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LEUCODYSTROPHIE A CELLULES GLOBOIDES (MALADIE DE KRABBE). LESIONS NERVEUSES PERIPHERIQUESMARTIN JJ; CEUTERICK C; MARTIN L et al.1974; ACTA NEUROL. BELG.; BELG.; DA. 1974; VOL. 74; NO 6; PP. 356-375; ABS. ANGL.; BIBL. 15REF.Article

A POSSIBLE THERAPEUTIC APPROACH TO KRABBE'S GLOBOID LEUKODYSTROPHY = UNE METHODE POSSIBLE DE TRAITEMENT DE LA LEUCODYSTROPHIE GLOBOIDE DE KRABBERADIN NS; ARORA RC; ULLMAN MD et al.1972; RES. COMMUNIC. CHEM. PATHOL. PHARMACOL.; U.S.A.; DA. 1972; VOL. 3; NO 3; PP. 637-644; BIBL. 9REF.Serial Issue

CHEMICAL PATHOLOGY OF KRABBE'S DISEASE. III. CERAMIDE-HEXOSIDES AND GANGLIOSIDES OF BRAIN.VANIER MT; SVENNERHOLM L.1975; ACTA PAEDIATR. SCAND.; SUEDE; DA. 1975; VOL. 64; NO 4; PP. 641-648; BIBL. 1 P.Article

ELECTROENCEPHALOGRAPHIC FINDINGS IN A CASE OF GLOBOID CELL LEUKODYSTROPHY = RESULTATS DE L'ELECTROENCEPHALOGRAPHIE DANS UN CAS DE LEUCODYSTROPHIE A CELLULES GLOBOIDESIINUMA K; ONUMA A.1975; TOHOKU J. EXPER. MED.; JAP.; DA. 1975; VOL. 115; NO 1; PP. 75-79; BIBL. 6REF.Article

GLYCOSPHINGOLIPID BETA -GALACTOSIDASES. II. ELECTROFOCUSING CHARACTERIZATION OF THE ENZYMES IN HUMAN GLOBOID CELL LEUKODYSTROPHY (KRABBE'S DISEASE) = GLYCOSPHINGOLIPIDE BETA -GALACTOSIDASES. II. CARACTERISATION PAR ELECTROFOCALISATION DES ENZYMES DANS LA LEUCODYSTROPHIE DES CELLULES GLOBOIDES HUMAINES (MALADIE DE KRABBE)SUZUKI Y; SUZUKI K.1974; J. BIOL. CHEM.; U.S.A.; DA. 1974; VOL. 249; NO 7; PP. 2105-2108; BIBL. 14 REF.Article

KRABBE DISEASE: A GALACTOSYLSPHINGOSINE (PSYCHOSINE) LIPIDOSISSVENNERHOLM L; VANIER MT; MANSSON JE et al.1980; J. LIPID RES.; USA; DA. 1980; VOL. 21; NO 1; PP. 53-64; BIBL. 39 REF.Article

USE OF A CHROMOGENIC SUBSTRATE FOR THE DIAGNOSIS OF KRABBE'S DISEASE WITH SPECIAL REFERENCE TO ITS APPLICATION IN PRENATAL DIAGNOSISBESLEY GTN; BAIN AD.1978; CLIN. CHIM. ACTA; NLD; DA. 1978; VOL. 88; NO 2; PP. 229-236; BIBL. 13 REF.Article

ZUR ENTSTEHUNG VON MEHRKERNIGEN RIESENZELLEN BEI DER EXPERIMENTELL-INDUZIERTEN UND SPONTANEN KRABBESCHEN KRANKHEIT (GLOLOID CELL LEUKODYSTROPHY) = SUR L'ORIGINE DE CELLULES GEANTES MULTINUCLEEES DE LA MALADIE DE KRABBE INDUITE ET SPONTANEE. (LEUCODYSTROPHIE A CELLULE GLOBOIDE)OEHMICHEN M; GRUENINGER H.1974; BEITR. PATHOL.; DTSCH.; DA. 1974; VOL. 153; NO 2; PP. 111-132; ABS. ANGL.; BIBL. 2 P.Article

NON-MEMBRANE-BOUND CYTOPLASMIC DEPOSITS IN KRABLE GLOBOID LEUKODYSTROPHY: FURTHER EVIDENCE FOR A REVISED CONCEPT OF LYSOSOMAL STORAGE DISEASE = DEPOTS CYTOPLASMIQUES NON LIES A LA MEMBRANE DANS LA LEUCODYSTROPHIE GLOBOIDE DE KRABBE: NOUVEL ARGUMENT EN FAVEUR D'UNE REVISION DES CONCEPTIONS SUR LES MALADIES DE LA MISE EN RESERVE LYSOSOMALEBLINZINGER K; ANZIL AP.1972; EXPERIENTIA; SUISSE; DA. 1972; VOL. 29; NO 7; PP. 780-781; ABS. ALLEM.; BIBL. 11 REF.Serial Issue

THE PATHOLOGY OF SPHINGOLIPIDOSES = LA PATHOLOGIE DES SPHINGOLIPIDOSESVOLK BW; ADACHI M; SCHNECK L et al.1972; SEMINARS HEMATOL.; U.S.A.; DA. 1972; VOL. 9; NO 3; PP. 317-348; BIBL. 9P.Serial Issue

USE OF LEUKOCYTES IN DIAGNOSIS OF KRABBE DISEASE AND DETECTION OF CARRIERSSVENNERHOLM L; VANIER MT; HAKANSSON G et al.1981; CLIN. CHIM. ACTA; ISSN 0009-8981; NLD; DA. 1981; VOL. 112; NO 3; PP. 333-342; BIBL. 16 REF.Article

A COMPARATIVE STUDY OF MYELIN FRACTIONS FROM METACHROMATIC AND GLOBOID LEUKODYSTROPHIES. = ETUDE COMPARATIVE DES FRACTIONS DE LA MYELINE DES LEUCODYSTROPHIES METACHROMATIQUE ET GLOBOIDEMALONE MJ; SAKURAGAWA N; SZOKE M et al.1975; NEUROLOGY; U.S.A.; DA. 1975; VOL. 25; NO 9; PP. 827-832; BIBL. 21 REF.Article

DOENCA DE KRABBE (LEUCODISTROFIA DE CELULAS GLOBOIDES = MALADIE DE KRABBE (LEUCODYSTROPHIE A CELLULES GLOBOIDESALENCAR A.1972; MEM. INST. OSWALDO CRUZ; BRAS.; DA. 1972; VOL. 70; NO 3; PP. 337-352; ABS. FR.; BIBL. 13REF.Serial Issue

IMPROVED MYELINATION IN NERVE GRAFTS FROM THE LEUCODYSTROPHIC TWITCHER INTO TREMBLER MICE: EVIDENCE FOR ENZYME REPLACEMENTSCARAVILLI F; JACOBS JM.1982; BRAIN RES.; ISSN 0006-8993; NLD; DA. 1982; VOL. 237; NO 1; PP. 163-172; BIBL. 26 REF.Article

ENZYME-HISTOCHEMICAL DIFFERENTIATION OF NEUROGLIA AND MICROGLIA: A CONTRIBUTION TO THE CYTOGENESIS OF MICROGLIA AND GLOBOID CELLSOEHMICHEN M.1980; PATHOL., RES. PRACT.; DEU; DA. 1980; VOL. 168; NO 4; PP. 344-373; BIBL. 167 REF.Article

APPLICATION OF A GALACTOSYLCERAMIDASE MICROASSAY METHOD TO EARLY PRENATAL DIAGNOSIS OF KRABBE'S DISEASETSUTSUMI O; SATOH K; SAKAMOTO S et al.1982; CLINICA CHIMICA ACTA; ISSN 0009-8981; NLD; DA. 1982; VOL. 125; NO 3; PP. 265-273; BIBL. 15 REF.Article

HEREDITARY LEUCODYSTROPHY IN THE MOUSE: THE NEW MUTANT TWITCHERDUCHEN LW; EICHER EM; JACOBS JM et al.1980; BRAIN; ISSN 0006-8950; GBR; DA. 1980; VOL. 103; NO 3; PP. 695-710; BIBL. 2 P.Article

PRENATAL DIAGNOSIS IN TWIN PREGNANCYSUZUKI Y; NAKAMURA N; JIMBO T et al.1978; J. PEDIATR.; USA; DA. 1978; VOL. 93; NO 2; PP. 293-294; BIBL. 8 REF.Article

QUANTITATIVE EVALUATION OF SPINAL CORD LESIONS IN CANINE GLOBOID LEUKODYSTROPHY.FLETCHER TF; JESSEN CR; BENDER AP et al.1977; J. NEUROPATHOL. EXPER. NEUROL.; U.S.A.; DA. 1977; VOL. 36; NO 1; PP. 84-99; BIBL. 7 REF.Article

PRAENATALE DIAGNOSE DER GLOBOIDZELL-LEUKODYSTROPHIE (MORBUS KRABBE) = DIAGNOSTIC PRENATAL DE LA LEUCODYSTROPHIE A CELLULES GLOBOIDES (MALADIE DE KRABBE)HARZER K; BENZ HU; KNORR GARTNER H et al.1976; DTSCHE MED. WSCHR.; DTSCH.; DA. 1976; VOL. 101; NO 21; PP. 821-828 (5P.); ABS. ANGL.; BIBL. 11 REF.Article

CYTOPLASMIC INCLUSIONS IN A CHILD AFFECTED WITH KRABBE'S DISEASE (GLOBOID LEUCODYSTROPHY) AND IN THE RABBIT INJECTED WITH GALACTOCEREBROSIDES = INCLUSIONS CYTOPLASMIQUES CHEZ UN ENFANT ATTEINT DE MALADIE DE KRABBE (LEUCODYSTROPHIE GLOBOIDE) ET CHEZ LE LAPIN APRES INJECTION DE GALACTOCEREBROSIDESANZIL AP; BLINZINGER K; MEHRAEIN P et al.1972; J. NEUROPATHOL. EXPER. NEUROL.; U.S.A.; DA. 1972; VOL. 31; NO 2; PP. 370-388; BIBL. 2 P.Serial Issue

KRABBE'S DISEASE. HISTOPATHOLOGY AND ULTRASTRUCTURE OF THE EYEEMERY JM; GREEN WR; HUFF DS et al.1972; AMER. J. OPHTHALMOL.; U.S.A.; DA. 1972; VOL. 74; NO 3; PP. 400-406; BIBL. 12REF.Serial Issue

Growth pattern in Krabbe's diseaseZLOTOGORA, J; REGEV, R; HADAR, S et al.Acta paediatrica scandinavica. 1986, Vol 75, Num 2, pp 251-254, issn 0001-656XArticle

LIPIDS OF DEVELOPING BRAIN OF TWITCHER MOUSE: AN AUTHENTIC MURINE MODEL OF HUMAN KRABBE DISEASEIGISU H; SHIMOMURA K; KISHIMOTO Y et al.1983; BRAIN; ISSN 0006-8950; GBR; DA. 1983; VOL. 106; NO 2; PP. 405-417; BIBL. 2 P.Article

THE CEREBRAL LIPIDOSES.MALONE MJ.1976; PEDIATR. CLIN. N. AMER.; U.S.A.; DA. 1976; VOL. 23; NO 2; PP. 303-326; BIBL. 2 P. 1/2Article

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