kw.\*:("PROPIONYL-COA")
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THE PRESENCE AND POSSIBLE FUNCTION OF METHYLMALONYL COA MUTASE AND PROPIONYL COA CARBOXYLASE IN SPIROMETRA MANSONOIDES.TKACHUCK RD; SAZ HJ; WEINSTEIN PP et al.1977; J. PARASITOL.; U.S.A.; DA. 1977; VOL. 63; NO 5; PP. 769-774; BIBL. 19 REF.Article
MOLECULAR BASIS FOR GENETIC COMPLEMENTATION IN PROPIONYL COA CARBOXYLASE DEFICIENCYWOLF B.1980; EXPER. CELL RES.; USA; DA. 1980; VOL. 125; NO 2; PP. 502-507; BIBL. 22 REF.Article
PYRUVATE CARBOXYLASE AND PROPIONYL-COA CARBOXYLASE AS ANAPLEROTIC ENZYMES IN SKELETAL MUSCLE MITOCHONDRIADAVIS EJ; SPYDEVOLD O; BREMER J et al.1980; EUR. J. BIOCHEM.; ISSN 0014-2956; DEU; DA. 1980; VOL. 110; NO 1; PP. 255-262; BIBL. 24 REF.Article
ISOLATION AND CHARACTERIZATION OF PROPIONYL-COA CARBOXYLASE FROM NORMAL HUMAN LIVER: EVIDENCE FOR A PROTOMERIC TETRAMER OF NONIDENTICAL SUBUNITSKALOUSEK F; DARIGO MD; ROSENBERG LE et al.1980; J. BIOL. CHEM.; USA; DA. 1980; VOL. 255; NO 1; PP. 60-65; BIBL. 35 REF.Article
LEUKOCYTE PROPIONYL-COA CARBOXYLASE DEFICIENCY IN A PATIENT WITH KETOTIC HYPERGLYCINAEMIADEL VALLE JA; MERINERO B; GARCIA MJ et al.1980; J. INHERIT. METAB. DIS.; GBR; DA. 1980; VOL. 3; NO 3; PP. 93; BIBL. 4 REF.Article
PURIFICATION OF HUMAN LIVER PROPIONYL-COA CARBOXYLASE BY CARBON TETRACHLORIDE EXTRACTION AND MONOMERIC AVIDIN AFFINITY CHROMATOGRAPHYGRAVEL RA; LAM KF; MAHURAN D et al.1980; ARCH. BIOCHEM. BIOPHYS.; USA; DA. 1980; VOL. 201; NO 2; PP. 669-673; BIBL. 22 REF.Article
ARE CARBOXYLATIONS INVOLVING BIOTIN CONCERTED OR NONCONCERTED.STUBBE JA; FISH S; ABELES RH et al.1980; J. BIOL. CHEM.; USA; DA. 1980; VOL. 255; NO 1; PP. 236-242; BIBL. 19 REF.Article
BIOCHEMICAL CHARACTERIZATION OF MUTANT PROPIONYL COA CARBOXYLASE FROM TWO MINOR GENETIC COMPLEMENTATION GROUPSWOLF B.1979; BIOCHEM. GENET.; USA; DA. 1979; VOL. 17; NO 7-8; PP. 703-707; BIBL. 6 REF.Article
GENETIC COMPLEMENTATION OF PROPIONYL-COA CARBOXYLASE DEFICIENCY IN CULTURED HUMAN FIBROBLASTS.GRAVEL RA; KAM FONG LAM; SCULLY KJ et al.1977; AMER. J. HUM. GENET.; U.S.A.; DA. 1977; VOL. 29; NO 4; PP. 378-388; BIBL. 1 P. 1/2Article
2-HYDROXY-2-METHYLSUCCINIC ACID: A URINARY METABOLITE IN PROPIONYL-COA CARBOXYLASE DEFICIENCYGRETER J; LINDSTEDT S; SEEMAN H et al.1980; CLIN. CHIM. ACTA; NLD; DA. 1980; VOL. 106; NO 1; PP. 103-106; BIBL. 9 REF.Article
BIOCHEMICAL DIFFERENCES BETWEEN MUTANT PROPIONYL-COA CARBOXYLASES FROM TWO COMPLEMENTATION GROUPSWOLF B; HSIA E; ROSENBERG LE et al.1978; AMER. J. HUM. GENET.; USA; DA. 1978; VOL. 30; NO 5; PP. 455-464; BIBL. 24 REF.Article
MODIFICATION OF FIBROBLAST PROPIONYL COA CARBOXYLASE ACTIVITY BY VALINE AS A POSSIBLE DIAGNOSTIC TECHNIQUE IN NON-KETOTIC HYPERGLYCINAEMIAFOX JS.1982; JOURNAL OF INHERITED METABOLIC DISEASE; ISSN 0141-8955; GBR; DA. 1982; VOL. 5; SUPPL. 2; PP. 121-123; BIBL. 19 REF.Article
IMMUNOLOGICAL STUDIES OF PROPIONYL COA CARBOXYLASE IN LIVERS AND FIBROBLASTS OF PATIENTS WITH PROPIONIC ACIDEMIAMCKEON C; EANES RZ; FALL RR et al.1980; CLIN. CHIM. ACTA; NLD; DA. 1980; VOL. 101; NO 2-3; PP. 217-223; BIBL. 17 REF.Article
STIMULATION OF PROPIONYL COA AND BETA -METHYLCROTONYL COA CARBOXYLASE ACTIVITIES IN HUMAN LEUKOCYTES AND CULTURED FIBROBLASTS BY BIOTINWOLF B; ROSENBERG LE.1979; PEDIATR. RES.; USA; DA. 1979; VOL. 13; NO 11; PP. 1275-1279; BIBL. 26 REF.Article
ASYMPTOMATIC PROPIONYL COA CARBOXYLASE DEFICIENCY IN A 13-YEAR-OLD GIRLWOLF B; PAULSEN EP; HSIA YE et al.1979; J. PEDIATR.; USA; DA. 1979; VOL. 95; NO 4; PP. 563-565; BIBL. 9 REF.Article
BOVINE KIDNEY 3-METHYLCROTONYL-COA AND PROPIONYL-COA CARBOXYLASES: EACH ENZYME CONTAINS NONIDENTICAL SUBUNITSLAU EP; COCHRAN BC; MUNSON L et al.1979; PROC. NATION. ACAD. SCI. USA; USA; DA. 1979; VOL. 76; NO 1; PP. 214-218; BIBL. 32 REF.Article
DETECTION OF PROPIONYL-COA CARBOXYLASE ACTIVITY AFTER ELECTROPHORESISGRAVEL RA; SCULLY KJ; HSIA YE et al.1978; BIOCHEM. MED.; USA; DA. 1978; VOL. 20; NO 1; PP. 1-6; BIBL. 15 REF.Article
ABSENCE OF CROSS-REACTING MATERIAL IN ISOLATED PROPIONYL COA CARBOXYLASE DEFICIENCY: NATURE OF RESIDUAL CARBOXYLATING ACTIVITYKALOUSEK F; ORSULAK MD; ROSENBERG LR et al.1983; AMERICAN JOURNAL OF HUMAN GENETICS; ISSN 0002-9297; USA; DA. 1983; VOL. 35; NO 3; PP. 409-420; BIBL. 25 REF.Article
INHIBITION OF THE GLYCINE CLEAVAGE SYSTEM BY BRANCHED-CHAIN AMINO ACID METABOLITESKOLVRAA S.1979; PEDIATR. RES.; USA; DA. 1979; VOL. 13; NO 8; PP. 889-893; BIBL. 34 REF.Article
EFFECTS OF PREGNANCY AND LACTATION IN SHEEP ON THE METABOLISM OF PROPIONATE BY THE RUMINAL MUCOSA AND ON SOME ENZYMIC ACTIVITIES IN THE RUMINAL MUCOSA = EFFETS DE LA GESTATION ET DE LA LACTATION DE LA BREBIS SUR LE METABOLISME DU PROPIONATE PAR LA MUQUEUSE DU RUMEN ET SUR QUELQUES ACTIVITES ENZYMATIQUES DANS LA MUQUEUSE DU RUMENWEEKES TEC.1972; J. AGRIC. SCI.; G.B.; DA. 1972; VOL. 79; NO 3; PP. 409-421; BIBL. 1 P.Article
DIETARY TREATMENT AND BIOCHEMICAL STUDIES ON A NEONATAL CASE OF PROPIONYL-COA CARBOXYLASE DEFICIENCYDEL VALLE JA; MERINERO B; JIMENEZ A et al.1982; J. INHERIT. METAB. DIS.; ISSN 0141-8955; GBR; DA. 1982; VOL. 5; NO 2; PP. 121-124; BIBL. 17 REF.Article
MAGNESIUM AND MAGNESIUM ADENOSINE TRIPHOSPHATE ACTIVATION OF HUMAN PROPIONYL COA CARBOXYLASE AND BETA -METHYLCROTONYL COA CARBOXYLASEMCKEON C; WOLF B.1982; ENZYME; ISSN 0013-9432; CHE; DA. 1982; VOL. 28; NO 1; PP. 76-81; BIBL. 13 REF.Article
EVALUATION OF BIOTIN RESPONSIVENESS IN CULTURED FIBROBLASTS FROM PATIENTS WITH PROPIONIC ACIDEMIA: ABSENCE OF RESPONSE BY STRUCTURALLY ALTERED CARBOXYLASESWOLF B.1979; BIOCHEM. GENET.; USA; DA. 1979; VOL. 17; NO 7-8; PP. 709-713; BIBL. 11 REF.Article
BIOTIN DEFICIENCY IN THE CAT AND THE EFFECT ON HEPATIC PROPIONYL COA CARBOXYLASE.CAREY CJ; MORRIS JG.1977; J. NUTRIT.; U.S.A.; DA. 1977; VOL. 107; NO 2; PP. 330-334; BIBL. 17 REF.Article
PROPRIONYL COENZYME A CARBOXYLASE DEFICIENCY PRESENTING AS NON-KETOTIC HYPERGLYCINAEMIAHARRIS DJ; THOMPSON RM; WOLF B et al.1981; J. MED. GENET.; ISSN 0022-2593; GBR; DA. 1981; VOL. 18; NO 2; PP. 156-157; BIBL. 8 REF.Article