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ADVANCES IN THE TREATMENT OF INHERITED METABOLIC DISEASESDESNICK RJ; GRABOWSKI GA.1981; ADV. HUM. GENET.; ISSN 0065-275X; USA; DA. 1981; VOL. 11; PP. 281-369; BIBL. 376 REF.Article

PURIFICATION AND PROPERTIES OF DELTA -AMINOLEVULINATE DEHYDRASE FROM HUMAN ERYTHROCYTESANDERSON PM; DESNICK RJ.1979; J. BIOL. CHEM.; USA; DA. 1979; VOL. 254; NO 15; PP. 6924-6930; BIBL. 29 REF.Article

ENZYME THERAPY. DIFFERENTIAL IN VIVO RETENTION OF BOVINE HEPATIC, RENAL, AND SPLENIC BETA -GLUCURONIDASES AND EVIDENCE FOR ENZYME STABILIZATION BY INTERMOLECULAR EXCHANGE.FIDDLER MB; DESNICK RJ.1977; ARCH. BIOCHEM. BIOPHYS.; U.S.A.; DA. 1977; VOL. 179; NO 2; PP. 397-408; BIBL. 35 REF.Article

PURIFICATION AND PROPERTIES OF UROPORPHYRINOGEN I SYNTHASE FROM HUMAN ERYTHROCYTES. IDENTIFICATION OF STABLE ENZYME-SUBSTRATE INTERMEDIATESANDERSON PM; DESNICK RJ.1980; J. BIOL. CHEM.; USA; DA. 1980; VOL. 255; NO 5; PP. 1993-1999; BIBL. 25 REF.Article

ENZYME THERAPY. IX. STABILIZATION OF HUMAN SPLENIC ALPHA -GALACTOSIDASE A BY ZINC ION.THORPE SR; DESNICK RJ.1978; INTERNATION. J. BIOCHEM.; G.B.; DA. 1978; VOL. 9; NO 2; PP. 103-105; BIBL. 14 REF.Article

MOLECULAR PATHOLOGY OF FABRY'S DISEASE. PHYSICAL AND KINETIC PROPERTIES OF ALPHA -GALACTOSIDASE A IN CULTURED HUMAN ENDOTHELLIAL CELLS.JOHNSON DL; DESNICK RJ.1978; BIOCHIM. BIOPHYS. ACTA; PAYS-BAS; DA. 1978; VOL. 538; NO 2; PP. 195-204; BIBL. 31 REF.Article

DETERMINATION OF DELTA -AMINOLEVULINATE DEHYDRATASE ACTIVITY BY A SPECIFIC FLUOROMETRIC COUPLED-ENZYME ASSAYGIAMPIETRO PF; DESNICK RJ.1983; ANALYTICAL BIOCHEMISTRY; ISSN 0003-2697; USA; DA. 1983; VOL. 131; NO 1; PP. 83-92; BIBL. 32 REF.Article

PORPHOBILINOGEN DEAMINASE: METHODS AND PRINCIPLES OF THE ENZYMATIC ASSAYANDERSON PM; DESNICK RJ.1982; ENZYME; ISSN 0013-9432; CHE; DA. 1982; VOL. 28; NO 2-3; PP. 146-157; BIBL. 48 REF.Article

AFFINITY PURIFICATION OF ALPHA -GALACTOSIDASE A FROM HUMAN SPLEEN, PLACENTA, AND PLASMA WITH ELIMINATION OF PYROGEN CONTAMINATION: PROPERTIES OF THE PURIFIED SPLENIC ENZYME COMPARED TO OTHER FORMSBISHOP DF; DESNICK RJ.1981; J. BIOL. CHEM.; ISSN 0021-9258; USA; DA. 1981; VOL. 256; NO 3; PP. 1307-1316; BIBL. 50 REF.Article

A NEW CONTINUOUS, MONODIMENSIONAL ELECTROPHORETIC SYSTEM FOR THE SEPARATION AND QUANTITATION OF INDIVIDUAL GLYCOSAMINOGLYCANSSCHUCHMAN EH; DESNICK RJ.1981; ANAL. BIOCHEM.; ISSN 0003-2697; USA; DA. 1981; VOL. 117; NO 2; PP. 419-426; BIBL. 11 REF.Article

PUNCTATE LENTICULAR OPACITIES IN TYPE II MANNOSIDOSIS.LETSON RD; DESNICK RJ.1978; AMER. J. OPHTHALMOL.; U.S.A.; DA. 1978; VOL. 85; NO 2; PP. 218-224; BIBL. 23 REF.Article

ENZYME THERAPY. VI. COMPARATIVE IN VIVO FATES AND EFFECTS ON LYSOSOMAL INTEGRITY OF ENZYME ENTRAPPED IN NEGATIVELY AND POSITIVELY CHARGED LIPOSOMES.STEGER LD; DESNICK RJ.1977; BIOCHIM. BIOPHYS. ACTA; PAYS-BAS; DA. 1977; VOL. 464; NO 3; PP. 530-546; BIBL. 1 P.Article

ABBREVIATED PR INTERVAL IN MANNOSIDOSIS.MEHTA J; DESNICK RJ.1978; J. PEDIATR.; U.S.A.; DA. 1978; VOL. 92; NO 4; PP. 599-601; BIBL. 12 REF.Article

THE OCULAR MANIFESTATIONS IN FABRY'S DISEASESHER NA; LETSON RD; DESNICK RJ et al.1979; ARCH. OPHTHALMOL.; USA; DA. 1979; VOL. 97; NO 4; PP. 671-676; BIBL. 31 REF.Article

IMMUNOLOGICAL EVALUATION OF REPEATED ADMINISTRATION OF ERYTHROCYTE-ENTRAPPED PROTEIN TO C3H/MEJ MICE.FIDDLER MB; HUDSON LDS; DESNICK RJ et al.1977; BIOCHEM. J.; G.B.; DA. 1977; VOL. 168; NO 2; PP. 141-145; BIBL. 13 REF.Article

MANNOSIDOSIS: PATHOLOGY OF THE NERVOUS SYSTEM.JOO HO SUNG; HAYANO M; DESNICK RJ et al.1977; J. NEUROPATHOL. EXPER. NEUROL.; U.S.A.; DA. 1977; VOL. 36; NO 5; PP. 807-820; BIBL. 1 P. 1/2Article

TAY-SACHS DISEASE: AN IMPROVED, FULLY-AUTOMATED METHOD FOR HETEROZYGOTE IDENTIFICATION BY TEAR BETA -HEXOSAMINIDASE ASSAY.GOLDBERG JD; TRUEX JH; DESNICK RJ et al.1977; CLIN. CHIM. ACTA; PAYS-BAS; DA. 1977; VOL. 77; NO 1; PP. 43-52; BIBL. 12 REF.Article

CHARACTERIZATION OF HEX S, THE MAJOR RESIDUAL BETA HEXOSAMINIDASE ACTIVITY IN TYPE OGM2 GANGLIOSIDOSIS (SANDHOFF-JATZKEWITZ DISEASE).IKONNE JU; RATTAZZI MC; DESNICK RJ et al.1975; AMER. J. HUM. GENET.; U.S.A.; DA. 1975; VOL. 27; NO 5; PP. 639-650; BIBL. 2 P.Article

IN VIVO RECOGNITION OF MURINE TISSUE AND SERUM PROTEINS.FIDDLER MB; WOLD F; DESNICK RJ et al.1975; INTERNATION. J. BIOCHEM.; G.B.; DA. 1975; VOL. 6; NO 11; PP. 793-799; BIBL. 25 REF.Article

ACUTE MYELOGENOUS LEUKAEMIA IN HURLER' SYNDROME.CHEN KTK; MCKENNA RW; DESNICK RJ et al.1978; J. MED. GENET.; GBR; DA. 1978; VOL. 15; NO 3; PP. 239-242; BIBL. 13 REF.Article

TOWARD ENZYME THERAPY FOR LYSOSOMAL STORAGE DISEASEDESNICK RJ; THORPE SR; FIDDLER MB et al.1976; PHYSIOL. REV.; U.S.A.; DA. 1976; VOL. 56; NO 1; PP. 57-99; BIBL. 5 P. 1/2Article

ELECTROPHORETIC SEPARATION OF NEUTRAL AND ACID BETA -GLUCOSIDASE ISOZYMES IN HUMAN TISSUESSHAFIT ZAGARDO B; DEVINE EA; DESNICK RJ et al.1980; BIOCHIM. BIOPHYS. ACTA; NLD; DA. 1980; VOL. 614; NO 2; PP. 459-465; BIBL. 16 REF.Article

GLUTAMATE DEHYDROGENASE DEFICIENCY IN THREE PATIENTS WITH SPINOCEREBELLAR SYNDROMEPLAITAKIS A; NICKLAS WJ; DESNICK RJ et al.1980; ANN. NEUROL.; USA; DA. 1980; VOL. 7; NO 4; PP. 297-303; BIBL. 34 REF.Article

ENZYME THERAPY. X: IMMUNE RESPONSE INDUCED BY ENZYME- AND BUFFER-LOADED LIPOSOMES IN C3H/HEJ GUSH MICEHUDSON LDS; FIDDLER MB; DESNICK RJ et al.1979; J. PHARMACOL. EXPER. THERAPEUT.; USA; DA. 1979; VOL. 208; NO 3; PP. 507-514; BIBL. 2 P.Article

FLUOROMETRIC COUPLED-ENZYME ASSAY FOR DELTA-AMINOLEVULINATE SYNTHASEBISHOP DF; MCBRIDE L; DESNICK RJ et al.1982; ENZYME; ISSN 0013-9432; CHE; DA. 1982; VOL. 28; NO 2-3; PP. 94-108; BIBL. DISSEM.Article

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