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kw.\*:("LEIGH DISEASE")

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ERYTHROCYTE TRANSKETOLASE ACTIVITY IN SUSPECTED CASES OF LEIGH'S DISEASE, OR SUBACUTE NECROTISING ENCEPHALOMYELOPATHYMCBURNEY A; LEIGH D; MCILWAIN H et al.1980; ARCH. DIS. CHILD.; ISSN 0003-9888; GBR; DA. 1980; VOL. 55; NO 10; PP. 789-794; BIBL. 29 REF.Article

COMPUTERIZED TOMOGRAPHY IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY (LEIGH DISEASE)SCHWARTZ WJ; HUTCHISON HT; BERG BO et al.1981; ANN. NEUROL.; ISSN 0364-5134; USA; DA. 1981; VOL. 10; NO 3; PP. 268; BIBL. 6 REF.Article

JUVENILE FORM DER SUBAKUTEN NEKROTISIERUNDEN ENCEPHALOMYELOPATHIE (LEIGH) MIT UNGEWOEHNLICHER ZNS-LOKALISATION = FORME JUVENILE D'ENCEPHALOMYELOPATHIE NECROSANTE SUBAIGUE (LEIGH) AVEC LOCALISATION INHABITUELLE AU NIVEAU DU SYSTEME NERVEUX CENTRALLAHL R.1981; ACTA NEUROPATHOL.; ISSN 0001-6322; DEU; DA. 1981; VOL. 55; NO 3; PP. 237-242; ABS. ENG; BIBL. 31 REF.Article

LEIGH'S DISEASE IN AN ADULT WITH EVIDENCE OF "INHIBITOR FACTOR" IN FAMILY MEMBERSWHETSELL WO JR; PLAITAKIS A.1978; ANN. NEUROL.; USA; DA. 1978; VOL. 3; NO 6; PP. 519-524; BIBL. 15 REF.Article

LEIGH'S SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY: POSSIBLE DIAGNOSIS BY CT SCANCHI JG; HAN WOOK YOO; KI KYUN CHANG et al.1981; NEURORADIOLOGY; ISSN 0028-3940; DEU; DA. 1981; VOL. 22; NO 3; PP. 141-144; BIBL. 10 REF.Article

Encéphalopathie nécrosante subaiguë, maladie de Leigh: à propos d'un cas = Subacute necrotizing encephalopathy (Leigh's disease). Case reportDELISLE, M. B; NETTER, J. C; PEYRILLE, F et al.Annales de pathologie (Paris). 1985, Vol 5, Num 4-5, pp 313-317, issn 0242-6498Article

BETEILIGUNG DES OPTISCHEN SYSTEMS UND DER AUGENMUSKELKERNE BEI DER SUBAKUTEN NEKROTISIERENDEN ENZEPHALOMYELOPATHIE (LEIGH) AUS PATHOMORPHISCHER SICHT. (FALLDARSTELLUNG) = PARTICIPATION DU SYSTEME OPTIQUE ET DES NOYAUX DES MUSCLES OCULAIRES DANS L'ENCEPHALOMYELOPATHIE NECROSANTE SUBAIGUE (LEIGH) D'UN POINT DE VUE MORPHOLOGIQUE (OBSERVATION)LAHL R.1981; KLIN. MONATSBL. AUGENHEILKD.; ISSN 0023-2165; DEU; DA. 1981; VOL. 178; NO 6; PP. 449-452; ABS. ENG; BIBL. 17 REF.Article

MYELIN STUDIES IN A CASE OF SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY (SNE). CLINICAL, HISTOCHEMICAL, AND NEUROCHEMICAL INVESTIGATIONS.KOHLSCHUTTER A; KRAUS RUPPERT R; ROHRER T et al.1978; J. NEUROPATHOL. EXPER. NEUROL.; U.S.A.; DA. 1978; VOL. 37; NO 2; PP. 155-164; BIBL. 20 REF.Article

L'ENCEPHALOPATHIE NECROSANTE SUBAIGUE (MALADIE DE LEIGH-FEIGIN-WOLF). A PROPOS DE DEUX CAS DANS UNE MEME FAMILLE.JOLY JB; RICHARD P; LEPAVEC P et al.1978; BORDEAUX MED.; FR.; DA. 1978; VOL. 11; NO 12; PP. 1021-1029; ABS. ANGL.; BIBL. 3 REF.Article

X-LINKED LEIGH'S SYNDROMEBENKE PJ; PARKER JC JR; LUBS ML et al.1982; HUMAN GENETICS; ISSN 0340-6717; DEU; DA. 1982; VOL. 62; NO 1; PP. 53-59; BIBL. 58 REF.Article

PYRUVATE CARBOXYLASE DEFICIENCY: AN ALLEGED BIOCHEMICAL CAUSE OF LEIGH'S DISEASEMURPHY JV; ISOHASHI F; WEINBERG MB et al.1981; PEDIATRICS EVANSTON; ISSN 0031-4005; USA; DA. 1981; VOL. 68; NO 3; PP. 401-404; BIBL. 29 REF.Article

MOTOR NERVE CONDUCTION VELOCITIES IN LEIGH'S ENCEPHALOMYELOPATHY.MOOSA A.1978; ARCH. DIS. CHILDH.; G.B.; DA. 1978; VOL. 53; NO 1; PP. 62-65; BIBL. 13 REF.Article

BEITRAG ZUR SUBAKUTEN NEKROTISIERENDEN ENZEPHALOMYELOPATHIE (LEIGH-SYNDROM). = CONTRIBUTIONS A L'ETUDE DE L'ENCEPHALOMYELOPATHIE NECROSANTE SUBAIGUE (SYNDROME DE LEIGH)HENKER J; BARZ H; BOHME B et al.1977; KINDERAERZTL. PRAXIS; DTSCH.; DA. 1977; VOL. 45; NO 3; PP. 121-124; BIBL. 14 REF.Article

SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY IN A NEONATAL INFANT.FEIGIN I; HYO SOON KIM.1977; J. NEUROPATHOL. EXPER. NEUROL.; U.S.A.; DA. 1977; VOL. 36; NO 2; PP. 364-372; BIBL. 20 REF.Article

ANESTHESIA FOR A CHILD WITH LEIGH'S SYNDROMEWARD DS.1981; ANESTHESIOLOGY; ISSN 0003-3022; USA; DA. 1981; VOL. 55; NO 1; PP. 80-81; BIBL. 11 REF.Article

TOMODENSITOMETRIE CRANIENNE DANS LA MALADIE DE LEIGH: UNE OBSERVATIONOLLIVIER A; DIEBLER C.1980; NOUV. PRESSE MED.; ISSN 0301-1518; FRA; DA. 1980; VOL. 9; NO 33; PP. 2355; BIBL. 2 REF.Article

COMPLEX ACID-BASE DISORDERS IN SUBACUTE NECROTIZING ENCEPHALOMYEOLOPATHY (LEIGH'S SYNDROME).HIRSCHMAN GH; CHAN JCM.1978; PEDIATRICS; U.S.A.; DA. 1978; VOL. 61; NO 2; PP. 278-281; BIBL. 14 REF.Article

MITOCHONDRIAL CYTOPATHY OR LEIGH'S SYNDROME. MITOCHONDRIAL ABNORMALITIES IN SPONGIFORM ENCEPHALOPATHIESEGGER J; WYNNE WILLIAMS CJE; ERDOHAZI M et al.1982; NEUROPEDIATRICS; ISSN 0174-304X; DEU; DA. 1982; VOL. 13; NO 4; PP. 219-224; BIBL. 46 REF.Article

STUDIES ON PYRUVATE CARBOXYLASE, PYRUVATE DECARBOXYLASE AND LIPOAMIDE DEHYDROGENASE IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHYHANSEN TL; CHRISTENSEN E; BRANDT NJ et al.1982; ACTA PAEDIATR. SCAND.; ISSN 0001-656X; SWE; DA. 1982; VOL. 71; NO 2; PP. 263-267; BIBL. 30 REF.Article

CHRONIC LEIGH DISEASE: A GENETIC AND BIOCHEMICAL STUDYPLAITAKIS A; WHETSELL O JR; COOPER JR et al.1980; ANN. NEUROL.; USA; DA. 1980; VOL. 7; NO 4; PP. 304-310; BIBL. 25 REF.Article

A PROPOS DE 2 OBSERVATIONS FAMILIALES DE SYNDROME DE LEIGH.DELGADO JL.1978; MONTPELLIER; QUICK PRINT; DA. 1978; PP. (80P.); H.T. 12; BIBL. 10 P.; (THESE DOCT. MED.; MONTPELLIER)Thesis

FURTHER OBSERVATIONS ON SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY IN ADULTS.FEIGIN I; BUDZILOVICH GN.1977; J. NEUROPATHOL. EXPER. NEUROL.; U.S.A.; DA. 1977; VOL. 36; NO 1; PP. 128-139; BIBL. 1 P. 1/2Article

THIAMINE TRIPHOSPHATE LEVELS AND HISTOPATHOLOGY. CORRELATION IN LEIGH DISEASE.PINCUS JH; SOLITARE GB; COOPER JR et al.1976; ARCH. NEUROL.; U.S.A.; DA. 1976; VOL. 33; NO 11; PP. 759-763; BIBL. 20 REF.Article

LA MALADIE DE LEIGH-FEIGIN-WOLF: (A PROPOS DE 2 OBSERVATIONS)DEGROISSE MICHEL.sd; FRA; DA. S.D.; 308; 116 P.-3 PL.; 30 CM; BIBL. 115 REF.; TH.: MED./LILLE 2/1978Thesis

ABNORMAL ACTIVATION OF PYRUVATE DEHYDROGENASE IN LEIGH DISEASE FIBROBLASTSSORBI S; BLASS JP.1982; NEUROLOGY; ISSN 0028-3878; USA; DA. 1982; VOL. 32; NO 5; PP. 555-558; BIBL. 19 REF.Article

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