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IMPROVED MYELINATION IN NERVE GRAFTS FROM THE LEUCODYSTROPHIC TWITCHER INTO TREMBLER MICE: EVIDENCE FOR ENZYME REPLACEMENTSCARAVILLI F; JACOBS JM.1982; BRAIN RES.; ISSN 0006-8993; NLD; DA. 1982; VOL. 237; NO 1; PP. 163-172; BIBL. 26 REF.Article

ENZYME-HISTOCHEMICAL DIFFERENTIATION OF NEUROGLIA AND MICROGLIA: A CONTRIBUTION TO THE CYTOGENESIS OF MICROGLIA AND GLOBOID CELLSOEHMICHEN M.1980; PATHOL., RES. PRACT.; DEU; DA. 1980; VOL. 168; NO 4; PP. 344-373; BIBL. 167 REF.Article

QUANTITATIVE DIFFERENCES IN GOBLET CELLS IN THE TRACHEAL EPITHELIUM OF MALE AND FEMALE RATS.HAYASHI M; HUBER GL.1977; AMER. REV. RESP. DIS.; U.S.A.; DA. 1977; VOL. 115; NO 4 PART. 1; PP. 595-599; BIBL. 27 REF.Article

GOBLET CELL DENSITY IN EUSTACHIAN TUBE OF CHILDREN.TOS M; BAD PEDERSEN K.1976; ARCH. OTOLARYNGOL.; U.S.A.; DA. 1976; VOL. 102; NO 1; PP. 20-26; BIBL. 21 REF.Article

GLOBOID CELLS, GLIAL NODULES, AND PECULIAR FIBRILLARY CHANGES IN THE CEREBRO-HEPATO-RENAL SYNDROME OF ZELLWEGER.DELEON GA; GROVER WD; HUFF DS et al.1977; ANN. NEUROL.; U.S.A.; DA. 1977; VOL. 2; NO 6; PP. 473-484; BIBL. 20 REF.Article

Late-onset globoid cell leukodystrophy mimicking and infiltrating gliomaEPSTEIN, M. A; ZIMMERMAN, R. A; RORKE, L. B et al.Pediatric radiology. 1991, Vol 21, Num 2, pp 131-132, issn 0301-0449Article

Goblet cell by hyperplasia is a feature of the adaptive response to jejunoileal bypass in ratsOLUBUYIDE, I. O; WILLIAMSON, R. C. N; BRISTOL, J. B et al.Gut. 1984, Vol 25, Num 1, pp 62-68, issn 0017-5749Article

Biochemical studies in mouse Krabbés disease (Twitcher)ETO, Y; UMEZAWA, F; KASAI, E et al.Journal of inherited metabolic disease. 1983, Vol 6, Num 3, pp 125-126, issn 0141-8955Article

Comparative clinico-pathological study of saposin-A-deficient (SAP-A-/-) and Twitcher miceYAGI, Takashi; MATSUDA, Junko; TAKIKITA, Shoichi et al.Journal of neuropathology and experimental neurology. 2004, Vol 63, Num 7, pp 721-734, issn 0022-3069, 14 p.Article

Morphological features of degenerating oligodendrocytes in twitcher miceLEVINE, S. M; TORRES, M. V.Brain research. 1992, Vol 587, Num 2, pp 348-352, issn 0006-8993Article

Galactosylceramide and galactosylsphingosine loadings studies in cultured skin fibroblasts in human and murine globoid cell leukodystrophyIDA, H; KUSANO, K; SUZUKI, H et al.Biochemical and biophysical research communications (Print). 1990, Vol 166, Num 2, pp 1053-1060, issn 0006-291XArticle

Acquired versus familial demyelinative neuropathies in childrenMILLER, R. G; GUTMANN, L; LEWIS, R. A et al.Muscle & nerve. 1985, Vol 8, Num 3, pp 205-210, issn 0148-639XArticle

The earliest MR imaging and proton MR spectroscopy abnormalities in adult-onset Krabbe diseaseWANG, C; MELBERG, A; WEIS, J et al.Acta neurologica scandinavica. 2007, Vol 116, Num 4, pp 268-272, issn 0001-6314, 5 p.Article

Late infantile onset Krabbe disease in siblings with cortical degeneration and absence of cerebral globoid cellsDEL BIGLO, M. R; CHUDLEY, A. E; BOOTH, F. A et al.Neuropediatrics. 2004, Vol 35, Num 5, pp 297-301, issn 0174-304X, 5 p.Article

Hematopoietic stem-cell transplantation in globoid-cell leukodystrophyKRIVIT, W; SHAPIRO, E. G; DUSENBERY, K et al.The New England journal of medicine. 1998, Vol 338, Num 16, pp 1119-1126, issn 0028-4793Article

Mucinous carcinoma of the skin, primary, and secondary : A clinicopathologic study of 63 cases with emphasis on the morphologic spectrum of primary cutaneous forms: Homologies with mucinous lesions in the breastKAZAKOV, Dmitry V; SUSTER, Saul; BALTACI, Mehmet et al.The American journal of surgical pathology. 2005, Vol 29, Num 6, pp 764-782, issn 0147-5185, 19 p.Article

Cellular uptake and lysosomal delivery of galactocerebrosidase tagged with the HIV Tat protein transduction domainZHANG, Xian-Yang; DINH, Annie; CRONIN, James et al.Journal of neurochemistry. 2008, Vol 104, Num 4, pp 1055-1064, issn 0022-3042, 10 p.Article

Increased TNF-α production by peripheral blood mononuclear cells in patients with Krabbe's disease : effect of psychosinePASQUI, A. L; DI RENZO, M; AUTERI, A et al.European journal of clinical investigation. 2007, Vol 37, Num 9, pp 742-745, issn 0014-2972, 4 p.Article

Neuropathology of twitcher mice : examination by histochemistry, immunohistochemistry, lectin histochemistry and Fourier transform infrared microspectroscopyLEVINE, S. M; WETZEL, D. L; EILERT, A. J et al.International journal of developmental neuroscience. 1994, Vol 12, Num 4, pp 275-288, issn 0736-5748Article

Intracranial Calcification after Cord Blood Neonatal Transplantation for Krabbe DiseaseLEHMAN, A. M; SCHULTZ, K. R; POSKITT, K et al.Neuropediatrics. 2009, Vol 40, Num 4, pp 189-191, issn 0174-304X, 3 p.Article

Hematopoietic cell transplantation ameliorates clinical phenotype and progression of the CNS pathology in the mouse model of late onset krabbe diseaseYAGI, Takashi; MATSUDA, Junko; TOMINAGA, Kumiko et al.Journal of neuropathology and experimental neurology. 2005, Vol 64, Num 7, pp 565-575, issn 0022-3069, 11 p.Article

Adult onset Krabbe disease may mimic motor neurone diseaseHENDERSON, R. D; MACMILLAN, J. C; BRADFIELD, J. M et al.Journal of clinical neuroscience. 2003, Vol 10, Num 5, pp 638-639, issn 0967-5868, 2 p.Article

Krabbe leukodystrophy in a selected population with high rate of late onset forms: longer survival linked to c.121G>A (p.Gly41Ser) mutationFIUMARA, A; BARONE, R; ARENA, A et al.Clinical genetics. 2011, Vol 80, Num 5, pp 452-458, issn 0009-9163, 7 p.Article

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