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Results 1 to 25 of 128

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THE PRESENCE AND POSSIBLE FUNCTION OF METHYLMALONYL COA MUTASE AND PROPIONYL COA CARBOXYLASE IN SPIROMETRA MANSONOIDES.TKACHUCK RD; SAZ HJ; WEINSTEIN PP et al.1977; J. PARASITOL.; U.S.A.; DA. 1977; VOL. 63; NO 5; PP. 769-774; BIBL. 19 REF.Article

MOLECULAR BASIS FOR GENETIC COMPLEMENTATION IN PROPIONYL COA CARBOXYLASE DEFICIENCYWOLF B.1980; EXPER. CELL RES.; USA; DA. 1980; VOL. 125; NO 2; PP. 502-507; BIBL. 22 REF.Article

PYRUVATE CARBOXYLASE AND PROPIONYL-COA CARBOXYLASE AS ANAPLEROTIC ENZYMES IN SKELETAL MUSCLE MITOCHONDRIADAVIS EJ; SPYDEVOLD O; BREMER J et al.1980; EUR. J. BIOCHEM.; ISSN 0014-2956; DEU; DA. 1980; VOL. 110; NO 1; PP. 255-262; BIBL. 24 REF.Article

ISOLATION AND CHARACTERIZATION OF PROPIONYL-COA CARBOXYLASE FROM NORMAL HUMAN LIVER: EVIDENCE FOR A PROTOMERIC TETRAMER OF NONIDENTICAL SUBUNITSKALOUSEK F; DARIGO MD; ROSENBERG LE et al.1980; J. BIOL. CHEM.; USA; DA. 1980; VOL. 255; NO 1; PP. 60-65; BIBL. 35 REF.Article

LEUKOCYTE PROPIONYL-COA CARBOXYLASE DEFICIENCY IN A PATIENT WITH KETOTIC HYPERGLYCINAEMIADEL VALLE JA; MERINERO B; GARCIA MJ et al.1980; J. INHERIT. METAB. DIS.; GBR; DA. 1980; VOL. 3; NO 3; PP. 93; BIBL. 4 REF.Article

PURIFICATION OF HUMAN LIVER PROPIONYL-COA CARBOXYLASE BY CARBON TETRACHLORIDE EXTRACTION AND MONOMERIC AVIDIN AFFINITY CHROMATOGRAPHYGRAVEL RA; LAM KF; MAHURAN D et al.1980; ARCH. BIOCHEM. BIOPHYS.; USA; DA. 1980; VOL. 201; NO 2; PP. 669-673; BIBL. 22 REF.Article

ARE CARBOXYLATIONS INVOLVING BIOTIN CONCERTED OR NONCONCERTED.STUBBE JA; FISH S; ABELES RH et al.1980; J. BIOL. CHEM.; USA; DA. 1980; VOL. 255; NO 1; PP. 236-242; BIBL. 19 REF.Article

BIOCHEMICAL CHARACTERIZATION OF MUTANT PROPIONYL COA CARBOXYLASE FROM TWO MINOR GENETIC COMPLEMENTATION GROUPSWOLF B.1979; BIOCHEM. GENET.; USA; DA. 1979; VOL. 17; NO 7-8; PP. 703-707; BIBL. 6 REF.Article

GENETIC COMPLEMENTATION OF PROPIONYL-COA CARBOXYLASE DEFICIENCY IN CULTURED HUMAN FIBROBLASTS.GRAVEL RA; KAM FONG LAM; SCULLY KJ et al.1977; AMER. J. HUM. GENET.; U.S.A.; DA. 1977; VOL. 29; NO 4; PP. 378-388; BIBL. 1 P. 1/2Article

2-HYDROXY-2-METHYLSUCCINIC ACID: A URINARY METABOLITE IN PROPIONYL-COA CARBOXYLASE DEFICIENCYGRETER J; LINDSTEDT S; SEEMAN H et al.1980; CLIN. CHIM. ACTA; NLD; DA. 1980; VOL. 106; NO 1; PP. 103-106; BIBL. 9 REF.Article

BIOCHEMICAL DIFFERENCES BETWEEN MUTANT PROPIONYL-COA CARBOXYLASES FROM TWO COMPLEMENTATION GROUPSWOLF B; HSIA E; ROSENBERG LE et al.1978; AMER. J. HUM. GENET.; USA; DA. 1978; VOL. 30; NO 5; PP. 455-464; BIBL. 24 REF.Article

MODIFICATION OF FIBROBLAST PROPIONYL COA CARBOXYLASE ACTIVITY BY VALINE AS A POSSIBLE DIAGNOSTIC TECHNIQUE IN NON-KETOTIC HYPERGLYCINAEMIAFOX JS.1982; JOURNAL OF INHERITED METABOLIC DISEASE; ISSN 0141-8955; GBR; DA. 1982; VOL. 5; SUPPL. 2; PP. 121-123; BIBL. 19 REF.Article

IMMUNOLOGICAL STUDIES OF PROPIONYL COA CARBOXYLASE IN LIVERS AND FIBROBLASTS OF PATIENTS WITH PROPIONIC ACIDEMIAMCKEON C; EANES RZ; FALL RR et al.1980; CLIN. CHIM. ACTA; NLD; DA. 1980; VOL. 101; NO 2-3; PP. 217-223; BIBL. 17 REF.Article

STIMULATION OF PROPIONYL COA AND BETA -METHYLCROTONYL COA CARBOXYLASE ACTIVITIES IN HUMAN LEUKOCYTES AND CULTURED FIBROBLASTS BY BIOTINWOLF B; ROSENBERG LE.1979; PEDIATR. RES.; USA; DA. 1979; VOL. 13; NO 11; PP. 1275-1279; BIBL. 26 REF.Article

ASYMPTOMATIC PROPIONYL COA CARBOXYLASE DEFICIENCY IN A 13-YEAR-OLD GIRLWOLF B; PAULSEN EP; HSIA YE et al.1979; J. PEDIATR.; USA; DA. 1979; VOL. 95; NO 4; PP. 563-565; BIBL. 9 REF.Article

BOVINE KIDNEY 3-METHYLCROTONYL-COA AND PROPIONYL-COA CARBOXYLASES: EACH ENZYME CONTAINS NONIDENTICAL SUBUNITSLAU EP; COCHRAN BC; MUNSON L et al.1979; PROC. NATION. ACAD. SCI. USA; USA; DA. 1979; VOL. 76; NO 1; PP. 214-218; BIBL. 32 REF.Article

DETECTION OF PROPIONYL-COA CARBOXYLASE ACTIVITY AFTER ELECTROPHORESISGRAVEL RA; SCULLY KJ; HSIA YE et al.1978; BIOCHEM. MED.; USA; DA. 1978; VOL. 20; NO 1; PP. 1-6; BIBL. 15 REF.Article

ABSENCE OF CROSS-REACTING MATERIAL IN ISOLATED PROPIONYL COA CARBOXYLASE DEFICIENCY: NATURE OF RESIDUAL CARBOXYLATING ACTIVITYKALOUSEK F; ORSULAK MD; ROSENBERG LR et al.1983; AMERICAN JOURNAL OF HUMAN GENETICS; ISSN 0002-9297; USA; DA. 1983; VOL. 35; NO 3; PP. 409-420; BIBL. 25 REF.Article

INHIBITION OF THE GLYCINE CLEAVAGE SYSTEM BY BRANCHED-CHAIN AMINO ACID METABOLITESKOLVRAA S.1979; PEDIATR. RES.; USA; DA. 1979; VOL. 13; NO 8; PP. 889-893; BIBL. 34 REF.Article

EFFECTS OF PREGNANCY AND LACTATION IN SHEEP ON THE METABOLISM OF PROPIONATE BY THE RUMINAL MUCOSA AND ON SOME ENZYMIC ACTIVITIES IN THE RUMINAL MUCOSA = EFFETS DE LA GESTATION ET DE LA LACTATION DE LA BREBIS SUR LE METABOLISME DU PROPIONATE PAR LA MUQUEUSE DU RUMEN ET SUR QUELQUES ACTIVITES ENZYMATIQUES DANS LA MUQUEUSE DU RUMENWEEKES TEC.1972; J. AGRIC. SCI.; G.B.; DA. 1972; VOL. 79; NO 3; PP. 409-421; BIBL. 1 P.Article

DIETARY TREATMENT AND BIOCHEMICAL STUDIES ON A NEONATAL CASE OF PROPIONYL-COA CARBOXYLASE DEFICIENCYDEL VALLE JA; MERINERO B; JIMENEZ A et al.1982; J. INHERIT. METAB. DIS.; ISSN 0141-8955; GBR; DA. 1982; VOL. 5; NO 2; PP. 121-124; BIBL. 17 REF.Article

MAGNESIUM AND MAGNESIUM ADENOSINE TRIPHOSPHATE ACTIVATION OF HUMAN PROPIONYL COA CARBOXYLASE AND BETA -METHYLCROTONYL COA CARBOXYLASEMCKEON C; WOLF B.1982; ENZYME; ISSN 0013-9432; CHE; DA. 1982; VOL. 28; NO 1; PP. 76-81; BIBL. 13 REF.Article

EVALUATION OF BIOTIN RESPONSIVENESS IN CULTURED FIBROBLASTS FROM PATIENTS WITH PROPIONIC ACIDEMIA: ABSENCE OF RESPONSE BY STRUCTURALLY ALTERED CARBOXYLASESWOLF B.1979; BIOCHEM. GENET.; USA; DA. 1979; VOL. 17; NO 7-8; PP. 709-713; BIBL. 11 REF.Article

BIOTIN DEFICIENCY IN THE CAT AND THE EFFECT ON HEPATIC PROPIONYL COA CARBOXYLASE.CAREY CJ; MORRIS JG.1977; J. NUTRIT.; U.S.A.; DA. 1977; VOL. 107; NO 2; PP. 330-334; BIBL. 17 REF.Article

PROPRIONYL COENZYME A CARBOXYLASE DEFICIENCY PRESENTING AS NON-KETOTIC HYPERGLYCINAEMIAHARRIS DJ; THOMPSON RM; WOLF B et al.1981; J. MED. GENET.; ISSN 0022-2593; GBR; DA. 1981; VOL. 18; NO 2; PP. 156-157; BIBL. 8 REF.Article

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