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kw.\*:("CEROIDE LIPOFUSCHINOSE NEURONALE INFANTILE")

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INFANTILE TYPE OF SO-CALLED NEURONAL CEROID-LIPOFUSCINOSIS = LA FORME INFANTILE DE LA CEROIDE-LIPOFUSCINOSE NEURONALESANTAVUORI P; HALTIA M; RAPOLA J et al.1974; DEVELOP. MED. CHILD NEUROL.; G.B.; DA. 1974; VOL. 16; NO 5; PP. 644-653; ABS. FR. ALLEM.; BIBL. 25REF.Article

NEURONAL STORAGE DISORDER WITH CHOREA AND CURVILINEAR BODIES = TROUBLE NEURONAL DE STOCKAGE AVEC CHOREE ET PRESENCE DE CORPS CURVILIGNESDAL CANTO MC; RAPIN I; SUZUKI K et al.1974; NEUROLOGY; U.S.A.; DA. 1974; VOL. 24; NO 11; PP. 1026-1032; BIBL. 31REF.Article

CONTRIBUTION A L'ETUDE DES CEROID-LIPOFUSCINOSESDUPREY JEAN.sd; FRA; LILLE: ASSOCIATION CORPORATIVE ETUDIANTS MED.; DA. S.D.; 198; 145-XXXIII P.; 30 CM; BIBL. 269 REF.; TH.: MED./LILLE 2/1978Thesis

NEURONAL CEROID-LIPOFUSCINOSIS. STUDIES OF GRANULOCYTE ENZYME ACTIVITIES.MIN FU TSAN; GALE AN; MURPHY EA et al.1978; J. NEUROL. SCI.; NETHERL.; DA. 1978; VOL. 36; NO 1; PP. 13-24; BIBL. 24 REF.Article

SUPEROXIDE DISMUTASE, CATALASE AND GLUTATHIONE PEROXIDASE IN INFANTILE, LATE INFANTILE AND JUVENILE NEURONAL CEROID-LIPOFUSCINOSISMARKLUND SL; SANTAVUORI P; WESTERMARCK T et al.1981; CLIN. CHIM. ACTA; ISSN 0009-8981; NLD; DA. 1981; VOL. 116; NO 2; PP. 191-198; BIBL. 24 REF.Article

RECENT FINDINGS ON SOME "NEW" NEUROMETABOLIC DISEASES.PALO J; SANTAVUORI P; HALTIA M et al.1976; RIV. PATOL. NERV. MENTALE; ITAL.; DA. 1976 PARU 1977; VOL. 97; NO 4; PP. 191-198; ABS. ITAL.; BIBL. 20 REF.Article

A HISTOCHEMICAL AND ULTRASTRUCTURAL STUDY OF STORED MATERIAL IN NEURONAL CEROID LIPOFUSCINOSISELLEDER M.1978; VIRCHOWS ARCH., B; DEU; DA. 1978; VOL. 28; NO 2; PP. 167-178; BIBL. 2 P.Article

IDENTIFICATION OF RETINOYL COMPLEXES AS THE AUTOFLUORESCENT COMPONENT OF THE NEURONAL STORAGE MATERIAL IN BATTEN DISEASE.WOLFE LS; NG YING KIN NMK; BAKER RR et al.1977; SCIENCE; U.S.A.; DA. 1977; VOL. 195; NO 4284; PP. 1360-1362; BIBL. 17 REF.Article

THE DIAGNOSIS OF INFANTILE GENERALIZED CEROID-LIPOFUSCINOSIS (TYPE HAGBERG-SANTAVUORI) USING SKIN BIOPSY.CEUTERICK C; MARTIN JJ; CASAER P et al.1976; NEUROPAEDIATRIE; DTSCH.; DA. 1976; VOL. 7; NO 3; PP. 250-260; ABS. FR.; BIBL. 25 REF.Article

ULTRASTRUCTURAL INVESTIGATIONS OF PERIPHERAL NERVES IN NEURONAL CEROID-LIPOFUSCINOSES (NCL).GOEBEL HH; ZEMAN W; PILZ H et al.1976; J. NEUROL.; GERM.; DA. 1976; VOL. 213; NO 4; PP. 295-303; ABS. ALLEM.; BIBL. 20 REF.Article

NEURONAL CEROID-LIPOFUSCINOSIS: ULTRASTRUCTURAL STUDY OF LYMPHOCYTIC DENSE BODIESAGUAS AP; MOURA NUNES JF; HASSE FERREIRA AD et al.1980; NEUROLOGY; ISSN 0028-3878; USA; DA. 1980; VOL. 30; NO 9; PP. 976-980; BIBL. 42 REF.Article

LATE INFANTILE NEURONAL STORAGE DISEASE WITH CURVILINEAR BODIES. SYSTEMIC PATHOLOGIC STUDIESDE BAECQUE CM; POLLACK MA; SUZUKI K et al.1976; ARCH. PATHOL. LAB. MED.; U.S.A.; DA. 1976; VOL. 100; NO 3; PP. 139-144; BIBL. 33 REF.Article

SO-CALLED NEURONAL CEROID-LIPOFUSCINOSIS. HISTOCHEMICAL STUDY WITH EVIDENCE OF EXTRATIBILITY OF THE STORED MATERIAL.ELLEDER M.1977; ACTA NEUROPATHOL.; ALLEM.; DA. 1977; VOL. 38; NO 2; PP. 117-122; BIBL. 38 REF.Article

THE ULTRASTRUCTURAL CHARACTERISTICS OF THE ABNORMAL CYTOSOMES IN BATTEN-KUF'S DISEASE.CARPENTER S; KARPATI G; ANDERMANN F et al.1977; BRAIN; G.B.; DA. 1977; VOL. 100; NO 1; PP. 137-156; BIBL. 3 P.Article

JUVENILE AMAUROTIC IDIOCY (NEURONAL CEROID LIPOFUSCINOSIS) AND LYMPHOCYTE FINGERPRINT PROFILESBAUMANN RJ; MARKESBERY WR.1978; ANN. NEUROL.; USA; DA. 1978; VOL. 4; NO 6; PP. 531-536; BIBL. 17 REF.Article

APPORT DE LA MICROSCOPIE ELECTRONIQUE DANS LE DIAGNOSTIC DES AFFECTIONS MUSCULAIRESCOQUET M; BIOULAC P; VITAL C et al.1978; BORDEAUX MED.; FRA; DA. 1978; VOL. 11; NO 20; PP. 1751-1755; ABS. ENG; BIBL. 13 REF.Article

DECREASED ERYTHOCYTE GLUTATHIONE PEROXIDASE ACTIVITY IN NEURONAL CEROID LIPOFUSCINOSIS (NCL)-CORRECTED WITH SELENIUM SUPPLEMENTATION.WESTERMARCK T; SANDHOLM M.1977; ACTA PHARMACOL. TOXICOL.; DANEM.; DA. 1977; VOL. 40; NO 1; PP. 70-74; BIBL. 17 REF.Article

JUVENILE BATTEN'S DISEASE: AN OPHTHALMOLOGICAL ASSESSMENT OF 26 PATIENTSSPALTON DJ; TAYLOR DSI; SANDERS MD et al.1980; BR. J. OPHTHALMOL.; ISSN 0007-1161; GBR; DA. 1980; VOL. 64; NO 10; PP. 726-732; BIBL. 17 REF.Article

INTERET DE L'ETUDE ULTRASTRUCTURALE DES BIOPSIES CUTANEE ET MUSCULAIRE DANS LES MALADIES DE SURCHARGE CONGENITALES A PROPOS DE 18 CASBIOULAC P; COQUET M; FONTAN D et al.1980; ANN. DERMATOL. VENEREOL.; FRA; DA. 1980; VOL. 107; NO 3; PP. 137-148; ABS. ENG; BIBL. 33 REF.Article

LATE-INFANTILE NEURONAL CEROID-LIPOFUSCINOSIS. AN ULTRASTRUCTURAL STUDY OF LYMPHOCYTE INCLUSIONS.MARKESBERY WR; SHIELD LK; EGEL RT et al.1976; ARCH. NEUROL.; U.S.A.; DA. 1976; VOL. 33; NO 9; PP. 630-635; BIBL. 43 REF.Article

NEURONAL CEROID LIPOFUSCINOSIS AND ARTHROPATHY: A FAMILY STUDYPROOPS R; GREEN SR.1981; J. MED. GENET.; ISSN 0022-2593; GBR; DA. 1981; VOL. 18; NO 2; PP. 101-104; BIBL. 10 REF.Article

ELECTRON MICROSCOPY OF SKIN AND PERIPHERAL BLOOD LYMPHOCYTES IN INFANTILE (SANTAVUORI) NEURONAL CEROID LIPOFUSCINOSISHAYNES ME; MANSON JI; CARTER RF et al.1979; NEUROPAEDIATRIE; DEU; DA. 1979; VOL. 10; NO 3; PP. 245-263; BIBL. 25 REF.Article

SERUM FATTY ACIDS AND PEROXIDASE ABNORMALITIES IN BATTEN'S DISEASESHUKLA VKS; JENSEN GE; CLAUSEN J et al.1978; RES. EXPER. MED.; DEU; DA. 1978; VOL. 173; NO 1; PP. 27-34; BIBL. 36 REF.Article

CLINICAL, ELECTROPHYSIOLOGICAL AND PATHOLOGICAL FEATURES OF THREE CASES OF CEREBROMACULAR DEGENERATION IN CHILDHOODMANSON JI; CARTER RF; HAYNES ME et al.1977; PROC. AUSTRAL. ASS. NEUROLOGISTS; AUS; DA. 1977 PUBL. 1978; VOL. 14; PP. 137-141; BIBL. 11 REF.Article

EEG-BEFUNDE IM VERLAUFE PROGREDIENTER HIRNERKRANKUNGEN IM KINDESALTER. = LES DONNEES DE L'ELECTROENCEPHALOGRAMME AU COURS DES AFFECTIONS CEREBRALES PROGRESSIVES CHEZ L'ENFANTEGGERS C; LEDERER H; SCHEFFNER D et al.1977; MONATSSCHR. KINDERHEILKDE; DTSCH.; DA. 1977; VOL. 125; NO 1; PP. 8-15; ABS. ANGL.; BIBL. 20 REF.Article

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