GM2 GANGLIOSIDOSIS: DEFICIENCY OF A FACTOR NECCESSARY FOR STIMULATION OF HEXOSAMINIDASE A-CATALYZED DEGRADATION OF GANGLIOSIDE GM2 AND GLYCOLIPID GA2CONZELMANN E; SANDHOFF K.1978; PROC. NATION. ACAD. SCI. USA; USA; DA. 1978; VOL. 75; NO 8; PP. 3979-3983; BIBL. 16 REF.Article

HALOTHANE INCREASES MEMBRANE FLUIDITY AND STIMULATES SPHINGOMYELIN DEGRADATION BY MEMBRANE-BOUND NEUTRAL SPHINGOMYELINASE OF SYNAPTOSOMAL PLASMA MEMBRANES FROM CALF BRAIN ALREADY AT CLINICAL CONCENTRATIONSPELLKOFER R; SANDHOFF K.1980; J. NEUROCHEM.; GBR; DA. 1980; VOL. 34; NO 4; PP. 988-992; BIBL. 16 REF.Article

PURIFICATION AND CHARACTERIZATION OF AN ACTIVATOR PROTEIN FOR THE DEGRADATION OF GLYCOLIPIDS G_M2 AND G_A2 BY HEXOSAMINIDASE ACONZELMANN E; SANDHOFF K.1979; Z. (HOPPE-SEYLER'S) PHYSIOL. CHEM.; DEU; DA. 1979; VOL. 360; NO 12; PP. 1837-1849; ABS. GER; BIBL. 27 REF.Article

BIOCHEMISTRY AND GENETICS OF GANGLIOSIDOSESSANDHOFF K; CHRISTOMANOU H.1979; HUM. GENET.; DEU; DA. 1979; VOL. 50; NO 2; PP. 108-143; BIBL. 13 P.Article

VARIATION OF ARYLSULPHATASE A: COMPARATIVE OF ARYLSULPHATASE A WITH SYNTHETIC AND NATURAL SUBSTRATES IN THREE FAMILIES WITH METACHROMATIC LEUCODYSTROPHYCHRISTOMANOU H; SANDHOFF K.1978; NEUROPAEDIATRIE; DEU; DA. 1978; VOL. 9; NO 4; PP. 385-395; ABS. GER; BIBL. 25 REF.Article

A SENSITIVE FLUORESCENCE ASSAY FOR THE SIMULTANEOUS AND SEPARATE DETERMINATION OF ARYLSULPHATASES A AND B.CHRISTOMANOU H; SANDHOFF K.1977; CLIN. CHIM. ACTA; PAYS-BAS; DA. 1977; VOL. 79; NO 3; PP. 527-531; BIBL. 16 REF.Article

SPHINGOLIPIDSPEICHERKRANKHEITEN ALS BEISPIEL EINER MOLEKULAREN NEUROPATHOLOGIE. = MALADIE DE STOCKAGE DES SPHINGOLIPIDES EN TANT QU'EXEMPLE DE NEUROPATHOLOGIE MOLECULAIREJATZKEWITZ H; SANDHOFF K.1976; ARCH. PSYCHIATR. NERVENKRANKLI.; DTSCH.; DA. 1976; VOL. 221; NO 3; PP. 213-225; ABS. ANGL.; BIBL. 1 P. 1/2Article

MEMBRANE-BOUND NEURAMINIDASE FROM CALF BRAIN: REGULATION OF OLIGOSIALOGANGLIOSIDE DEGRADATION BY MEMBRANE FLUIDITY AND MEMBRANE COMPONENTS.SANDHOFF K; PALLMANN B.1978; PROC. NATION. ACAD. SCI. U.S.A.; U.S.A.; DA. 1978; VOL. 75; NO 1; PP. 122-126; BIBL. 25 REF.Article

EFFECT OF XENON, NITROUS OXIDE AND HALOTHANE ON MEMBRANE-BOUND SIALIDASE FROM CALF BRAINSANDHOFF K; SCHRAVEN J; NOWOCZEK G et al.1976; F.E.B.S. LETTERS; NETHERL.; DA. 1976; VOL. 62; NO 3; PP. 284-287; BIBL. 18 REF.Article

PRENATAL DIAGNOSIS OF TAY-SACHS DISEASE IN CELL-FREE AMNIOTIC FLUIDCHRISTOMANOU H; CAP C; SANDHOFF K et al.1978; KLIN. WSCHR.; DEU; DA. 1978; VOL. 56; NO 22; PP. 1133-1135; ABS. GER; BIBL. 9 REF.Article

ISOELECTRIC FOCUSING PATTERN OF ACID HYDROLASES IN CULTURED FIBROBLASTS, LEUCOCYTES AND CELL-FREE AMNIOTIC FLUID.CHRISTOMANOU H; CAP C; SANDHOFF K et al.1977; NEUROPAEDIATRIE; DTSCH.; DA. 1977; VOL. 8; NO 3; PP. 238-252; ABS. ALLEM.; BIBL. 16 REF.Article

SPECIFICITY OF HUMAN LIVER HEXOSAMINIDASES A AND B AGAINST GLYCOSPHINGOLIPIDS G_M2 AND G_A2. PURIFICATION OF THE ENZYMES BY AFFINITY CHROMATOGRAPHY EMPLOYING SPECIFIC ELUTION.SANDHOFF K; CONZELMANN E; NEHRKORN H et al.1977; Z. (HOPPE-SEYLER'S) PHYSIOL. CHEM.; DTSCH.; DA. 1977; VOL. 358; NO 7; PP. 779-787; ABS. ALLEM.; BIBL. 32 REF.Article

IMMUNOCHEMICAL AND BIOCHEMICAL INVESTIGATION OF HEXOSAMINIDASE S.GEIGER B; ARNON R; SANDHOFF K et al.1977; AMER. J. HUM. GENET.; U.S.A.; DA. 1977; VOL. 29; NO 5; PP. 508-522; BIBL. 24 REF.Article

Human acid sphingomyelinase from human urineQUINTERN, L. E; SANDHOFF, K.Methods in enzymology. 1991, Vol 197, pp 536-540, issn 0076-6879Article

Zentralnervöse Sphingolipid-Speicherkrankheiten: Grundlagen ihrer biochemischen und klinischen Heterogenität = Sphingolipidose du système nerveux central: hétérogénéité biochimique et clinique = Sphingolipidosis and central nervous system: biochemical and clinical heterogeneitySANDHOFF, K; QUINTERN, L.Naturwissenschaften. 1988, Vol 75, Num 3, pp 123-131, issn 0028-1042Article

Activator proteins for lysosomal glycolipid hydrolysisCONZELMANN, E; SANDHOFF, K.Methods of biochemical analysis. 1987, Vol 32, pp 1-23, issn 0076-6941Article

Ganglioside metabolism : enzymology, topology, and regulationVAN ECHTEN, G; SANDHOFF, K.The Journal of biological chemistry (Print). 1993, Vol 268, Num 8, pp 5341-5344, issn 0021-9258Article

Metabolism and intracellular transport of glycosphingolipidsSCHWARZMANN, G; SANDHOFF, K.Biochemistry (Easton). 1990, Vol 29, Num 49, pp 10865-10871, issn 0006-2960, 7 p.Article

Evidence for two different active sites on human β-hexosaminidase A: interaction of G_M2 activator protein with β-hexosaminidase AKYTZIA, H.-J; SANDHOFF, K.The Journal of biological chemistry (Print). 1985, Vol 260, Num 12, pp 7568-7572, issn 0021-9258Article

Biochemical basis of late-onset neurolipidosesCONZELMANN, E; SANDHOFF, K.Developmental neuroscience. 1991, Vol 13, Num 4-5, pp 197-204, issn 0378-5866Article

Partial enzyme deficiencies: residual activities and the development of neurological disordersCONZELMANN, E; SANDHOFF, K.Developmental neuroscience. 1983, Vol 6, Num 1, pp 58-71, issn 0378-5866Article

COMPLEXING OF GLYCOLIPIDS AND THEIR TRANSFER BETWEEN MEMBRANES BY THE ACTIVATOR PROTEIN FOR DEGRADATION OF LYSOSOMAL GANGLIOSIDE GM₂CONZELMANN E; BURG J; STEPHAN G et al.1982; EUR. J. BIOCHEM.; ISSN 0014-2956; DEU; DA. 1982; VOL. 123; NO 2; PP. 455-464; BIBL. 35 REF.Article