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MORPHOLOGIC AND IMMUNOPATHOLOGIC FINDINGS IN MYASTHENIA GRAVIS AND IN CONGENITAL MYASTHENIC SYNDROMESENGEL AG.1980; J. NEUROL. NEUROSURG. PSYCHIATRY; ISSN 0022-3050; GBR; DA. 1980; VOL. 43; NO 7; PP. 577-589; BIBL. 24 REF.Article

NEUROMUSCULAR MANIFESTATIONS OF GRAVES' DISEASE = MANIFESTATIONS NEUROMUSCULAIRES DE LA MALADIE DE BASEDOWENGEL AG.1972; MAYO CLIN. PROC.; U.S.A.; DA. 1972; VOL. 47; NO 12; PP. 919-925; BIBL. 53REF.Article

PRIMARY SYSTEMIC CARNITINE DEFICIENCY. I: CARNITINE BIOSYNTHESISREBOUCHE CJ; ENGEL AG.1981; NEUROLOGY; ISSN 0028-3878; USA; DA. 1981; VOL. 31; NO 7; PP. 813-818; BIBL. 28 REF.Article

SIGNIFICANCE OF RENAL GAMMA -BUTYROBETAINE HYDROXYLASE FOR CARNITINE BIOSYNTHESIS IN MANREBOUCHE CJ; ENGEL AG.1980; J. BIOL. CHEM.; ISSN 0021-9258; USA; DA. 1980; VOL. 255; NO 18; PP. 8700-8705; BIBL. 40 REF.Article

COMPLEMENT ACTIVATION IN MUSCLE FIBER NECROSIS: DEMONSTRATION OF THE MEMBRANE ATTACK COMPLEX OF COMPLEMENT IN NECROTIC FIBERSENGEL AG; BIESECKER G.1982; ANN. NEUROL.; ISSN 0364-5134; USA; DA. 1982; VOL. 12; NO 3; PP. 289-296; BIBL. 44 REF.Article

TISSUE DISTRIBUTION OF CARNITINE BIOSYNTHETIC ENZYMES IN MANREBOUCHE CJ; ENGEL AG.1980; BIOCHIM. BIOPHYS. ACTA; NLD; DA. 1980; VOL. 630; NO 1; PP. 22-29; BIBL. 22 REF.Article

DUCHENNE DYSTROPHY: ELECTRON MICROSCOPIC FINDINGS POINTING TO A BASIC OR EARLY ABNORMALITY IN THE PLASMA MEMBRANE OF THE MUSCLE FIBER = DYSTROPHIE DE DUCHENNE: RESULTATS DE LA MICROSCOPIE ELECTRONIQUE MONTRANT UNE ANOMALIE FONDAMENTALE OU PRECOCE DE LA MEMBRANE PLASMIQUE DES FIBRES MUSCULAIRESBAHRAM MOKRI; ENGEL AG.1975; NEUROLOGY; U.S.A.; DA. 1975; VOL. 25; NO 12; PP. 1111-1120; BIBL. 20 REF.Article

CARNITINE TRANSPORT IN CULTURED MUSCLE CELLS AND SKIN FIBROBLASTS FROM PATIENTS WITH PRIMARY SYSTEMIC CARNITINE DEFICIENCYREBOUCHE CJ; ENGEL AG.1982; IN VITRO; ISSN 0073-5655; USA; DA. 1982; VOL. 18; NO 5; PP. 495-500; BIBL. 22 REF.Article

EXPERIMENTAL LIPID STORAGE MYOPATHY. A QUANTITATIVE ULTRASTRUCTURAL AND BIOCHEMICAL STUDY.BROWNELL AKW; ENGEL AG.1978; J. NEUROL. SCI.; NETHERL.; DA. 1978; VOL. 35; NO 1; PP. 31-41; BIBL. 1 P.Article

INTRACELLULAR CALCIUM CALCIUM ACCUMULATION IN DUCHENNE DYSTROPHY AND OTHER MYOPATHIES: A STUDY OF 567,000 MUSCLE FIBERS IN 114 BIOPSIES.BODENSTEINER JB; ENGEL AG.1978; NEUROLOGY; U.S.A.; DA. 1978; VOL. 28; NO 5; PP. 439-446; BIBL. 15 REF.Article

EFFECTS OF MICROEMBOLIZATION OF THE SKELETAL MUSCLE BLOOD FLOW. A CRITIQUE OF THE MICROVASCULAR OCCLUSION MODEL OF DUCHENNE DYSTROPHY = EFFETS DE LA MICROEMBOLISATION DE LA CIRCULATION DANS LE MUSCLE SQUELETTIQUE. UNE CRITIQUE DU TYPE D'OCCLUSION MICROVASCULAIRE DANS LA DYSTROPHIE DE DUCHENNEBOYSEN G; ENGEL AG.1975; ACTA NEUROL. SCAND.; DANEM.; DA. 1975; VOL. 52; NO 1; PP. 71-80; BIBL. 14 REF.Article

LIPID STORAGE MYOPATHY RESPONSIVE TO PREDNISONE = MYOPATHIE A DEPOTS LIPIDIQUES SENSIBLE A LA DELTA -CORTISONEENGEL AG; SIEKERT RG.1972; ARCH. NEUROL.; U.S.A.; DA. 1972; VOL. 27; NO 2; PP. 174-181; BIBL. 21 REF.Serial Issue

ACID MALTASE DEFICIENCY IN ADULTS PRESENTING AS RESPIRATORY FAILUREROSENOW EC III; ENGEL AG.1978; AMER. J. MED.; USA; DA. 1978; VOL. 64; NO 3; PP. 485-491; BIBL. 25 REF.Article

SYSTEMIC CARNITINE DEFICIENCY SIMULATING RECURRENT REYE SYNDROMEGLASGOW AM; ENG G; ENGEL AG et al.1980; J. PEDIATR.; USA; DA. 1980; VOL. 96; NO 5; PP. 889-891; BIBL. 7 REF.Article

MOTOR END-PLATE FINE STRUCTURE IN ACRYLAMIDE DYING-BACK NEUROPATHY: A SEQUENTIAL MORPHOMETRIC STUDYTSUJIHATA M; ENGEL AG; LAMBERT EH et al.1974; NEUROLOGY; U.S.A.; DA. 1974; VOL. 24; NO 9; PP. 849-856; BIBL. 21REF.Article

ADULT ACID MALTASE DEFICIENCY. ABNORMALITIES IN FIBROBLASTS CULTURED FROM PATIENTS = DEFICIT EN MALTASE ACIDE CHEZ L'ADULTE. ANOMALIES DES FIBROBLASTES DE MALADES EN CULTUREANGELINI C; ENGEL AG; TITUS JL et al.1972; NEW ENGL. J. MED.; U.S.A.; DA. 1972; VOL. 287; NO 19; PP. 948-951; BIBL. 14REF.Serial Issue

ACETYLCHOLINESTERASE OF HUMAN ERYTHROCYTES AND NEUROMUSCULAR JUNCTIONS: HOMOLOGIES REVEALED BY MONOCLONAL ANTIBODIES = ACETYLCHOLINESTERASE DES ERYTHROCYTES HUMAINS ET DES JONCTIONS NEUROMUSCULAIRES: HOMOLOGIES REVELEES PAR LES ANTICORPS MONOCLONAUXFAMBROUGH DM; ENGEL AG; ROSENBERRY TL et al.1982; PROC. NATL. ACAD. SCI. U.S.A., BIOL. SCI.; ISSN 0273-1134; USA; DA. 1982; VOL. 79; NO 4; PP. 1078-1082; BIBL. 15 REF.Article

STUDIES ON IN VITRO POLYMERIZATION OF TUBULIN FROM RENAL MEDULLARY EXTRACTS.BARNES LD; ENGEL AG; DOUSA TP et al.1975; BIOCHIM. BIOPHYS. ACTA; PAYS-BAS; DA. 1975; VOL. 405; NO 2; PP. 422-433; BIBL. 34 REF.Article

STEREOMETRIC ESTIMATION OF THE AREA OF THE FREEZE-FRACTURED MEMBRANEENGEL AG; FUKUNAGA H; OSAME M et al.1982; MUSCLE AND NERVE; ISSN 0148-639X; USA; DA. 1982; VOL. 5; NO 9; PP. 682-685; BIBL. 6 REF.Article

CARNITINE DEFICIENCY: CLINICAL, MORPHOLOGICAL, AND BIOCHEMICAL OBSERVATIONS IN A FATAL CASE.ENGEL AG; BANKER BQ; EIBEN RM et al.1977; J. NEUROL. NEUROSURG. PSYCHIATRY; G.B.; DA. 1977; VOL. 40; NO 4; PP. 313-322; BIBL. 25 REF.Article

A NEW MYASTHENIC SYNDROME WITH END-PLATE ACETYLCHOLINESTERASE, DEFICIENCY, SMALL NERVE TERMINALS, AND REDUCED ACETYLCHOLINE RELEASE.ENGEL AG; LAMBERT EH; GOMEZ MR et al.1977; ANN. NEUROL.; U.S.A.; DA. 1977; VOL. 1; NO 4; PP. 315-330; BIBL. 2 P.Article

IMMUNE COMPLEXES (IGG AND C3) AT THE MOTOR END-PLATE IN MYASTHENIA GRAVIS. ULTRASTRUCTURAL AND LIGHT MICROSCOPIC LOCALIZATION AND ELECTROPHYSIOLOGIC CORRELATIONS.ENGEL AG; LAMBERT EH; HOWARD FM JR et al.1977; MAYO CLIN. PROC.; U.S.A.; DA. 1977; VOL. 52; NO 5; PP. 267-280; BIBL. 33 REF.Article

HUMAN MUSCLE FIBER FINE STRUCTURE: MORPHOMETRIC DATA ON CONTROLS = STRUTURE FINE DES FIBRES MUSCULAIRES HUMAINES : DONNEES MORPHOMETRIQUES SUR DES TEMOINSJERUSALEM F; ENGEL AG; PETERSON HA et al.1975; NEUROLOGY; U.S.A.; DA. 1975; VOL. 25; NO 2; PP. 127-134; BIBL. 15REF.Article

FINGERPRINT BODY MYOPATHY. A NEWLY RECOGNIZED CONGENITAL MUSCLE DISEASE = MYOPATHIE EN EMPREINTE DIGITALE. UNE MALADIE CONGENITALE DU MUSCLE CONNUE DEPUIS PEUENGEL AG; ANGELINI C; GOMEZ MR et al.1972; MAYO CLIN. PROC.; U.S.A.; DA. 1972; VOL. 47; NO 6; PP. 377-388; BIBL. 38 REF.Serial Issue

ULTRASTRUCTURAL ASPECTS OF ACETYLCHOLINE RECEPTOR TURNOVER AT THE NORMAL END-PLATE AND IN AUTOIMMUNE MYASTHENIA GRAVISFUMAGALLI G; ENGEL AG; LINDSTROM J et al.1982; JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY; ISSN 0022-3069; USA; DA. 1982; VOL. 41; NO 6; PP. 567-579; BIBL. 24 REF.Article

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