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STUDIES ON THE VALINE SENSITIVITY IN NON-KETOTIC HYPERGLYCINEMIA. = LES ETUDES SUR LA SENSIBILITE A LA VALINE DANS L'HYPERGLYCINEMIE NON CETOSIQUEDE GROOT CJ; VAN DEN BERG H; HOMMES FA et al.1975; HELV. PAEDIATR. ACTA; SUISSE; DA. 1975; VOL. 30; NO 3; PP. 247-254; ABS. ALLEM. FR.; BIBL. 10 REF.Article

A BLOCK IN GLYCINE CLEAVAGE REACTION AS A COMMON MECHANISM IN KETOTIC AND NONKETOTIC HYPERGLYCINEMIA = UN BLOC DANS LA REACTION DE CLIVAGE DE LA GLYCINE COMME MECANISME COMMUN DANS L'HYPERGLYCINEMIE CETOSIQUE ET NON CETOSIQUETADA K; CORBEEL LM; EECKELS R et al.1974; PEDIATR. RES.; U.S.A.; DA. 1974; VOL. 8; NO 7; PP. 721-723; BIBL. 15REF.Article

Nonketotic hyperglycinemia: two patients with primary defects of P-protein and T-protein, respectively, in the glycine cleavage systemHAYASAKA, K; TADA, K; KIKUCHI, G et al.Pediatric research. 1983, Vol 17, Num 12, pp 967-970, issn 0031-3998Article

NON-KETOTIC HYPERGLYCINEMIA: A CASE REPORTMEHARBAN SINGH; GHAI OP.1975; INDIAN PEDIATR.; INDIA; DA. 1975; VOL. 12; NO 2; PP. 197-199; BIBL. 7REF.Article

INTERPRETATION OF ELEVATED BLOOD GLYCINE LEVELS IN CHILDREN. = INTERPRETATION DE L'ELEVATION DU TAUX SANGUIN DE GLYCINE CHEZ LES ENFANTSAPPLEGARTH DA; POON S.1975; CLIN. CHIM. ACTA; PAYS-BAS; DA. 1975; VOL. 63; NO 1; PP. 49-54; BIBL. 13 REF.Article

L'HYPERGLYCINEMIE SANS CETOSE CONGENITALE. UNE NOUVELLE OBSERVATIONPIUSSAN C; SAUDUBRAY JM; VAN POPERINGHE M et al.1975; PEDIATRIE; FR.; DA. 1975; VOL. 30; NO 4; PP. 429-431Article

HYPERGLYCINEMIEHYANEK J; POSPISIL R; HOZA J et al.1975; CESKOSL. PEDIATR.; CESKOSL.; DA. 1975; VOL. 30; NO 11; PP. 543-545; ABS. RUSSE ANGL.; BIBL. 7 REF.Article

INHIBITION OF GLYCINE SERINE INTERCONVERSION IN CULTURED HUMAN FIBROBLASTS BY PRODUCTS OF ISOLEUCINE CATABOLISM = INHIBITION PAR LES PRODUITS DU CATABOLISME DE L'ISOLEUCINE DE L'INTERCONVERSION GLYCINE-SERINE DANS LES FIBROBLASTES HUMAINS EN CULTUREHILLMAN RE; OTTO EF.1974; PEDIATR. RES.; U.S.A.; DA. 1974; VOL. 8; NO 12; PP. 941-945; BIBL. 19REF.Article

NONKETOTIC HYPERGLYCINEMIA. GLYCINE ACCUMULATION DUE TO ABSENCE OF GLYCINE CLEAVAGE IN BRAIN. = HYPERGLYCINEMIE NON CETONIQUE. ACCUMULATION DE GLYCINE DUE A L'ABSENCE DE CLIVAGE DE LA GLYCINE DANS L'ENCEPHALEPERRY TL; URQUHART N; MAC LEAN J et al.1975; NEW ENGL. J. MED.; U.S.A.; DA. 1975; VOL. 292; NO 24; PP. 1269-1273; BIBL. 21 REF.Article

GLYCINE TRANSPORT BY HUMAN DIPLOID FIBROBLASTS. ABSENCE OF A DEFECT IN CELLS FROM PATIENTS WITH NONKETOTIC HYPERGLYCINEMIAKELLY JC; OTTO EF; HILLMAN RE et al.1979; PEDIATR. RES.; USA; DA. 1979; VOL. 13; NO 2; PP. 127-130; BIBL. 30 REF.Article

THE VITAMIN B12-DEFICIENT RAT AS A POSSIBLE MODEL OF KETOTIC HYPERGLYCINEMIA. = LE RAT CARENCE EN VITAMINE B12, MODELE POSSIBLE DE L'HYPERGLYCINEMIE CETOSIQUEO'NEILL ROWLEY B; BROTHERS V; GERRITSEN T et al.1975; PEDIATR. RES.; U.S.A.; DA. 1975; VOL. 9; NO 10; PP. 782-786; BIBL. 41 REF.Article

Nonketotic hyperglycinemia: analyses of glycine cleavage system in typical and atypical casesHAYASAKA, K; TADA, K; SCHUTGENS, R. B. H et al.The Journal of pediatrics. 1987, Vol 110, Num 6, pp 873-877, issn 0022-3476Article

LEUKOCYTE PROPIONYL-COA CARBOXYLASE DEFICIENCY IN A PATIENT WITH KETOTIC HYPERGLYCINAEMIADEL VALLE JA; MERINERO B; GARCIA MJ et al.1980; J. INHERIT. METAB. DIS.; GBR; DA. 1980; VOL. 3; NO 3; PP. 93; BIBL. 4 REF.Article

NONKETOTIC HYPERGLYCINEMIA: A GENETIC STUDY OF 13 FINNISH FAMILIESWENDT LV; HIRVASNIEMI A; SIMILA S et al.1979; CLIN. GENET.; DNK; DA. 1979; VOL. 15; NO 5; PP. 411-417; BIBL. 27 REF.Article

METHYLMALONIC ACIDAEMIA AND NONKETOTIC HYPERGLYCINAEMIA: CLINICAL AND BIOCHEMICAL ASPECTS = ACIDEMIE METHYLMALONIQUE ET HYPERGLYCINEMIE NON CETOSIQUE: ASPECTS CLINIQUES ET BIOCHIMIQUESCORBEEL L; TADA K; COLOMBO JP et al.1975; ARCH. DIS. CHILDH.; G.B.; DA. 1975; VOL. 50; NO 2; PP. 103-109; BIBL. 31REF.Article

METABOLISM OF GLYCINE IN THE NORMAL INDIVIDUAL AND IN PATIENTS WITH NON-KETOTIC HYPERGLYCINAEMIANYHAN WL.1982; JOURNAL OF INHERITED METABOLIC DISEASE; ISSN 0141-8955; GBR; DA. 1982; VOL. 5; SUPPL. 2; PP. 105-110; BIBL. 2 P.Article

DEFECTIVE GLYCINE CLEAVAGE SYSTEM IN NONKETOTIC HYPERGLYCINEMIA. OCCURRENCE OF A LESS ACTIVE GLYCINE DECARBOXYLASE AND AN ABNORMAL AMINOMETHYL CARRIER PROTEINHIRAGA K; KOCHI H; HAYASAKA K et al.1981; J. CLIN. INVEST.; ISSN 0021-9738; USA; DA. 1981; VOL. 68; NO 2; PP. 525-534; BIBL. 36 REF.Article

HYPERGLYCINEMIA AND PROPIONYL COA CARBOXYLASE DEFICIENCY AND EPISODIC SEVERE ILLNESS WITHOUT CONSISTENT KETOSIS. = HYPERGLYCINEMIE, DEFICIT EN PROPIONYL COA CARBOXYLASE ET MALADIE EPISODIQUE SEVERE SANS CETOSE CONSTANTEWADLINGTON WB; KILROY A; ANDO T et al.1975; J. PEDIATR.; U.S.A.; DA. 1975; VOL. 86; NO 5; PP. 707-712; BIBL. 26 REF.Article

THE OXIDATION OF GLYCINE AND PROPIONIC ACID IN PROPIONIC ACIDEMIA WITH KETOTIC HYPERGLYCINEMIA = L'OXYDATION DE LA GLYCINE ET DE L'ACIDE PROPIONIQUE DANS L'ACIDOSE PROPIONIQUE AVEC HYPERGLYCINEMIE CETOSIQUEANDO T; NYHAN WL; CONNOR JD et al.1972; PEDIATR. RES.; SWITZ.; DA. 1972; VOL. 6; NO 6; PP. 576-583; BIBL. 31 REF.Serial Issue

IDENTIFICATION OF METABOLITES USING COMBINED GASCHROMATOGRAPHY. MASS SPECTROMETRY. = IDENTIFICATION DES METABOLITES A L'AIDE DE L'ASSOCIATION CHROMATOGRAPHIE EN PHASE GAZEUSE (CG)-SPECTROMETRIE DE LA MASSE (SM)1975; SCAND. J. CLIN. LAB. INVEST., SUPPL.; NORWAY; DA. 1975; VOL. 35; NO 143; PP. 145-149; BIBL. 7 REF.; (15TH MEET. SCAND. SOC. CLIN. CHEM. CLIN. PHYSIOL. TRANS.; ARHUS, DEN.; 1975)Conference Paper

A PATIENT WITH NONKETOTIC HYPERGLYCINEMIA: BIOCHEMICAL FINDINGS AND THERAPEUTIC APPROACHES = SIGNES BIOCHIMIQUES ET APPROCHES THERAPEUTIQUES CHEZ UN MALADE ATTEINT D'HYPERGLYCINEMIE NON CETOSIQUETRIJBELS JMF; MONNENS LAH; VAN DER ZEE SPM et al.1974; PEDIATR. RES.; U.S.A.; DA. 1974; VOL. 8; NO 5; PP. 598-605; BIBL. 26 REF.Article

NON-KETOTIC HYPERGLYCINAEMIA - A REVIEW OF 70 PATIENTSCARSON NAJ.1982; JOURNAL OF INHERITED METABOLIC DISEASE; ISSN 0141-8955; GBR; DA. 1982; VOL. 5; SUPPL. 2; PP. 126-128; BIBL. 2 REF.Article

PROGRESSIVE NEURODEGENERATIVE DISORDER IN A PATIENT WITH NONKETOTIC HYPERGLYCINEMIATRAUNER DA; PAGE T; GRECO C et al.1981; J. PEDIATR.; ISSN 0022-3476; USA; DA. 1981; VOL. 98; NO 2; PP. 272-275; BIBL. 11 REF.Article

MEGALOCORNEA IN NONKETOTIC HYPERGLYCINEMIAHOYT CS; BROWN RA.1978; J. PEDIATR. OPHTHALMOL. STRABISM.; USA; DA. 1978; VOL. 15; NO 2; PP. 85-88; BIBL. 27 REF.Article

D-GLYCERIC-ACIDAEMIA AND NON-KETOTIC HYPERGLYCINAEMIA.BRANDT NJ; RASMUSSEN K; BRANDT S et al.1976; ACTA PAEDIATR. SCAND.; SUEDE; DA. 1976; VOL. 65; NO 1; PP. 17-22; BIBL. 19 REF.Article

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