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INVESTIGATIONS IN ENZYME REPLACEMENT THERAPY IN LIPID STORAGE DISEASESBRADY RO; PENTCHEV PG; GAL AE et al.1975; FEDER. PROC.; U.S.A.; DA. 1975; VOL. 34; NO 5; PP. 1310-1315; BIBL. 35REF.Serial Issue

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L-GLUCOSYLCERAMIDE: SYNTHESIS, PROPERTIES, AND RESISTANCE TO CATABOLISM BY GLUCOCEREBROSIDASE IN VITROGAL AF; PENTCHEV PG; MASSEY JM et al.1979; PROC. NATION. ACAD. SCI.; USA; DA. 1979; VOL. 76; NO 7; PP. 3083-3086; BIBL. 15 REF.Article

THE DISTRIBUTION OF GLUCOCEREBROSIDE IN THE LIVER OF PATIENTS WITH GAUCHER'S DISEASEGAL AE; PENTCHEV PG; BARRANGER JA et al.1979; ANAL BIOCHEM.; USA; DA. 1979; VOL. 95; NO 1; PP. 127-132; BIBL. 14 REF.Article

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A NEW FORM OF NIEMANN-PICK DISEASE CHARACTERISED BY TEMPERATURE-LABILE SPHINGOMYELINASESCHNEIDER EL; PENTCHEV PG; HIBBERT SR et al.1978; J. MED. GENET.; GBR; DA. 1978; VOL. 15; NO 5; PP. 370-374; BIBL. 19 REF.Article

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STUDIES OF LYSOSOMAL FUNCTION. I. METABOLISM OF SOME COMPLEX LIPIDS BY ISOLATED HEPATOCYTES AND KUPFFER CELLSBARRANGER JA; PENTCHEV PG; FURBISH FS et al.1978; BIOCHEM. BIOPHYS. RES. COMMUNIC.; USA; DA. 1978; VOL. 83; NO 3; PP. 1055-1060; BIBL. 28 REF.Article

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NIEMANN-PICK DISEASE EXPERIMENTAL MODEL: SPHINGOMYELINASE REDUCTION INDUCED BY AY-9944.SAKURAGAWA N; SAKURAGAWA M; KUWABARA T et al.1977; SCIENCE; U.S.A.; DA. 1977; VOL. 196; NO 4287; PP. 317-319; BIBL. 14 REF.Article

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