ATAXIN-3 PROTECTS CELLS AGAINST H₂O₂-INDUCED OXIDATIVE STRESS BY ENHANCING THE INTERACTION BETWEEN BCL-X_L AND BAXZHOU, L; WANG, H; WANG, P et al.Neuroscience. 2013, Vol 243, pp 14-21, issn 0306-4522, 8 p.Article

Oxidative stimuli affect polyglutamine aggregation and cell death in human mutant ataxin-1-expressing cellsKIM, Sung-Jo; KIM, Tae-Soo; HONG, Sunghoi et al.Neuroscience letters. 2003, Vol 348, Num 1, pp 21-24, issn 0304-3940, 4 p.Article

Ataxin-2 promotes apoptosis of human neuroblastoma cellsWIEDEMEYER, Ruprecht; WESTERMANN, Frank; WITTKE, Isabel et al.Oncogene (Basingstoke). 2003, Vol 22, Num 3, pp 401-411, issn 0950-9232, 11 p.Article

Stress responses of PML nuclear domains are ablated by ataxin-I and other nucleoprotein inclusionsDOVEY, Claire L; VARADARAJ, Archana; WYLLIE, Andrew H et al.Journal of pathology. 2004, Vol 203, Num 4, pp 877-883, issn 0022-3417, 7 p.Article

Preferential recruitment of ataxin-3 independent of expanded polyglutamine: an immunohistochemical study on marinesco bodiesFUJIGASAKI, H; UCHIHARA, T; TAKAHASHI, J et al.Journal of neurology, neurosurgery and psychiatry. 2001, Vol 71, Num 4, pp 518-520, issn 0022-3050Article

The spinocerebellar ataxia type 1 protein, ataxin-1, has RNA-binding activity that is inversely affected by the length of its polyglutamine tractSHINJI YUE; SERRA, Heliane G; ZOGHBI, Huda Y et al.Human molecular genetics (Print). 2001, Vol 10, Num 1, pp 25-30, issn 0964-6906Article

Polyglutamine-expanded ataxin-7 upregulates Bax expression by activating p53 in cerebellar and inferior olivary neuronsWANG, Hung-Li; CHOU, An-Hsun; LIN, An-Chi et al.Experimental neurology (Print). 2010, Vol 224, Num 2, pp 486-494, issn 0014-4886, 9 p.Article

Rescue of polyglutamine-mediated cytotoxicity by double-stranded RNA-mediated RNA interferenceCAPLEN, Natasha J; TAYLOR, J. Paul; STATHAM, Victoria S et al.Human molecular genetics (Print). 2002, Vol 11, Num 2, pp 175-184, issn 0964-6906Article

Distribution of ataxin-7 in normal human brain and retinaCANCEL, Géraldine; DUYCKAERTS, Charles; BRICE, Alexis et al.Brain. 2000, Vol 123, pp 2519-2530, issn 0006-8950, 12Article

Caspase-mediated proteolysis of the polyglutamine disease protein ataxin-3SHOESMITH BERKE, Sarah J; FLORES SCHMIED, Francisca A; BRUNT, Ewout R et al.Journal of neurochemistry. 2004, Vol 89, Num 4, pp 908-918, issn 0022-3042, 11 p.Article

Promyelocytic leukemia protein is redistributed during the formation of intranuclear inclusions independent of polyglutamine expansion: An immunohistochemical study on marinesco bodiesKUMADA, Satoko; UCHIHARA, Toshiki; HAYASHI, Masaharu et al.Journal of neuropathology and experimental neurology. 2002, Vol 61, Num 11, pp 984-991, issn 0022-3069, 8 p.Article

Exercise and Genetic Rescue of SCA1 via the Transcriptional Repressor CapicuaFRYER, John D; PENG YU; ZOGHBI, Huda Y et al.Science (Washington, D.C.). 2011, Vol 334, Num 6056, pp 690-693, issn 0036-8075, 4 p.Article

Evidence against haploinsuffiency of human ataxin 10 as a cause of spinocerebellar ataxia type 10KEREN, Boris; JACQUETTE, Aurélia; HERON, Delphine et al.Neurogenetics (Oxford. Print). 2010, Vol 11, Num 2, pp 273-274, issn 1364-6745, 2 p.Article

A cell-based screen for modulators of ataxin-1 phosphorylationKAYTOR, Michael D; BYAM, Courtney E; TOUSEY, Susan K et al.Human molecular genetics (Print). 2005, Vol 14, Num 8, pp 1095-1105, issn 0964-6906, 11 p.Article

SCA7 mouse models show selective stabilization of mutant ataxin-7 and similar cellular responses in different neuronal cell typesYVERT, Gaël; LINDENBERG, Katrin S; DEVYS, Didier et al.Human molecular genetics (Print). 2001, Vol 10, Num 16, pp 1679-1692, issn 0964-6906Article

High level expression of expanded full-length ataxin-3 in vitro causes cell death and formation of intranuclear inclusions in neuronal cellsEVERT, B. O; WÜLLNER, U; SCHULZ, J. B et al.Human molecular genetics (Print). 1999, Vol 8, Num 7, pp 1169-1176, issn 0964-6906Article

Ataxin-3 is transported into the nucleus and associates with the nuclear matrixTAIT, D; RICCIO, M; SITTLER, A et al.Human molecular genetics (Print). 1998, Vol 7, Num 6, pp 991-997, issn 0964-6906Article

Cloning and developmental expression analysis of the murine homolog of the spinocerebellar ataxia type 1 gene (Sca1)BANFI, S; SERVADIO, A; CHUNG, M.-Y et al.Human molecular genetics (Print). 1996, Vol 5, Num 1, pp 33-40, issn 0964-6906Article

Ataxin-7 associates with microtubules and stabilizes the cytoskeletal networkNAKAMURA, Yoko; TAGAWA, Kazuhiko; OKA, Tsutomu et al.Human molecular genetics (Print). 2012, Vol 21, Num 5, pp 1099-1110, issn 0964-6906, 12 p.Article

The Machado―Joseph disease-associated mutant form of ataxin-3 regulates parkin ubiquitination and stabilityDURCAN, Thomas M; KONTOGIANNEA, Maria; THORARINSDOTTIR, Thorhildur et al.Human molecular genetics (Print). 2011, Vol 20, Num 1, pp 141-154, issn 0964-6906, 14 p.Article

Preventing Ataxin-3 protein cleavage mitigates degeneration in a Drosophila model of SCA3JUNG, Joonil; KEXIANG XU; LESSING, Derek et al.Human molecular genetics (Print). 2009, Vol 18, Num 24, pp 4843-4852, issn 0964-6906, 10 p.Article

Ataxin-2 and huntingtin interact with endophilin-A complexes to function in plastin-associated pathwaysRALSER, Markus; NONHOFF, Ute; ALBRECHT, Mario et al.Human molecular genetics (Print). 2005, Vol 14, Num 19, pp 2893-2909, issn 0964-6906, 17 p.Article

Interference of Crx-dependent transcription by ataxin-7 involves interaction between the glutamine regions and requires the ataxin-7 carboxy-terminal region for nuclear localizationSHIMING CHEN; PENG, Guang-Hua; XUEJIAO WANG et al.Human molecular genetics (Print). 2004, Vol 13, Num 1, pp 53-67, issn 0964-6906, 15 p.Article

Intranuclear aggregation of nonexpanded ataxin-3 in marinesco bodies of the nonhuman primate substantia nigraKETTNER, Mattias; WILLWOHL, Dirk; HUBBARD, Gene B et al.Experimental neurology (Print). 2002, Vol 176, Num 1, pp 117-121, issn 0014-4886, 5 p.Article

CAG tract of MJD-1 may be prone to frameshifts causing polyalanine accumulationGASPAR, C; JANNATIPOUR, M; DION, P et al.Human molecular genetics (Print). 2000, Vol 9, Num 13, pp 1957-1966, issn 0964-6906Article