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au.\*:("BRADY RO")

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BIOCHEMICAL AND METABOLIC BASIS OF FAMILIAL SPHINGOLIPIDOSES = LES BASES BIOCHIMIQUES ET METABOLIQUES DES SPHINGOLIPIDOSES FAMILIALESBRADY RO.1972; SEMINARS HEMATOL.; U.S.A.; DA. 1972; VOL. 9; NO 3; PP. 273-284; BIBL. 2P.Serial Issue

INHERITED METABOLIC STORANGE DISORDERSBRADY RO.1982; ANNU. REV. NEUROSCI.; ISSN 0147-006X; USA; DA. 1982; VOL. 5; PP. 33-56; BIBL. 5 P.Article

DISORDERS OF LIPID METABOLISM = LES TROUBLES DU METABOLISME DES LIPIDESBRADY RO.1972; BIOCHEM. SOC. SYMP.; G.B.; DA. 1972; NO 35; PP. 113-127; BIBL. 1P.1/2; (CURR. TRENDS BIOCHEM. LIPIDS. PROC. INT. SYMP. LIPIDS; BANGALORE; 1971)Conference Paper

ENZYMOLOGICAL APPROACHES TO THE LIPIDOSES.BRADY RO.1977; ANN. CLIN. LAB. SCI.; U.S.A.; DA. 1977; VOL. 7; NO 2; PP. 105-112; BIBL. 2 P.Article

ERBKRANKHEITEN. URSACHEN, BEHANDLUNG UND PROBLEME = MALADIES HEREDITAIRES, ETIOLOGIE, TRAITEMENT ET PROBLEMESBRADY RO.1973; ANGERV. CHEM.; DTSCH.; DA. 1973; VOL. 85; NO 1; PP. 28-38; BIBL. 1P.1/2Serial Issue

LIPIDOSESBRADY RO.1972; BIOCHIMIE; FR.; DA. 1972; VOL. 54; NO 5-6; PP. 723-733; ABS. FR.; BIBL. 1P.Serial Issue

BIOTRANSDUCERS OF MEMBRANE-MEDIATED INFORMATIONBRADY RO; FISHMAN PH.1979; ADV. IN ENZYMOL.; USA; DA. 1979; VOL. 50; PP. 303-323; BIBL. 90 REF.Article

COMPARISON OF THE EFFECTS OF DELTA 9-TETRAHYDROCANNABINOL, 11-HYDROXY-DELTA 9-TETRAHYDROCANNABINOL, AND ETHANOL ON THE ELECTROPHYSIOLOGICAL ACTIVITY OF THE GIANT AXON OF THE SQUID = COMPARAISON DES EFFETS DU DELTA 9-TETRAHYDROCANNABINOL, DE L'HYDROXY-11 DELTA 9-TETRAHYDROCANNABINOL ET DE L'ETHANOL SUR L'ACITIVITE ELECTROPHYSIOLOGIQUE DE L'AXONE GEANT DU CALMARBRADY RO; CARBONE E.1973; NEUROPHARMACOLOGY; G.B.; DA. 1973; VOL. 12; NO 6; PP. 601-605; BIBL. 12REF.Serial Issue

THE EFFECT OF A HEAST-STABLE FACTOR IN HUMAN SPLEEN ON GLUCOCEREBROSIDASE AND ACID BETA -GLUCOSIDASE ACTIVITIESPENTCHEV PG; BRADY RO.1973; BIOCHIM. BIOPHYS. ACTA; PAYS-BAS; DA. 1973; VOL. 297; NO 2; PP. 491-496; BIBL. 7REF.Serial Issue

BIOSYNTHESIS AND FUNCTION OF GANGLIOSIDES.FISHMAN PH; BRADY RO.1976; SCIENCE; U.S.A.; DA. 1976; VOL. 194; NO 4268; PP. 906-915; BIBL. 1 P.Article

EXTERNAL LABELING OF GALACTOSE IN SURFACE MEMBRANE GLYCOPROTEINS OF THE INTACT MYELIN SHEATHPODUSLO JF; QUARLES RH; BRADY RO et al.1976; J. BIOL. CHEM.; U.S.A.; DA. 1976; VOL. 251; NO 1; PP. 153-158; BIBL. 35 REF.Article

METABOLISM OF A MYELIN-ASSOCIATED GLYCOPROTEIN IN DEVELOPING RAT BRAINDRUSE MJ; BRADY RO; QUARLES RH et al.1974; BRAIN RES.; NETHERL.; DA. 1974; VOL. 76; NO 3; PP. 423-434; BIBL. 1P.Article

SUSCEPTIBILITY OF THE MYELIN-ASSOCIATED GLYCOPROTEIN AND BASIC PROTEIN TO A NEUTRAL PROTEASE IN HIGHLY PURIFIED MYELIN FROM HUMAN AND RAT BRAINSATO S; QUARLES RH; BRADY RO et al.1982; J. NEUROCHEM.; ISSN 0022-3042; GBR; DA. 1982; VOL. 39; NO 1; PP. 97-105; BIBL. 29 REF.Article

A BETA -GLUCOSIDASE IN FELINE KIDNEY THAT HYDROLYZES AMYGDALIN (LAETRILE)FREESE A; BRADY RO; GAL AE et al.1980; ARCH. BIOCHEM. BIOPHYS.; USA; DA. 1980; VOL. 201; NO 2; PP. 363-368; BIBL. 21 REF.Article

EFFECT OF THYROID PHOSPHOLIPIDS ON THE INTERACTION OF THYROTROPIN WITH THYROID MEMBRANESOMODEO SALE F; BRADY RO; FISHMAN PH et al.1978; PROC. NATION. ACAD. SCI.; USA; DA. 1978; VOL. 75; NO 11; PP. 5301-5305; BIBL. 38 REF.Article

INVESTIGATIONS IN ENZYME REPLACEMENT THERAPY IN LIPID STORAGE DISEASESBRADY RO; PENTCHEV PG; GAL AE et al.1975; FEDER. PROC.; U.S.A.; DA. 1975; VOL. 34; NO 5; PP. 1310-1315; BIBL. 35REF.Serial Issue

EVOLUTION OF ENZYME REPLACEMENT THERAPY FOR LIPID STORAGE DISEASES = EVOLUTION DU TRAITEMENT DES LIPIDOSES PAR REMPLACEMENT DES ENZYMESBRADY RO; GAL AE; PENTCHEV PG et al.1974; LIFE SCI.; G.B.; DA. 1974; VOL. 15; NO 7; PP. 1235-1248; BIBL. 2P.1/2Article

THE LIVER IN LIPID STORAGE DISEASE: BIOCHERMICAL BASIS OF PATHOGENESIS AND CLINICAL FEATURESBRADY RO; JAMES SP; BARRANGER JA et al.1982; PROGRESS IN LIVER DISEASES; ISSN 0079-6409; USA; DA. 1982; VOL. 7; PP. 331-346; BIBL. 37 REF.Article

CHANGE IN A MYELIN-ASSOCIATED GLYCOPROTEIN IN RAT BRAIN DURING DEVELOPMENT: METABOLIC ASPECTSMATTHIEU JM; BRADY RO; QUARLES RH et al.1975; BRAIN RES.; NETHERL.; DA. 1975; VOL. 86; NO 1; PP. 55-65; BIBL. 13REFArticle

THE METABOLISM OF TAY-SACHS GANGLIOSIDE: CATABOLIC STUDIES WITH LYSOSOMAL ENZYMES FROM NORMAL AND TAY-SACHS BRAIN TISSUE = LE METABOLISME DU GANGLIOSIDE DE LA MALADIE DE TAY-SACHS: ETUDES CATABOLIQUES AVEC LES ENZYMES LYSOSOMALES DU TISSU CEREBRAL NORMAL ET DE LA MALADIE DE TAY-SACHSTALLMAN JF; JOHNSON WG; BRADY RO et al.1972; J. CLIN. INVEST.; U.S.A.; DA. 1972; VOL. 51; NO 9; PP. 2339-2345; BIBL. 27 REF.Serial Issue

DEXAMETHASONE-INDUCED CHANGE IN THE SPINGOMYELIN CONTENT OF HUMAN POLYMORPHONUCLEAR LEUKOCYTES IN VITRONELSON DH; MURRAY DK; BRADY RO et al.1982; J. CLIN. ENDOCRINOL. METAB.; ISSN 0021-972X; USA; DA. 1982; VOL. 54; NO 2; PP. 292-295; BIBL. 28 REF.Article

A RADIOIMMUNOASSAY FOR THE MYELIN-ASSOCIATED GLYCOPROTEINJOHNSON D; QUARLES RH; BRADY RO et al.1982; JOURNAL OF NEUROCHEMISTRY; ISSN 0022-3042; GBR; DA. 1982; VOL. 39; NO 5; PP. 1356-1362; BIBL. 22 REF.Article

NIEMANN-PICK DISEASE EXPERIMENTAL MODEL.LULLMANN H; LULLMANN RAUCH R; BRADY RO et al.1978; SCIENCE; USA; DA. 1978; VOL. 200; NO 4341; PP. 568-569; BIBL. 8 REF.Article

PROTEINS AND GLYCOPROTEINS IN MYELIN PURIFIED FROM THE DEVELOPING BOVINE AND HUMAN CENTRAL NERVOUS SYSTEMS.EVERLY JL; QUARLES RH; BRADY RO et al.1977; J. NEUROCHEM.; G.B.; DA. 1977; VOL. 28; NO 1; PP. 95-101 (6P.); BIBL. 27 REF.Article

AN ENZYMOLOGICAL APPROACH TO THE LIPIDOSESTALLMAN JF; PENTCHEV PG; BRADY RO et al.1974; ENZYME; SWITZ.; DA. 1974; VOL. 18; NO 12; PP. 136-149; BIBL. 4P.Article

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