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kw.\*:("DEFICIT HEREDITAIRE ENZYME HEMATIE")

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RED CELL ENZYME DEFICIENCIES AS A CAUSE OF HEMOLYTIC DISORDERS = LES DEFICIENCES DES ENZYMES ERYTHROCYTAIRES COMME CAUSE DE TROUBLES HEMOLYTIQUESVALENTINE WN.1972; ANNU. REV. MED.; U.S.A.; DA. 1972; VOL. 23; PP. 93-100; BIBL. 34REF.Serial Issue

DISORDERS DUE TO ENZYME DEFECTS IN THE RED BLOOD CELL = DESORDRES PROVOQUES PAR DES DEFICITS ENZYMATIQUES DANS LES GLOBULES ROUGESBEUTLER E.1972; ADV. METABOL. DISORD.; U.S.A.; DA. 1972; VOL. 6; PP. 131-160; BIBL. 6P.Serial Issue

THE HEREDITARY HEMOLYTIC ANAEMIAS. MEMBRANE AND ENZYME DEFECTS = LES ANEMIES HEMOLYTIQUES HEREDITAIRES: ANOMALIES DES MEMBRANES ET DES ENZYMESMILLER DR.1972; PEDIATR. CLIN. N. AMER.; U.S.A.; DA. 1972; VOL. 19; NO 4; PP. 865-887; BIBL. 3 P. 1/2Serial Issue

COMPLETE DEFICIENCY OF LEUKOCYTE GLUCOSE-6-PHOSPHATE DEHYDROGENASE WITH DEFECTIVE BACTERICIDAL ACTIVITY = DEFICIENCE COMPLETE DE G6PD LEUCOCYTAIRE AVEC ACTIVITE BACTERICIDE DEFECTUEUSE1972; J. CLINIC. INVEST.; U.S.A.; DA. 1972; VOL. 51; NO 4; PP. 769-778; BIBL. 1P.1/2Serial Issue

GLUCOSE-6-PHOSPHATE DEHYDROGENASE DEFICIENCYJAIN KK; CHOPRA PK.1972; INDIAN PEDIATR.; INDIA; DA. 1972; VOL. 9; NO 2; PP. 110-113; BIBL. 5REF.Serial Issue

L'INSUFFISANCE DE LA GLUCOSE PHOSPHATE-6 DESHYDROGENASE, L'UNE DES FORMES DE L'ANEMIE HEMOLYTIQUE. (REVUE DE LA LITTERATURE)TSIRKINA AS.1973; LAB. DELO; S.S.S.R.; DA. 1973; NO 4; PP. 221-223; BIBL. 45REF.Serial Issue

DETECTION OF GLUCOSE-PHOSPHATE ISOMERASE DEFICIENCY BY A SCREENING PROCEDURE = DETECTION DE LA DEFICIENCE DE GLUCOSE-PHOSPHATE ISOMERASE PAR UN PROCEDE DE DEPISTAGE1972; BLOOD; U.S.A.; DA. 1972; VOL. 39; NO 5; PP. 685-687; BIBL. 15REF.Serial Issue

AUTOMATED FLUOROMETRIC METHOD FOR SCREENING FOR ERYTHROCYTE GLUCOSE-6-PHOSPHATE DEHYDROGENASE DEFICIENCY = METHODE FLUORIMETRIQUE AUTOMATISEE POUR LA RECHERCHE DE LA DEFICIENCE DE G6PD ERYTHROCYTAIREDICKSON LG; JOHNSON CB; JOHNSON DR et al.1973; CLIN. CHEM.; U.S.A.; DA. 1973; VOL. 19; NO 3; PP. 301-303; BIBL. 6REF.Serial Issue

GLUCOSE VI. PHOSPHATE DEHYDROGENASE DEFICIENCY = DEFICIT EN GLUCOSE-6-PHOSPHATE DESHYDROGENASESISWADI I; HARSONO NOTOPURO; UNTARIO S et al.1972; PAEDIATR. INDONES.; INDONES.; DA. 1972; VOL. 12; NO 4; PP. 182-190; BIBL. 8REF.Serial Issue

STUDIES ON HUMAN ERYTHROCYTE NUCLEOTIDE METABOLISM. II. NONSPHEROCYTIC HEMOLYTIC ANEMIA, HIGH RED CELL ATP, AND RIBOSEPHOSPHATE PYROPHOSPHOKINASE (RPK, E.C. 2.7.6.1.) DEFICIENCY = ETUDE DU METABOLISME DES NUCLEOTIDES DES HEMATIES HUMAINES. II. ANEMIE HEMOLYTIQUE NON SPHEROCYTAIRE, AUGMENTATION DE L'ATP ERYTHROCYTAIRE ET DEFICIENCE DE RIBOSEPHOSPHATE PYROPHOSPHOKINASE (RPK, E.C. 2.7.6.1.)VALENTINE WN; ANDERSON HM; PAGLIA DE et al.1972; BLOOD; U.S.A.; DA. 1972; VOL. 39; NO 5; PP. 764-684; BIBL. 1P.1/2Serial Issue

G-6-PD HEMOLYTIC ANEMIA COMPLICATING DIABETIC KETOACIDOSIS = ANEMIE HEMOLYTIQUE G-6-PD COMPLIQUANT UNE ACIDO-CETOSE DIABETIQUEGELLADY AM; GREENWOOD RD.1972; J. PEDIATR.; U.S.A.; DA. 1972; VOL. 80; NO 6; PP. 1037-1038; BIBL. 10REF.Serial Issue

ANEMIES HEMOLYTIQUES PAR DEFICIT ENZYMATIQUE DU GLOBULE ROUGEBOYER C; BOIVIN P.1972; CONCOURS MED.; FR.; DA. 1972; VOL. 94; NO 39; PP. 6157-6162Serial Issue

DEFICIT FAMILIAL EN DIPHOSPHOGLYCERATE-MUTASE: ETUDE HEMATOLOGIQUE ET BIOCHIMIQUECARTIER P; LABIE D; LEROUX JP et al.1972; NOUV. REV. FR. HEMATOL.; FR.; DA. 1972; VOL. 12; NO 3; PP. 269-287; ABS. ANGL; BIBL. 65REF.Serial Issue

CLINICAL HETEROGENEITY OF ERYTHROCYTE PYRUVATE KINASE DEFICIENCY. EVIDENCE OF AN IMPAIRED UTILIZATION OF ATP IN A CLINICALLY SEVERE FORM = L'HETEROGENEITE CLINIQUE DU DEFICIT EN ERYTHROCYTE PYRUVATE KINASE. L'EVIDENCE D'UNE MAUVAISE UTILISATION DE L'ADENOSINE TRIPHOSPHATE DANS UNE FORME CLINIQUE SEVERESCHROETER W.1972; HELV. PAEDIATR. ACTA; SUISSE; DA. 1972; VOL. 27; NO 5; PP. 471-488; ABS. ALLEM.; BIBL. 2P.Serial Issue

HEMOLYTIC ANEMIA AND G6PD DEFICIENCY = ANEMIE HEMOLYTIQUE ET DEFICIENCE EN G6PDYOSHIDA A.1973; SUISSE; U.S.A.; DA. 1973; VOL. 179; NO 4073; PP. 532-537; BIBL. 44 REF.Serial Issue

GAMMA -GLUTAMYLCYSTEINE SYNTHETASE DEFICIENCY. A CAUSE OF HEREDITARY HEMOLYTIC ANEMIA = DEFICIT EN GAMMA -GLUTAMYLCYSTEINE SYNTHETASE. UNE CAUSE D'ANEMIE HEMOLYTIQUE HEREDITAIREKONRAD PN; RICHARDS F II; VALENTINE WN et al.1972; NEW ENGL. J. MED.; U.S.A.; DA. 1972; VOL. 286; NO 11; PP. 557-561; BIBL. 25 REF.Serial Issue

THE FOURTH CONFERENCE ON THE CLINICAL DELINEATION OF BIRTH DEFECTS. XIV. BLOOD. BALTIMORE, MD, JUNE 7-11, 19711972; BIRTH DEFECTS ORIGIN. ARTICLE SER.; U.S.A.; DA. 1972; VOL. 8; NO 3; PP. 1-209; H.T. 1; BIBL. DISSEM.Serial Issue

ANOMALIE DE LA GLUTATHION REDUCTASE DANS UNE FAMILLE ALGERIENNE (NOTE PRELIMINAIRE)VERGNES H; BIERME R; PRIS J et al.1972; NOUV. REV. FR. HEMATOL.; FR.; DA. 1972; VOL. 12; NO 4; PP. 564-567; BIBL. 8REF.Serial Issue

ACUTE REVERSIBLE RENAL FAILURE ASSOCIATED WITH GLUCOSE-6-PHOSPHATE-DEHYDROGENASE DEFICIENCY = DEFAILLANCE RENALE AIGUE REVERSIBLE ASSOCIEE A UNE DEFICIENCE EN GLUCOSE-6-PHOSPHATE-DESHYDROGENASEOWUSU SK; ADDY JH; FOLI AK et al.1972; LANCET; G.B.; DA. 1972; NO 7763; PP. 1255-1257; BIBL. 7REF.Serial Issue

HEMOLYTIC CRISES OF FAVISM IN SICILIAN FEMALES HETEROZYGOUS FOR G-6-PD DEFICIENCY = CRISES HEMOLYTIQUES DE FAVISME CHEZ DES FILLES SICILIENNES HETEROZYGOTES POUR LE DEFICIT EN G-6-PDRUSSO G; MOLLICA F; PAVONE L et al.1972; PEDIATRICS; U.S.A.; DA. 1972; VOL. 49; NO 6; PP. 854-859; BIBL. 22 REF.Serial Issue

ASPECTS BIOLOGIQUES ET GENETIQUES DU DEFICIT EN GLUCOSE-6 PHOSPHATE DESHYDROGENASE (G6PD): ENZYMOPENIE ET ENZYMOPATHIEDUHAMEL JF.1972; MED. INFANT.; FR.; DA. 1972; VOL. 79; NO 10; PP. 831-837; BIBL. 7REF.Serial Issue

ABSENCE OF GLUCOSE-6-PHOSPHATE DEHYDROGENASE IN RED CELLS OF AN AFRICAN = ABSENCE DE GLUCOSE-6-PHOSPHATE DESHYDROGENASE DANS LES HEMATIES D'UN AFRICAINOWUSU SK.1972; BRIT. MED. J.; G.B.; DA. 1972; NO 5831; PP. 25-26; BIBL. 14REF.Serial Issue

INCREASED ACTIVITY OF TWO ENZYMES OF PYRIMIDINE BIOSYNTHESIS DE NOVO IN ERYTHROCYTES FROM PATIENTS WITH THE LESCH-NYHAM SYNDROME = ACTIVITE ACCRUE DE DEUX ENZYMES DE LA BIOSYNTHESE DE NOVO DE LA PYRIMIDINE DANS LES ERYTHROCYTES DE SUJETS ATTEINTS DE SYNDROME DE LESCH-NYHAMBEARDMORE TD; MEADE JC; KELLEY WN et al.1973; J. LAB. CLIN. MED.; U.S.A.; DA. 1973; VOL. 81; NO 1; PP. 43-52; BIBL. 1P.Serial Issue

CHRONIC SEVERE HEMOLYTIC ANEMIA DUE TO G-6-PD CHARLESTON: A NEW DEFICIENT VARIANT = ANEMIE HEMOLYTIQUE CHRONIQUE SEVERE DUE A UNE G-6-PD CHARLESTON, UNE NOUVELLE VARIANTE DEFICITAIREBEUTLER E; GROOMS AM; MORGAN SK et al.1972; J. PEDIATR.; U.S.A.; DA. 1972; VOL. 80; NO 6; PP. 1005-1009; BIBL. 11REF.Serial Issue

CLINICAL AND BIOCHEMICAL INTERACTIONS OF GLUCOSE-6-PHOSPHATE DEHYDROGENASE DEFICIENCY AND SICKLE-CELL ANEMIA = INTERACTIONS CLINIQUES ET BIOCHIMIQUES ENTRE LE DEFICIT EN GLUCOSE PHOSPHATE-6 DESHYDROGENASE ET L'ANEMIE A HEMATIES FALCIFORMESPIOMELLI S; REINDORF CA; ARZANIAN MT et al.1972; NEW ENGL. J. MED.; U.S.A.; DA. 1972; VOL. 287; NO 5; PP. 213-217; BIBL. 18REF.Serial Issue

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