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Results 1 to 25 of 127

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NEW METABOLITES IN ISOVALERIC ACIDEMIATRUSCOTT RJW; MALEGAN D; MCCAIRNS E et al.1981; CLIN. CHIM. ACTA; ISSN 0009-8981; NLD; DA. 1981; VOL. 110; NO 2-3; PP. 187-203; BIBL. 31 REF.Article

FORMATION OF BETA -HYDROXYISOVALERATE BY AN ALPHA -KETOISOCAPROATE OXYGENASE IN HUMAN LIVERSABOURIN PJ; BIEBER LL.1983; METABOLISM, CLINICAL AND EXPERIMENTAL; ISSN 0026-0495; USA; DA. 1983; VOL. 32; NO 2; PP. 160-164; BIBL. 33 REF.Article

CONTRIBUTION A L'ETUDE DES METHODES ENZYMOLOGIQUES PERMETTANT LA MESURE DE LA DEGRADATION DES ACIDES AMINES RAMIFIES. APPLICATION A LA LEUCINOSE ET A L'ACIDEMIE ISOVALERIQUEBRUYANT DUMOULIN RENEE.1978; ; FRA; DA. 1978; 786; 80 P.; 29 CM; BIBL. 92 REF.; TH. 3EME CYCLE: BIOCHIM./LYON 1/1978Thesis

ANTAGONISTIC EFFECTS OF ISOVALERATE AND GLYCINE ON PLASMA CHOLINE LEVELS IN RABBITSSCHUBERTH J; DAHLBERG L.1980; LIFE SCI.; GBR; DA. 1980; VOL. 26; NO 4; PP. 273; BIBL. 14 REF.Article

EXTRACTION DE L'ACIDE BORIQUE PAR L'ALCOOL ISO-AMYLIQUE A PARTIR DE SOLUTIONS AQUEUSES CONTENANT DU CHLORURE DE LIAZAROVA LA; VINOGRADOV EE.1976; ZH. NEORG. KHIM.; S.S.S.R.; DA. 1976; VOL. 21; NO 9; PP. 2484-2487; BIBL. 7 REF.Article

ISOTACHOPHORETIC ANALYSIS OF ISOVALERYLGLYCINE IN URINE OF A PATIENT WITH ISOVALERIC ACIDEMIAKODAMA H; UASA S.1979; J. CHROMATOGR.; NLD; DA. 1979; VOL. 163; NO 3; PP. 300-303; BIBL. 12 REF.Article

Smoking accelerates biotin catabolism in womenSEALEY, Wendy M; TEAGUE, April M; STRATTON, Shawna L et al.The American journal of clinical nutrition. 2004, Vol 80, Num 4, pp 932-935, issn 0002-9165, 4 p.Article

CORRELATION BETWEEN BLOOD AMMONIA CONCENTRATION AND ORGANIC ACID ACCUMULATION IN ISOVALERIC AND PROPIONIC ACIDEMIACOUDE FX; OGIER H; GRIMBER G et al.1982; PEDIATRICS (EVANSTON); ISSN 0031-4005; USA; DA. 1982; VOL. 69; NO 1; PP. 115-117; BIBL. 10 REF.Article

ACIDEMIE ISOVALERIQUE. ETUDE ET TRAITEMENT CHEZ TROIS FRERESSAUDUBRAY JM; SORIN M; DEPONDT E et al.1976; ARCH. FR. PEDIATR.; FR.; DA. 1976; VOL. 33; NO 8; PP. 795-808; ABS. ANGL.; BIBL. 1 P. 1/2Article

ISOVALERIC ACIDEMIA: USE OF GLYCINE THERAPY IN NEONATESCOHN RM; YUDKOFF M; ROTHMAN R et al.1978; NEW ENGL. J. MED.; USA; DA. 1978; VOL. 299; NO 18; PP. 996-999; BIBL. 15 REF.Article

DEMONSTRATION OF A SPECIFIC MITOCHONDRIAL ISOVALERYL-COA DEHYDROGENASE DEFICIENCY IN FIBROBLASTS FROM PATIENTS WITH ISOVALERIC ACIDEMIARHEAD WJ; TANAKA K.1980; PROC. NATION. ACAD. SCI.; USA; DA. 1980; VOL. 77; NO 1 PART. 1; PP. 580-583; BIBL. 22 REF.Article

SYNTHETIC FLAVORS: EFFICIENCY AND SAFETY FACTORS FOR SWEATY AND FISHY ODORANTSAMOORE JE; GUMBMANN MR; BOOTH AN et al.1978; CHEM. SENS. FLAVOUR; NLD; DA. 1978; VOL. 3; NO 3; PP. 307-317; BIBL. 14 REF.Article

THE OCCURRENCE OF 2-HYDROXYISOVALERIC ACID IN PATIENTS WITH LACTIC ACIDOSIS AND KETOACIDOSIS.LANDAAS S; JAKOBS C.1977; CLIN. CHIM. ACTA; PAYS-BAS; DA. 1977; VOL. 78; NO 3; PP. 489-493; BIBL. 13 REF.Article

ISOVALERIC ACIDAEMIA PRESENTING WITH DWARFISM, CATARACT AND CONGENITAL ABNORMALITIESDURAN M; BRUINVIS L; KETTING D et al.1982; J. INHERIT. METAB. DIS.; ISSN 0141-8955; GBR; DA. 1982; VOL. 5; NO 2; PP. 125-127; BIBL. 11 REF.Article

THE PANCYTOPENIA OF ISOVALERIC ACIDEMIAKELLEHER JF JR; YUDKOFF M; HUTCHINSON R et al.1980; PEDIATRICS; USA; DA. 1980; VOL. 65; NO 5; PP. 1023-1027; BIBL. 15 REF.Article

ISOVALERICACIDEMIA. A CASE REPORTWINOKUR PA; VASHISTHA K; RAJALAKSHMI SESHAMANI et al.1978; PEDIATRICS; USA; DA. 1978; VOL. 61; NO 6; PP. 902-903; BIBL. 7 REF.Article

ISOVALERIANAZIDAEMIE. = ACIDEMIE ISOVALERIANIQUELIPINSKI C; TREFZ F; KLETT M et al.1977; THERAPIEWOCHE; DTSCH.; DA. 1977; VOL. 27; NO 39; PP. 6725-6728 (3P.); BIBL. 16 REF.; (AKTUEL. KINDERHEILKD. TAG. SUEDDTSCH. KINDERAERZTE. 25; ERLANGEN; 1976)Conference Paper

METABOLISM OF (1-14C) AND (2-14C) LEUCINE IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH ISOVALERIC ACIDEMIA. CHARACTERIZATION OF METABOLIC DEFECTS.TANAKA K; MANDELL R; SHIH VE et al.1976; J. CLIN. INVEST.; U.S.A.; DA. 1976; VOL. 58; NO 1; PP. 164-172; BIBL. 22 REF.Article

L-carnitine therapy in isovaleric acidemiaROE, C. R; MILLINGTON, D. S; MALBY, D. A et al.The Journal of clinical investigation. 1984, Vol 74, Num 6, pp 2290-2295, issn 0021-9738Article

Could valerian have been the first anticonvulsant?EADIE, Mervyn J.Epilepsia (Copenhagen). 2004, Vol 45, Num 11, pp 1338-1343, issn 0013-9580, 6 p.Article

Molecular heterogeneity of variant isovaleryl-CoA dehydrogenase from cultured isovaleric acidemia fibroblastsIKEDA, Y; KEESE, S. M; TANAKA, K et al.Proceedings of the National Academy of Sciences of the United States of America. 1985, Vol 82, Num 20, pp 7081-7085, issn 0027-8424Article

The identification and the excretion pattern of isovaleryl glucuronide in the urine of patients with isovaleric acidemiaHINE, D. G; TANAKA, K.Pediatric research. 1984, Vol 18, Num 6, pp 508-512, issn 0031-3998Article

TWO SISTERS WITH ISOVALERIC ACIDAEMIA, MULTIPLE ATTACKS OF KETOACIDOSIS AND NORMAL DEVELOPMENTDURAN M; VAN SPRANG FJ; DREWES JG et al.1979; EUROP. J. PEDIATR.; DEU; DA. 1979; VOL. 131; NO 3; PP. 205-211; BIBL. 16 REF.Article

ISOVALERIANACIDAEMIE KOMBINIERT MIT HYPERTROPHISCHER PYLORUSSTENOSE = ISOVALERIANACIDEMIE ASSOCIEE A UNE STENOSE HYPERTROPHIQUE DU PYLORELEHNERT W; SCHENCK W; NIEDERHOFF H et al.1979; KLIN. PAEDIATR.; DEU; DA. 1979; VOL. 191; NO 5; PP. 477-482; ABS. ENG; BIBL. 5 REF.Article

ACIDEMIE ISOVALERIQUE CHEZ UN JEUNE NOURRISSON.NIEDERHOFF H; LEHNERT W; KUNZER W et al.1977; PEDIATRIE; FR.; DA. 1977; VOL. 32; NO 5; PP. 421-424; ABS. ANGL.; BIBL. 3 REF.Article

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