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kw.\*:("COCKAYNE SYNDROME")

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THE RECOVERY OF COLONNY-FORMING ABILITY AND THE RATE OF SEMI-CONSERVATIVE DNA SYNTHESIS IN ULTRAVIOLET-IRRADIATED COCKAYNE AND NORMAL HUMAN CELLSIKENAGA M; INOUE M; KOZUKA T et al.1981; MUTAT. RES.; ISSN 0027-5107; NLD; DA. 1981; VOL. 91; NO 1; PP. 87-91; BIBL. 14 REF.Article

GENETIC COMPLEMENTATION GROUPS IN COCKAYNE SYNDROMETANAKA K; KAWAI K; KUMAHARA Y et al.1981; SOMATIC CELL GENET.; ISSN 0098-0366; USA; DA. 1981; VOL. 7; NO 4; PP. 445-455; BIBL. 19 REF.Article

IDENTICAL MALE TWINS AND BROTHER WITH COCKAYNE SYNDROMEHOUSTON CS; ZALESKI WA; ROZDILSKY B et al.1982; AM. J. MED. GENET.; ISSN 0148-7299; USA; DA. 1982; VOL. 13; NO 2; PP. 211-223; BIBL. 3 P.Article

UNUSUAL SENSITIVITY OF TWO COCKAYNE'S SYNDROME CELL STRAINS TO BOTH UV AND GAMMA IRRADIATIONDESCHAVANNE PJ; DIATLOFF ZITO C; MACIEIRA COELHO A et al.1981; MUTAT. RES.; ISSN 0027-5107; NLD; DA. 1981; VOL. 91; NO 4-5; PP. 403-406; BIBL. 16 REF.Article

THREE COMPLEMENTATION GROUPS IN COCKAYNE SYNDROMELEHMANN AR.1982; MUTAT. RES.; ISSN 0027-5107; NLD; DA. 1982; VOL. 106; NO 2; PP. 347-356; BIBL. 21 REF.Article

A DEFICIENCY IN THE REPAIR OF UV ANC GAMMA -RAY DAMAGED DNA IN FIBROBLASTS FROM COCKAYNE'S SYBDROMERAINBOW AJ; HOWES M.1982; MUTAT. RES.; ISSN 0027-5107; NLD; DA. 1982; VOL. 93; NO 1; PP. 235-247; BIBL. 41 REF.Article

DECREASED HOST CELL REACTIVATION OF UV-IRRADIATED ADENOVIRUS 5 BY FIBROBLASTS FROM COCKAYNE'S SYNDROME PATIENTSDAY RS III; ZIOLKOWSKI HJ; DIMATTINA M et al.1981; PHOTOCHEM. PHOTOBIOL.; ISSN 0031-8655; GBR; DA. 1981; VOL. 34; NO 5; PP. 603-607; BIBL. 18 REF.Article

SENSITIVITY OF EXCISION REPAIR IN NORMAL HUMAN, XERODERMA PIGMENTOSUM VARIANT AND COCKAYNE'S SYNDROME FIBROBLASTS TO INHIBITION BY CYTOSINE ARABINOSIDECLEAVER JE.1981; J. CELL. PHYSIOL.; ISSN 0021-9541; USA; DA. 1981; VOL. 108; NO 2; PP. 163-173; BIBL. 2 P.Article

HOST-CELL REACTIVATION OF UV-IRRADIATED ADENOVIRUS IN COCKAYNE SYNDROMEHOAR DI; DAVIS F.1979; MUTATION RES.; NLD; DA. 1979; VOL. 62; NO 3; PP. 401-405; BIBL. 15 REF.Article

U.V. ENHANCED REACTIVATION OF U.V. AND GAMMA -IRRADIATED ADENOVIRUS IN COCKAYNE SYNDROME AND XERODERMA PIGMENTOSUM FIBROBLASTSJEEVES WP; RAINBOW AJ.1983; INTERNATIONAL JOURNAL OF RADIATION BIOLOGY & RELATED STUDIES IN PHYSICS, CHEMISTRY & MEDICINE; ISSN 0020-7616; GBR; DA. 1983; VOL. 43; NO 6; PP. 625-647; BIBL. 2 P.Article

DAS COCKAYNESCHE SYNDROM. = LE SYNDROME DE COCKAYNEBREZINA Z; DOCKALOVA M.1976; KINDERAERZTL. PRAXIS; DTSCH.; DA. 1976; VOL. 44; NO 6; PP. 259-262Article

COCKAYNE'S SYNDROME. ANOTHER CAUSE OF DIFFICULT INTUBATIONCOOK S.1982; ANAESTHESIA; ISSN 0003-2409; GBR; DA. 1982; VOL. 37; NO 11; PP. 1104-1107; BIBL. 2 REF.Article

NORMAL RECONSTRUCTION OF DNA SUPERCOILING AND CHROMATIN STRUCTURE IN COCKAYNE SYNDROME CELLS DURING REPAIR OF DAMAGE FROM ULTRAVIOLET LIGHTCLEAVER JE.1982; AMERICAN JOURNAL OF HUMAN GENETICS; ISSN 0002-9297; USA; DA. 1982; VOL. 34; NO 4; PP. 566-575; BIBL. 35 REF.Article

THE SPECTRUM OF X-RAY MANIFESTATIONS IN COCKAYNE'S SYNDROMEBENSMAN A; FAURE C; KAUFMANN HJ et al.1981; SKELET. RADIOL.; ISSN 0364-2348; DEU; DA. 1981; VOL. 7; NO 3; PP. 173-177; BIBL. 10 REF.Article

CANCER-ASSOCIATED HUMAN GENETIC DISEASES WITH DEFECTS IN DNA REPAIRLEHMANN AR.1981; Z. KREBSFORSCH. KLIN. ONKOL.; ISSN 0084-5353; DEU; DA. 1981; VOL. 100; NO 2; PP. 117-124; BIBL. 2 P.Article

INCREASED SENSITIVITY OF CELL STRAINS FROM COCKAYNE'S SYNDROME TO SISTER-CHROMATID-EXCHANGE INDUCTION AND CELL KILLING BY UV LIGHTMARSHALL RR; ARLETT CF; HARCOURT SA et al.1980; MUTATION RES.; NLD; DA. 1980; VOL. 69; NO 1; PP. 107-112; BIBL. 22 REF.Article

COCKAYNE SYNDROME: CLINICAL STUDY OF TWO PATIENTS AND NEUROPATHOLOGIC FINDINGS IN ONE.SUGARMAN GI; LANDING BH; REED WB et al.1977; CLIN. PEDIATR.; U.S.A.; DA. 1977; VOL. 16; NO 3; PP. 225-232; BIBL. 24 REF.Article

An integrated mechanistic model for transcription-coupled nucleotide excision repairPATEL, Shwetal; VENKATESH, K. V; EDWARDS, Jeremy S et al.DNA repair. 2004, Vol 3, Num 3, pp 343-348, issn 1568-7864, 6 p.Article

NEW FORMS OF DISEASES WITH DNA REPAIR DEFECTSROBBINS JH.1979; PHOTOCHEM. AND PHOTOBIOL.; GBR; DA. 1979; VOL. 30; NO 6; PP. 739-741; BIBL. 28 REF.Article

EXCISION REPAIR IN ATAXIA TELANGIECTASIA, FANCONI'S ANEMIA, COCKAYNE SYNDROME, AND BLOOM'S SYNDROME AFTER TREATMENT WITH ULTRAVIOLET RADIATION AND N-ACETOXY-2-ACETYLAMINOFLUORENEAHMED FE; SETLOW RB.1978; BIOCHIM. BIOPHYS. ACTA; NLD; DA. 1978; VOL. 521; NO 2; PP. 805-817; BIBL. 37 REF.Article

LA SINDROME DI COCKAYNE. (STUDIO DI DUE CASI). = LE SYNDROME DE COCKAYNE. ETUDE DE DEUX CAS)LANZI G; CALLIGARO A; DANESINO C et al.1976; MINERVA PEDIATR.; ITAL.; DA. 1976; VOL. 28; NO 26; PP. 1597-1608; ABS. ANGL.; BIBL. 39 REF.Article

HUMAN DISORDERS SHOWING INCREASED SENSITIVITY TO THE INDUCTION OF GENETIC DAMAGEARLETT CF; LEHMANN AR.1978; ANNU. REV. GENET.; USA; DA. 1978; VOL. 12; PP. 95-115; BIBL. 125 REF.Article

LE SYNDROME DE COCKAYNE. UNE ENTITE RADIOLOGIQUE. A PROPOS DE DEUX OBSERVATIONS FAMILIALES.BENSMAN A; BRAUNER M; TEBOUL FAURE L et al.1978; J. RADIOL. ELECTROL. MED. NUCL.; FRA; DA. 1978; VOL. 59; NO 6-7; PP. 375-380; ABS. ENG; BIBL. 17 REF.Article

SINDROME DI COCKAYNE. TRE CASI. = SYNDROME DE COCKAYNE. TROIS CASPELIZZA A; CORDONE G; GEMME G et al.1976; RADIOL. MED.; ITAL.; DA. 1976; VOL. 62; NO 4; PP. 265-274; ABS. ANGL.; BIBL. 32 REF.Article

Distinctive skeletal dysplasia in Cockayne syndromeCIRILLO SILENGO, M; FRANCESCHINI, P; BIANCO, R et al.Pediatric radiology. 1986, Vol 16, Num 3, pp 264-266, issn 0301-0449Article

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