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kw.\*:("ENCEPHALOMYELOPATHIE NECROSANTE SUBAIGUE LEIGH")

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ENCEFALOPATIA DI WERNICKE IN BAMBINI CARDIOPATICI = ENCEPHALOPATHIE DE WERNICK CHEZ LES ENFANTS CARDIOPATHESGUILOTTA F.1976; ACTA NEUROL.; ITAL.; DA. 1976; VOL. 31; NO 1; PP. 71-73; ABS. ANGL.; BIBL. 12 REF.Article

SPECIFICITY OF THE URINE INHIBITOR TEST FOR LEIGH'S DISEASEPINCUS JH; COOPER JR; PIROS K et al.1974; NEUROLOGY; U.S.A.; DA. 1974; VOL. 24; NO 9; PP. 885-890; BIBL. 15REF.Article

Encéphalopathie nécrosante subaiguë, maladie de Leigh: à propos d'un cas = Subacute necrotizing encephalopathy (Leigh's disease). Case reportDELISLE, M. B; NETTER, J. C; PEYRILLE, F et al.Annales de pathologie (Paris). 1985, Vol 5, Num 4-5, pp 313-317, issn 0242-6498Article

BEITRAG ZUR SUBAKUTEN NEKROTISIERENDEN ENZEPHALOMYELOPATHIE (LEIGH-SYNDROM) = CONTRIBUTION A L'ENCEPHALOMYELOPATHIE NECROSANTE SUBAIGUE (SYNDROME DE LEIGH)BARZ H; HENKER J.1975; ZBL. ALLG. PATHOL. PATHOL. ANAT.; DTSCH.; DA. 1975; VOL. 119; NO 6; PP. 488-494; ABS. ANGL.; BIBL. 20 REF.Article

SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY. RAPIDLY FATAL COURSE OF LEIGH DISEASE IN A 5-YEAR-OLD CHILD = L'ENCEPHALOMYELOPATHIE NECROSANTE SUBAIGUE. EVOLUTION RAPIDEMENT MORTELLE D'UNE MALADIE DE LEIGH CHEZ UN ENFANT DE 5ANSEISENGART MA; POWERS JM; ROSE AL et al.1974; AMER. J. DIS. CHILD.; U.S.A.; DA. 1974; VOL. 127; NO 5; PP. 730-732; BIBL. 15REF.Article

SUR LA DELIMITATION CLINICOPATHOLOGIQUE DE L'ENCEPHALOPATHIE DE GAYET-WERNICKE ET DE LA FORME ADULTE DE L'ENCEPHALOPATHIE DE LEIGHMARTIN JJ.1972; ACTA NEUROL. BELG.; BELG.; DA. 1972; VOL. 72; NO 5; PP. 347-354; ABS. ANGL. ALLEM.; BIBL. 12REF.Serial Issue

COMPUTERIZED TOMOGRAPHY IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY (LEIGH DISEASE)SCHWARTZ WJ; HUTCHISON HT; BERG BO et al.1981; ANN. NEUROL.; ISSN 0364-5134; USA; DA. 1981; VOL. 10; NO 3; PP. 268; BIBL. 6 REF.Article

RILIEVI SU UN CASO DI ENCEFALOPATIA SUBACUTA NECROTIZZANTE INFANTILE (ENCEFALITE DI LEIGH) CON CISTINURIA MATERNA = SUR UN CAS D'ENCEPHALOPATHIE SUBAIGUE NECROSANTE INFANTILE (ENCEPHALITE DE LEIGH) AVEC CYSTINURIE MATERNELLEMARCUCCI F; COTTARDO F; MONALDI B et al.1975; CLIN. PEDIATR.; ITAL.; DA. 1975; VOL. 57; NO 7; PP. 308-317; ABS. ANGL.; BIBL. 14 REF.Article

Chronic relapsing course of encephalomyeloradiculopathy in a 6-year-old boyRIIKONEN, R; DONNER, M.Neuropediatrics. 1987, Vol 18, Num 4, pp 235-238, issn 0174-304XArticle

LEIGH'S SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY: POSSIBLE DIAGNOSIS BY CT SCANCHI JG; HAN WOOK YOO; KI KYUN CHANG et al.1981; NEURORADIOLOGY; ISSN 0028-3940; DEU; DA. 1981; VOL. 22; NO 3; PP. 141-144; BIBL. 10 REF.Article

PERIPHERAL NEUROPATHY IN LEIGH'S ENCEPHALOMYELOPATHY = POLYNEVRITE PERIPHERIQUE DANS L'ENCEPHALOMYELOPATHIE DE LEIGHMOOSA A.1975; DEVELOP. MED. CHILD NEUROL.; G.B.; DA. 1975; VOL. 17; NO 5; PP. 621-624; ABS. FR. ALLEM. ESP.; BIBL. 13 REF.Article

LEIGH DISEASE, BIOCHEMICAL CHARACTERISTICS OF THE INHIBITOR = MALADIE DE LEIGH. CARACTERISTIQUES BIOCHIMIQUES DE L'INHIBITEURMURPHY JV; CRAIG LJ; GLEW RH et al.1974; ARCH. NEUROL.; U.S.A.; DA. 1974; VOL. 31; NO 4; PP. 220-227; BIBL. 21REF.Article

The adult form of subacute necrotizing encephalopathyHEGEDUS, K; NEMETH, G.Surgical neurology. 1984, Vol 21, Num 6, pp 572-576, issn 0090-3019Article

MITOCHONDRIAL CYTOPATHY OR LEIGH'S SYNDROME. MITOCHONDRIAL ABNORMALITIES IN SPONGIFORM ENCEPHALOPATHIESEGGER J; WYNNE WILLIAMS CJE; ERDOHAZI M et al.1982; NEUROPEDIATRICS; ISSN 0174-304X; DEU; DA. 1982; VOL. 13; NO 4; PP. 219-224; BIBL. 46 REF.Article

STUDIES ON PYRUVATE CARBOXYLASE, PYRUVATE DECARBOXYLASE AND LIPOAMIDE DEHYDROGENASE IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHYHANSEN TL; CHRISTENSEN E; BRANDT NJ et al.1982; ACTA PAEDIATR. SCAND.; ISSN 0001-656X; SWE; DA. 1982; VOL. 71; NO 2; PP. 263-267; BIBL. 30 REF.Article

CHRONIC LEIGH DISEASE: A GENETIC AND BIOCHEMICAL STUDYPLAITAKIS A; WHETSELL O JR; COOPER JR et al.1980; ANN. NEUROL.; USA; DA. 1980; VOL. 7; NO 4; PP. 304-310; BIBL. 25 REF.Article

X-LINKED LEIGH'S SYNDROMEBENKE PJ; PARKER JC JR; LUBS ML et al.1982; HUMAN GENETICS; ISSN 0340-6717; DEU; DA. 1982; VOL. 62; NO 1; PP. 53-59; BIBL. 58 REF.Article

PYRUVATE CARBOXYLASE DEFICIENCY: AN ALLEGED BIOCHEMICAL CAUSE OF LEIGH'S DISEASEMURPHY JV; ISOHASHI F; WEINBERG MB et al.1981; PEDIATRICS EVANSTON; ISSN 0031-4005; USA; DA. 1981; VOL. 68; NO 3; PP. 401-404; BIBL. 29 REF.Article

MOTOR NERVE CONDUCTION VELOCITIES IN LEIGH'S ENCEPHALOMYELOPATHY.MOOSA A.1978; ARCH. DIS. CHILDH.; G.B.; DA. 1978; VOL. 53; NO 1; PP. 62-65; BIBL. 13 REF.Article

BEITRAG ZUR SUBAKUTEN NEKROTISIERENDEN ENZEPHALOMYELOPATHIE (LEIGH-SYNDROM). = CONTRIBUTIONS A L'ETUDE DE L'ENCEPHALOMYELOPATHIE NECROSANTE SUBAIGUE (SYNDROME DE LEIGH)HENKER J; BARZ H; BOHME B et al.1977; KINDERAERZTL. PRAXIS; DTSCH.; DA. 1977; VOL. 45; NO 3; PP. 121-124; BIBL. 14 REF.Article

SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY IN A NEONATAL INFANT.FEIGIN I; HYO SOON KIM.1977; J. NEUROPATHOL. EXPER. NEUROL.; U.S.A.; DA. 1977; VOL. 36; NO 2; PP. 364-372; BIBL. 20 REF.Article

A PROPOS DE 2 OBSERVATIONS FAMILIALES DE SYNDROME DE LEIGH.DELGADO JL.1978; MONTPELLIER; QUICK PRINT; DA. 1978; PP. (80P.); H.T. 12; BIBL. 10 P.; (THESE DOCT. MED.; MONTPELLIER)Thesis

FURTHER OBSERVATIONS ON SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY IN ADULTS.FEIGIN I; BUDZILOVICH GN.1977; J. NEUROPATHOL. EXPER. NEUROL.; U.S.A.; DA. 1977; VOL. 36; NO 1; PP. 128-139; BIBL. 1 P. 1/2Article

THIAMINE TRIPHOSPHATE LEVELS AND HISTOPATHOLOGY. CORRELATION IN LEIGH DISEASE.PINCUS JH; SOLITARE GB; COOPER JR et al.1976; ARCH. NEUROL.; U.S.A.; DA. 1976; VOL. 33; NO 11; PP. 759-763; BIBL. 20 REF.Article

THE CORTICAL FORM OF SUBACUTE NECROTIZING ENCEPHALOPATHY OF THE LEIGH TYPE. A LIGHT- AND ELECTRON-MICROSCOPIC STUDY = LA FORME CORTICALE DE L'ENCEPHALOPATHIE NECROSANTE SUBAIGUE TYPE LEIGH. ETUDE AUX MICROSCOPES PHOTONIQUE ET ELECTRONIQUEVUIA O.1975; J. NEUROL. SCI.; NETHERL.; DA. 1975; VOL. 26; NO 3; PP. 295-304; BIBL. 15 REF.Article

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