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kw.\*:("Aspartoacylase")

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PURIFICATION OF COBALT-ACTIVATED ACYLASE BY AFFINITY CHROMATOGRAPHYSLOWINSKA R; SZEWCZUK A.1979; ACTA BIOCHIM. POLON.; POL; DA. 1979; VOL. 26; NO 3; PP. 229-258; ABS. POL; BIBL. 2 P.Article

N-acetylaspartic aciduria due to aspartoacylase deficiency ― a new aetiology of childhood leukodystrophyHAGENFELDT, L; BOLLGREN, I; VENIZELOS, N et al.Journal of inherited metabolic disease. 1987, Vol 10, Num 2, pp 135-141, issn 0141-8955Article

Aspartoacylase deficiency and N-acetylaspartic aciduria in patients with Canavan disease. ReplyDIVRY, P; MATHIEU, M; MATALON, R et al.American journal of medical genetics. 1989, Vol 32, Num 4, pp 550-551, issn 0148-7299Article

Differential aminoacylase expression in neuroblastomaLONG, Patrick M; STRADECKI, Holly M; MINTURN, Jane E et al.International journal of cancer (Print). 2011, Vol 129, Num 6, pp 1322-1330, issn 0020-7136, 9 p.Article

Adenoviral gene transfer of aspartoacylase ameliorates tonic convulsions of spontaneously epileptic ratsSEKI, Takahiro; MATSUBAYASHI, Hiroaki; AMANO, Taku et al.Neurochemistry international. 2004, Vol 45, Num 1, pp 171-178, issn 0197-0186, 8 p.Article

Purification, characterization, and localization of aspartoacylase from bovine brainKAUL, R; CASANOVA, J; JOHNSON, A. B et al.Journal of neurochemistry. 1991, Vol 56, Num 1, pp 129-135, issn 0022-3042, 7 p.Article

Aspartoacylase deficiency: the enzyme defect in Canavan diseaseMATALON, R; KAUL, R; CASANOVA, J et al.Journal of inherited metabolic disease. 1989, Vol 12, pp 329-331, issn 0141-8955, suppl. 2Article

Developmental and regional distribution of aspartoacylase in rat brain tissueBHAKOO, Kishore K; CRAIG, Tim J; STYLES, Peter et al.Journal of neurochemistry. 2001, Vol 79, Num 1, pp 211-220, issn 0022-3042Article

Variable course of canavan disease in two boys with early infantile aspartoacylase deficiencyMOERS, A; SPERNER, J; MICHAEL, T et al.Developmental medicine and child neurology (Print). 1991, Vol 33, Num 9, pp 824-828, issn 0012-1622Article

Identification and distribution of aspartoacylase in the postnatal rat brainKLUGMANN, Matthias; SYMES, C. Wymond; KLAUSSNER, Bettina K et al.Neuroreport (Oxford). 2003, Vol 14, Num 14, pp 1837-1840, issn 0959-4965, 4 p.Article

Implication des acylases dans le métabolisme des protéines N-acylées chez les mammifères = Acylases and N-acetylated proteins metabolism by mammalsGIARDINA, T; FERJANCIC-BIAGINI, A; PUIGSERVER, A et al.Regard sur la biochimie. 1997, Num 2, pp 21-29, issn 0336-1640Article

Biochemical diagnosis of Canavan diseaseBARTALINI, G; MARGOLLICCI, M; BALESTRI, P et al.Child's nervous system (Print). 1992, Vol 8, Num 8, pp 468-470, issn 0256-7040Article

Canavan disease : findings in four new casesMICHELAKAKIS, H; GIOUROUKOS, S; DIVRY, P et al.Journal of inherited metabolic disease. 1991, Vol 14, Num 2, pp 267-268, issn 0141-8955, 2 p.Article

Prolonged survival in canavan diseaseFEIGELMAN, T; SHIH, V. E; BUYSE, M. L et al.Dysmorphology and clinical genetics. 1991, Vol 5, Num 4, pp 107-110, issn 0893-6633Article

Intraneuronal N-acetylaspartate supplies acetyl groups for myelin lipid synthesis : evidence for myelin-associated aspartoacylaseCHAKRABORTY, Goutam; MEKALA, Praveen; YAHYA, Daniel et al.Journal of neurochemistry. 2001, Vol 78, Num 4, pp 736-745, issn 0022-3042Article

Aspartoacylase deficiency and canavan disease in Saudi ArabiaOZAND, P. T; GASCON, G. G; MOHAMMED DHALLA et al.American journal of medical genetics. 1990, Vol 35, Num 2, pp 266-268, issn 0148-7299Article

DEACETYLATION AND DEFORMYLATION OF N-ACYL AMINO ACIDS BY KIDNEY ACYLASESENDO Y.1978; F.E.B.S. LETTERS; NLD; DA. 1978; VOL. 95; NO 2; PP. 281-283; BIBL. 5 REF.Article

Biochemistry and molecular biology of Canavan diseaseMATALON, R; MICHALS-MATALON, K.Neurochemical research. 1999, Vol 24, Num 4, pp 507-513, issn 0364-3190Article

Reliable prenatal diagnosis of Canavan disease (aspartoacylase deficiency) : comparison of enzymatic and metabolite analysisBENNETT, M. J; GIBSON, K. M; SHERWOOD, W. G et al.Journal of inherited metabolic disease. 1993, Vol 16, Num 5, pp 831-836, issn 0141-8955Article

Aspartoacylase supports oxidative energy metabolism during myelinationFRANCIS, Jeremy S; STRANDE, Louise; MARKOV, Vladamir et al.Journal of cerebral blood flow and metabolism. 2012, Vol 32, Num 9, pp 1725-1736, issn 0271-678X, 12 p.Article

Adenoviral gene transfer of aspartoacylase into the tremor rat, a genetic model of epilepsy, as a trial of gene therapy for inherited epileptic disorderSEKI, Takahiro; MATSUBAYASHI, Hiroaki; AMANO, Taku et al.Neuroscience letters. 2002, Vol 328, Num 3, pp 249-252, issn 0304-3940Article

Canavan disease : molecular basis of aspartoacylase deficiencyKAUL, R; GAO, G. P; BALAMURUGAN, K et al.Journal of inherited metabolic disease. 1994, Vol 17, Num 3, pp 295-297, issn 0141-8955Conference Paper

Triacetin-based acetate supplementation as a chemotherapeutic adjuvant therapy in gliomaTSEN, Andrew R; LONG, Patrick M; JAWORSKI, Diane M et al.International journal of cancer (Print). 2014, Vol 134, Num 6, pp 1300-1310, issn 0020-7136, 11 p.Article

Possible genotype-phenotype correlations in children with mild clinical course of canavan diseaseTACKE, U; OLBRICH, H; VARGIAMI, E et al.Neuropediatrics. 2005, Vol 36, Num 4, pp 252-255, issn 0174-304X, 4 p.Article

Ultrasound findings in follow-up investigations in a case of aspartoacylase deficiency (Canavan disease)BREITBACH-FALLER, N; SCHRADER, K; RATING, D et al.Neuropediatrics. 2003, Vol 34, Num 2, pp 96-99, issn 0174-304X, 4 p.Article

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