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kw.\*:("Bernard Soulier disease")

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Esquisse d'une histoire de la dystrophie thrombocytaire hémorragipare congénitale = Brief case history of congenital hemorrhagic thrombocytic dystrophyBERNARD, J; BELLUCHI, S.Actualités hématologiques. 1983, Vol 17, pp 3-13, issn 0567-8757Article

Micropipette aspiration of human blood platelets: a defect in Bernard-Soulieŕs syndromeWHITE, J. G; BURRIS, S. M; HASEGAWA, D et al.Blood. 1984, Vol 63, Num 5, pp 1249-1252, issn 0006-4971Article

INVAGINATED PLASMA MEMBRANE OF HUMAN PLATELETS: EVAGINATION AND MEASUREMENT IN NORMAL AND "GIANT" PLATELETSMILTON JG; FROJMOVIC MM.1979; J. LAB. CLIN. MED.; USA; DA. 1979; VOL. 93; NO 1; PP. 162-170; BIBL. 29 REF.Article

UNE NOUVELLE THROMBOPATHIE CONGENITALE FAMILIALEWATTEBLED DE DUCLA BARRABES GENEVIEVE; BARRABES MICHEL.1979; ; FRA; BORDEAUX: ED. BERGERET; DA. 1979; 90-91; 98 P.: ILL.-PL.; 23 CM; BIBL. 76 REF.; TH.: MED./BORDEAUX 2/1979Thesis

VALOR DE LA SEPARACION DE LAS PLAQUETAS POR GRADIENTES EN EL DIAGNOSTICO DE LAS TROMBOPATIAS CONGENITAS = VALEUR DE LA SEPARATION DES PLAQUETTES PAR GRADIENTS DANS LE DIAGNOSTIC DES THROMBOPATHIES CONGENITALES. A PROPOS D'UN CAS DE THROMBOPATHIE DE SOUBER-BERNARDGALLEGO CUBILES R; GONZALEZ AZA C; LARA AL et al.1979; SANGRE; ESP; DA. 1979; VOL. 24; NO 6; PP. 1119-1124; ABS. ENG; BIBL. 28 REF.Article

Abnormal phospholipid organization in Bernard-Soulier plateletsPERRET, B; LEVY-TOLEDANO, S; PLANTAVID, M et al.Thrombosis research. 1983, Vol 31, Num 4, pp 529-537, issn 0049-3848Article

Abord moléculaire des thrombopathies constitutionelles = Hereditary thrombopathiesCAEN, J.-P.Actualités hématologiques. 1985, Num 19, pp 28-29, issn 0567-8757Article

Additional glycoprotein defects in Bernard Soulier's syndrome: confirmation of genetic basis by parental analysisBERNDT, M. C; GREGORY, C; CHONG, B. H et al.Blood. 1983, Vol 62, Num 4, pp 800-807, issn 0006-4971Article

DYSTROPHIE THROMBOCYTAIRE HEMORRAGIPAREBERNARD J; CAEN J; TOBELEM G et al.1982; ACTUAL. HEMATOL.; ISSN 0567-8757; FRA; DA. 1982; NO 15; PP. 127-129; BIBL. 12 REF.Article

PLATELETS FROM "GIANT PLATELET SYNDROME (BSS)" ARE DISCOCYTES AND NORMAL SIZED.FROJMOVIC MM; MILTON JG; CAEN JP et al.1978; J. LAB. CLIN. MED.; U.S.A.; DA. 1978; VOL. 91; NO 1; PP. 109-118; BIBL. 1 P. 1/2Article

AN INVESTIGATION OF THROMBASTHENIC PLATELETS WITH SELECTED LECTINSFIRKIN BG; HENDRIX L; GOH A et al.1978; THROMBOSIS RES.; GBR; DA. 1978; VOL. 13; NO 3; PP. 337-344; BIBL. 13 REF.Article

FURTHER INVESTIGATIONS ON BERNARD-SOULIER PLATELET ABNORMALITIESRENDU F; NURDEN AT; LEBRET M et al.1981; J. LAB. CLIN. MED.; ISSN 0022-2143; USA; DA. 1981; VOL. 97; NO 5; PP. 689-699; BIBL. 41 REF.Article

BERNARD-SOULIER DISEASE: A STUDY OF FOUR PATIENTS AND THEIR PARENTSGEORGE JN; REIMANN TA; MOAKE JL et al.1981; BR. J. HAEMATOL.; ISSN 0007-1048; GBR; DA. 1981; VOL. 48; NO 3; PP. 459-467; BIBL. 19 REF.Article

DONNEES CLINIQUES ET BIOLOGIQUES SUR LA DYSTROPHIE THROMBOCYTAIRE HEMORRAGIPARE.TOBELEM G.1976; NOUV. REV. FR. HEMATOL.; FR.; DA. 1976; VOL. 16; NO 3; PP. 407-411; ABS. ANGL.; BIBL. 16 REF.; (CONGR. FR. HEMATOL. 2. SYMP. THROMBOPATHIES CONST. ACQUISES; LE TOUQUET; 1976)Conference Paper

ETUDE D'UN ANTICORPS ANTIPLAQUETTAIRE SURVENU CHEZ UN MALADE ATTEINT DE DYSTROPHIE THROMBOCYTAIRE HEMORRAGIPARE.TOBELEM G.1976; ; S.L.; DA. 1976; PP. 1-60; BIBL. 7 P. 1/2; (THESE DOCT. MED.; PARIS VII)Thesis

PLATELET GLYCOPROTEINS OF BERNARD-SOULIER SYNDROME: ANALYSIS BY ISOELECTRIC FOCUSING AND SODIUM DODECYL SULFATE POLYACRYLAMIDE GEL ELECTROPHORESIS IN A TWO-DIMENSIONAL TECHNIQUENIBU K; IDEGUCHI H; HAMASAKI N et al.1982; THROMBOSIS RESEARCH; ISSN 0049-3848; USA; DA. 1982; VOL. 28; NO 1; PP. 67-74; BIBL. 23 REF.Article

PLASMA FACTORS AND THROMBASTHEMIC PLATELETSDE CATALDO F; BAUDO F.1981; BR. J. HAEMATOL.; ISSN 0007-1048; GBR; DA. 1981; VOL. 48; NO 3; PP. 511-512; BIBL. 5 REF.Article

SITES MEMBRANAIRES SPECIFIQUES ET FONCTIONS PLAQUETTAIRES. ETUDE GRACE A UN ANTICORPS SURVENU CHEZ UN DYSTROPHIQUE POLYTRANSFUSETOBELEM G; LEVY TOLEDANO S; BREDOUX R et al.1977; ACTUAL. HEMATOL.; FRA; DA. 1977; VOL. 11; PP. 267-272; BIBL. 6 REF.Article

Le syndrome de Bernard Soulier = Bernard Soulier syndromeAYKAN, N. F; DINCAC, E.Archives de l'Union Médicale Balkanique. 1985, Vol 23, Num 5-6, pp 384-385, issn 0041-6940Conference Paper

Les thrombopathies constitutionnelles = Constitutional thrombopathyCAEN, J.Comptes rendus des séances de la Société de biologie et de ses filiales. 1984, Vol 178, Num 3, pp 241-250, issn 0037-9026Article

Morphometric analysis of platelets in Bernard-Soulier syndrome: size and configuration in patients and carriersMCGILL, M; JAMIESON, G. A; DROUIN, J et al.Thrombosis and haemostasis. 1984, Vol 52, Num 1, pp 37-41, issn 0340-6245Article

Inherited platelet disordersBELLUCCI, S; TOBELEM, G; CAEN, J. P et al.Progress in hematology. 1983, Vol 13, pp 223-263, issn 0079-6301Article

Double heterozygosity for mutations in the platelet glycoprotein IX gene in three siblings with Bernard-Soulier syndromeWRIGHT, S. D; MICHAELIDES, K; JOHNSON, D. J. D et al.Blood. 1993, Vol 81, Num 9, pp 2339-2347, issn 0006-4971Article

GLYCOPROTEIN-SIALYLTRANSFERASE ACTIVITY OF NORMAL HUMAN, THROMBASTHENIC AND BERNARD-SOULIER PLATELETSBAUVOIS B; CARTRON JP; NURDEN A et al.1981; VOX SANG.; ISSN 0042-9007; CHE; DA. 1981; VOL. 40; NO 2; PP. 71-78; BIBL. 19 REF.Article

EFFECT OF SHEAR RATE ON PLATELET INTERACTION WITH SUBENDOTHELIUM IN CITRATED AND NATIVE BLOOD. I: SHEAR RATE-DEPENDENT DECREASE OF ADHESION IN VON WILLEBRAND'S DISEASE AND THE BERNARD-SOULIER SYNDROMEWEISS HJ; TURITTO VT; BAUMGARTNER HR et al.1978; J. LAB. CLIN. MED.; USA; DA. 1978; VOL. 92; NO 5; PP. 750-764; BIBL. 42 REF.Article

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