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kw.\*:("KUGELBERG WELANDER DISEASE")

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SU UN CASO DI MALATTIA DI WOHLFART-KUGELBERG-WELANDER O ATROFIA MUSCOLARE GIOVANILE SPINALE EREDOFAMILIARE. = SUR UN CAS DE MALADIE DE WOHLFART-KUGELBERG-WELANDER OU ATROPHIE MUSCULAIRE JUVENILE SPINALE HEREDOFAMILIALEMANARA F; GASCO P; MILANI L et al.1977; MINERVA MED.; ITAL.; DA. 1977; VOL. 68; NO 6; PP. 417-424; BIBL. 27 REF.Article

MALATTIA DI WOHLFART-KUGELBERG-WELANDER. CONTRIBUTO CLINICO. NOTA PRELIMINARE. = MALADIE DE WOHLFART-KUGELBERG-WELANDER. PRESENTATION DE CAS. NOTE PRELIMINAIRERUBINO AD; MAZZELLA GG; CEDROLA GM et al.1977; MINERVA MED.; ITAL.; DA. 1977; VOL. 68; NO 3; PP. 203-208; BIBL. 11 REF.Article

ASPECTS ACTUELS DU SYNDROME DE WOHLFART-KUGELBERG-WELANDER (AMYOTROPHIE SPINALE PROGRESSIVE)BENCE YR; PAOLI F; MARTIN J et al.1979; LYON MEDITERR. MED.; FRA; DA. 1979; VOL. 15; NO 16; PP. 1443-1453; (7 P.)Article

SPINAL MUSCULAR ATROPHY IN CHILDHOOD: REVIEW OF 50 CASESBENADY SG.1978; DEVELOP. MED. CHILD NEUROL.; GBR; DA. 1978; VOL. 20; NO 6; PP. 746-757; ABS. FRE/GER/SPA; BIBL. 15 REF.Article

CHRONIC FORM OF CHILDHOOD SPINAL MUSCULAR ATROPHY: ARE THE PROBLEMS OF ITS GENETICS REALLY SOLVED.HAUSMANOWA PETRUSEWICZ I; ZAREMBA J; BORKOWSKA J et al.1979; J. NEUROL. SCI.; NLD; DA. 1979; VOL. 43; NO 2; PP. 317-327; BIBL. 13 REF.Article

ATROFIE MUSCOLARI SPINALI INFANTILI DI TIPO BENIGNO: ASPETTI NOSOGRAFICI CLINICI, E METODOLOGICI = ATROPHIE MUSCULAIRE SPINALE INFANTILE DE TYPE BENIN. ASPETS NOSOGRAPHIQUES, CLINIQUES ET METHODOLOGIQUESCARBONI P; SIDERI G; GIACANELLI M et al.1979; NEUROPSICHIATR. INFANT.; ITA; DA. 1979; NO 221; PP. 1141-1150; ABS. ENG; BIBL. 9 REF.Article

Genetic counseling in families with spinal muscular atrophy type Kugelberg-WelanderZERRES, K; GRIMM, T.Human genetics. 1983, Vol 65, Num 1, pp 74-75, issn 0340-6717Article

AMIOTROFIA SPINALE TIPO KUGELBERG-WELANDER: STUDIO SUI FAMILIARI DI DUE CASI = AMYOTROPHIE SPINALE DE TYPE KUGELBERG-WELANDER: ETUDE CONCERNANT LES MEMBRES DES FAMILLES DE 2 MALADESDE FALCO FA; MANDARINI A; PERRETTI A et al.1978; QUAD. ACTA NEUROL.; ITA; DA. 1978; VOL. 37; PP. 39-44; ABS. ENG; BIBL. 20 REF.Article

LA MYOCARDIOPATHIE DANS LA MALADIE DE KUGELBERG-WELANDERMOSCOVIZ ROLAND.1980; ; FRA; DA. 1980; 18; 118 P.: ILL.; 30 CM; BIBL. 115 REF.; TH.: MED./NANCY 1/1980Thesis

LE AMIOTROPIE SPINALI PROSSIMALI INFANTILI E GIOVANILI: CONTRIBUTO CLINICO E GENETICO SU VENTI CASI PERSONALI = L'AMYOTROPHIE MEDULLAIRE PROXIMALE INFANTILE ET JUVENILE, CONTRIBUTION CLINIQUE ET GENETIQUE AVEC 20 CAS PERSONNELSTREVISAN C; MOSTACCIVOLO ML; BATTISTELLA PA et al.1978; NEUROPSICHIATR. INFANT.; ITA; DA. 1978; NO 209; PP. 1307-1319; ABS. ENG; BIBL. 12 REF.Article

LATE ONSET SPINAL MUSCLE ATROPHY: A SEX LINKED VARIANT OF KUGELBERG-WELANDERPAULSON GW; LISS P; SWEENEY PJ et al.1980; ACTA NEUROL. SCAND.; DNK; DA. 1980; VOL. 61; NO 1; PP. 49-55; BIBL. 9 REF.Article

ANAESTHESIE BEI KUGELBERG-WELANDER-SYNDROM (JUVENILE PSEUDOMYOPATHISCHE MUSKELATROPHIE) = ANESTHESIE DANS LE SYNDROME DE KUGELBERG, WELANDER (ATROPHIE MUSCULAIRE JUVENILE PSEUDOMYOPATHIQUE)GOETZ E; BOGOSYAN S.1980; ANAESTH. INTENSIVTHER. NOTFALLMED.; DEU; DA. 1980; VOL. 15; NO 4; PP. 360-362; ABS. ENG; BIBL. 11 REF.Article

JUVENILE SPINAL MUSCULAR ATROPHY: A NEW HEXOSAMINIDASE DEFICIENCY PHENOTYPEJOHNSON WG; WIGGER HJ; KARP HR et al.1982; ANN. NEUROL.; ISSN 0364-5134; USA; DA. 1982; VOL. 11; NO 1; PP. 11-16; BIBL. 23 REF.Article

Carnitine and acyltransferase in experimental neurogenic atrophies: changes with treatmentBRESOLIN, N; FREDDO, L; TEGAZZIN, V et al.Journal of neurology. 1985, Vol 231, Num 4, pp 170-175, issn 0340-5354Article

A CASE OF THE KUGELBERG-WELANDER SYNDROME COMPLICATED WITH CARDIAC LESIONSKIMURA S; YOKOTA H; TATEDA K et al.1980; JAP. HEART J.; JPN; DA. 1980; VOL. 21; NO 3; PP. 417-422; BIBL. 10 REF.Article

MYOPATHOLOGIE CHRONISCHER DENERVATIONSPROZESSE = MYOPATHOLOGIE DES PROCESSUS DE DENERVATION CHRONIQUESBRENNI G; JERUSALEM F; SCHILLER H et al.1981; NERVENARZT; ISSN 0028-2804; DEU; DA. 1981; VOL. 52; NO 12; PP. 692-702; BIBL. 35 REF.Article

MYOCARDIAL ULTRASTRUCTURAL CHANGES IN KUGELBERG-WELANDER SYNDROME.TANAKA H; NISHI S; NURUKI K et al.1977; BRIT. HEART J.; G.B.; DA. 1977; VOL. 39; NO 12; PP. 1390-1393; BIBL. 16 REF.Article

SENSORY NERVE CONDUCTION IN THE SPINAL MUSCULAR ATROPHIES.SCHWARTZ MS; MOOSA A.1977; DEVELOP. MED. CHILD NEUROL.; G.B.; DA. 1977; VOL. 19; NO 1; PP. 50-53; ABS. FR. ALLEM. ESP.; BIBL. 14 REF.Article

THE EFFECT OF HYDROCORTISONE ON THE SERUM CREATINE KINASE ACTIVITY OF MUSCLES DISEASES.CZYZEWSKI K.1977; J. NEUROL.; GERM.; DA. 1977; VOL. 216; NO 4; PP. 283-287; ABS. ALLEM.; BIBL. 12 REF.Article

A FAMILY OF JUVENILE PROXIMAL SPINAL MUSCULAR ATROPHY WITH DOMINANT INHERITANCE.CAO A; CIANCHETTI C; CALISTI L et al.1976; J. MED. GENET.; G.B.; DA. 1976; VOL. 13; NO 2; PP. 131-135; BIBL. 22 REF.Article

Cardiopulmonary response to exercise in patients with neuromuscular diseasesLYAGER, S; NAERAA, N; PEDERSEN, O. F et al.Respiration (Basel). 1984, Vol 45, Num 2, pp 89-99, issn 0025-7931Article

SPINAL PROGRESSIVE MUSCULAR ATROPHY WITH PROXIMAL MUSCLE INVOLVEMENTOTA T; IWASAKI I; NAKAMURA Y et al.1978; BULL. YAMAGUCHI MED. SCH.; JPN; DA. 1978; VOL. 25; NO 1-6; PP. 33-39; BIBL. 12 REF.Article

LES FORMES "INTERMEDIAIRES" DE L'AMYOTROPHIE SPINALE INFANTILE. A PROPOS DE VINGT OBSERVATIONS PERSONNELLES.POU SERRADELL A; MONTSERRAT L; UGARTE A et al.1978; REV. NEUROL.; FR.; DA. 1978; VOL. 134; NO 1; PP. 35-44; ABS. ANGL.; BIBL. 16 REF.Article

CHRONIC SPINAL MUSCULAR ATROPHY OF FACIOSCAPULOHUMERAL TYPE.FURUKAWA T; TOYOKURA Y.1976; J. MED. GENET.; G.B.; DA. 1976; VOL. 13; NO 4; PP. 285-289; BIBL. 26 REF.Article

ENFERMEDADES DE LA MOTONEURONA DEL ASTA ANTERIOR, DE PREFERENTE APARICION EN LA INFANCIA (W.-H.) Y EN LA JUVENTUD (W.-K.-W.). RELACIONES ELECTROCLINICAS. = MALADIES DU MOTONEURONE DE LA CORNE ANTERIEURE, D'APPARITION PREFERENTIELLE DANS L'ENFANCE (WERDNIG HOFFMANN) ET DANS L'ADOLESCENCE (WOHLFART KUGELBERG WELANDER). RELATIONS ELECTROCLINIQUESPEREZ MAIQUEZ F; PERMUY RODRIGUEZ J.1976; ARCH. NEUROBIOL.; ESP.; DA. 1976; VOL. 39; NO 4; PP. 273-284; ABS. ANGL.; BIBL. 2 P. 1/2Article

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