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Results 1 to 25 of 194

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FUCOSE PLAYS A ROLE IN THE CLEARANCE AND UPTAKE OF GLUCOCEREBROSIDASE BY RAT LIVER CELLSFURBISH FS; KRETT NL; BARRANGER JA et al.1980; BIOCHEM. BIOPHYS. RES. COMMUN.; ISSN 0006-291X; USA; DA. 1980; VOL. 95; NO 4; PP. 1768-1774; BIBL. 21 REF.Article

THE UPTAKE OF NATIVE AND DESIALYLATED GLUCOCEREBROSIDASE BY RAT HEPATOCYTES AND KUPFER CELLS.FURBISH FS; STEER CJ; BARRANGER JA et al.1978; BIOCHEM. BIOPHYS. RES. COMMUNIC.; USA; DA. 1978; VOL. 81; NO 3; PP. 1047-1053; BIBL. 22 REF.Article

L-GLUCOSYLCERAMIDE: SYNTHESIS, PROPERTIES, AND RESISTANCE TO CATABOLISM BY GLUCOCEREBROSIDASE IN VITROGAL AF; PENTCHEV PG; MASSEY JM et al.1979; PROC. NATION. ACAD. SCI.; USA; DA. 1979; VOL. 76; NO 7; PP. 3083-3086; BIBL. 15 REF.Article

SOLUBILIZATION OF GLUCOCEREBROSIDASE FROM HUMAN PLACENTA AND DEMONSTRATION OF A PHOSPHOLIPID REQUIREMENT FOR ITS CATALYTIC ACTIVITY.DALE GL; VILLACORTE DG; BEUTLER E et al.1976; BIOCHEM. BIOPHYS. RES. COMMUNIC.; U.S.A.; DA. 1976; VOL. 71; NO 4; PP. 1048-1053; BIBL. 10 REF.Article

GAUCHER'S DISEASE: LACK OF ANTIBODY RESPONSE TO INTRAVENOUS GLUCOCEREBROSIDASEBRITTON DE; LEINIKKI PO; BARRANGER JA et al.1978; LIFE SCI.; GBR; DA. 1978; VOL. 23; NO 25; PP. 2517-2520; BIBL. 5 REF.Article

THE UPTAKE OF AGALACTO-GLUCOCEREBROSIDASE BY RAT HEPATOCYTES AND KUPFFER CELLSSTEER CJ; FURBISH FS; BARRANGER JA et al.1978; F.E.B.S. LETTERS; NLD; DA. 1978; VOL. 91; NO 2; PP. 202-205; BIBL. 17 REF.Article

MUTATIONS OF GLUCOCEREBROSIDASE: DISCRIMINATION OF NEUROLOGIC AND NON-NEUROLOGIC PHENOTYPES OF GAUCHER DISEASEGINNS EI; BRADY RO; PIRRUCCELLO S et al.1982; PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA. BIOLOGICAL SCIENCES; ISSN 0273-1134; USA; DA. 1982; VOL. 79; NO 18; PP. 5607-5610; BIBL. 36 REF.Article

STUDIES IN VIVO OF THE TISSUE UPTAKE, CELLULAR DISTRIBUTION AND CATABOLIC TURNOVER OF EXOGENOUS GLUCOCEREBROSIDASE IN RATMORRONE S; PENTCHEV PG; BAYNES J et al.1981; BIOCHEM. J. (LOND.); ISSN 0006-2936; GBR; DA. 1981; VOL. 194; NO 3; PP. 733-742; BIBL. 2 P.Article

PROPRIETES DES FORMES MOLECULAIRES DE LA BETA -GLUCOSIDASE ET DE LA BETA -GLUCOCEREBROSIDASE DE RATE HUMAINE NORMALE ET DE MALADIE DE GAUCHERMARET A; SALVAYRE R; NEGRE A et al.1981; EUR. J. BIOCHEM.; ISSN 0014-2956; DEU; DA. 1981; VOL. 115; NO 3; PP. 455-461; ABS. ENG; BIBL. 34 REF.Article

Complex alleles of the acid β-glucosidase gene in Gaucher diseaseLATHAM, T; GRABOWSKI, G. A; THEOPHILUS, B. D. M et al.American journal of human genetics. 1990, Vol 47, Num 1, pp 79-86, issn 0002-9297, 8 p.Article

GAUCHER DISEASE: ISOLATION AND COMPARISON OF NORMAL AND MUTANT GLUCOCERESIDASE FROM HUMAN SPLEEN TISSUEPENTCHEV PG; BRADY RO; BLAIR HE et al.1978; PROC. NATION. ACAD. SCI. USA; USA; DA. 1978; VOL. 75; NO 8; PP. 3970-3973; BIBL. 14 REF.Article

ENZYMIC DIFFERENTIATION OF NEUROLOGIC AND NONNEUROLOGIC FORMS OF GAUCHER'S DISEASEGLEW RH; DANIELS LB; CLARK LS et al.1982; JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY; ISSN 0022-3069; USA; DA. 1982; VOL. 41; NO 6; PP. 630-641; BIBL. 24 REF.Article

UNE OBSERVATION DE MALADIE DE GAUCHER DE L'ADULTERENIER JC; BONTOUX L; BERNAT M et al.1978; SEM. HOP.; FRA; DA. 1978; VOL. 54; NO 29-32; PP. 969-971; ABS. ENG; BIBL. 7 REF.Article

DIFFERENTIATION OF BETA -GLUCOCEREBROSIDASE FROM BETA -GLUCOSIDASE IN HUMAN TISSUES USING SODIUM TAUROCHOLATE.PETERS SP; COYLE P; GLEW RH et al.1976; ARCH. BIOCHEM. BIOPHYS.; U.S.A.; DA. 1976; VOL. 175; NO 2; PP. 569-582; BIBL. 29 REF.Article

Purification of β-glucocerebrosidase by preparative-scale high-performance liquid chromatography: the use of ethylene glycol-containing buffers for chromatography of hydrophobic glycoprotein enzymesMURRAY, G. J; YOULE, R. J; GANDY, S. E et al.Analytical biochemistry. 1985, Vol 147, Num 2, pp 301-310, issn 0003-2697Article

PURIFICATION AND PROPERTIES OF A HEAT-STABLE GLUCOCEREBROSIDASE ACTIVATING FACTOR FROM CONTROL AND GAUCHER SPLEEN.PETERS SP; COYLE P; COFFEE CJ et al.1977; J. BIOL. CHEM.; U.S.A.; DA. 1977; VOL. 252; NO 2; PP. 563-573; BIBL. 56 REF.Article

A DIALYSIS PROCEDURE FOR LOADING ERYTHROCYTES WITH ENZYMES AND LIPIDS.DELOACH J; IHLER G.1977; BIOCHIM. BIOPHYS. ACTA; PAYS-BAS; DA. 1977; VOL. 496; NO 1; PP. 136-145; BIBL. 15 REF.Article

The occurrence of two immunologically distinguishable β-glucocerebrosidases in human spleenAERTS, J. M. F. G; DONKER-KOOPMAN, W. E; VAN DER VLIET, M. K et al.European journal of biochemistry (Print). 1985, Vol 150, Num 3, pp 565-574, issn 0014-2956Article

Effect of experimental conditions on the appearance of distinct forms of placentral glucosylceramidase : use of gel filtration analysis as a means of ascertaining their occurrenceVACCARO, A. M; SALVIOLI, R; GALLOZZI, E et al.Biochimica et biophysica acta. 1990, Vol 1047, Num 1, pp 57-62, issn 0006-3002, 6 p.Article

Heterogeneity in human acid β-glucosidase revealed by cellulose-acetate electrophoresisSA MIRANDA, M. C; AERTS, J. M. F. G; PINTO, R. A. A et al.Biochimica et biophysica acta. 1988, Vol 965, Num 2-3, pp 163-168, issn 0006-3002Article

CONTRIBUTION A L'ETUDE DE LA MALADIE DE GAUCHER DE L'ADULTE. A PROPOS D'UNE OBSERVATION. DISCUSSION DES METHODES D'APPROCHE THERAPEUTIQUE PAR REMPLACEMENT ENZYMATIQUEDESCHASEAUX ERIC.1979; ; FRA; DA. 1979; 79-97; 212 P.: ILL.-PL.; 30 CM; BIBL. 187 REF.; TH.: MED./BESANCON/1979Thesis

Interaction of saposins, acidic lipids, and glucosylceramidaseMORIMOTO, S; KISHIMOTO, Y; TOMICH, J et al.The Journal of biological chemistry (Print). 1990, Vol 265, Num 4, pp 1933-1937, issn 0021-9258, 5 p.Article

The use of glycosides of 6- and 8-acylamino-4-methylumbeliferone in studies of the specificities and properties of human lysosomal glycolipid hydrolasesWIEDERSCHAIN, G. Y; KOZLOVA, I. K; ILYINA, G. S et al.Carbohydrate research. 1992, Vol 224, pp 255-272, issn 0008-6215Article

Purification and the effect of peptide N-glycosidase F on lysosomal membrane-bound glucocerebrosidase from human cultured fibroblastsCHOY, F. Y. M; WOO, M.Biochemistry and cell biology. 1991, Vol 69, Num 8, pp 551-556, issn 0829-8211Article

Human acid β-glucosidase : glycosylation is required for catalytic activityGRACE, M. E; GRABOWSKI, G. A.Biochemical and biophysical research communications (Print). 1990, Vol 168, Num 2, pp 771-777, issn 0006-291X, 7 p.Article

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