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LIGHT INDUCED PROTOPORPHYRIN RELEASE FROM ERYTHROCYTES IN ERYTHROPOIETIC PROTOPORPHYRIASANDBERG S; BRUN A.1982; J. CLIN. INVEST.; ISSN 0021-9738; USA; DA. 1982; VOL. 70; NO 3; PP. 693-698; BIBL. 29 REF.Article

LIENALE UND INTRAVASALE KORPUSKULAERE HAEMOLYSE BEI ERYTHROPOIETISCHER PROTOPORPHYRIE = HEMOLYSE SPLENIQUE ET INTRAVASCULAIRE DANS LA PROTOPORPHYRIE ERYTHROPOIETIQUEROSENMUND A; ZIEGLER G; RUEGG R et al.1975; SCHWEIZ. MED. WSCHR.; SCHWEIZ; DA. 1975; VOL. 105; NO 47; PP. 1596; ABS. ANGL.; BIBL. 2 REF.Article

ERYTHROPOIETIC PROTOPORPHYRIA. HISTOCHEMICAL STUDY OF HYALINE MATERIALSASAI Y.1973; ACTA DERMATO-VENEREOL.; SUEDE; DA. 1973; VOL. 53; NO 3; PP. 179-184; BIBL. 20REF.Serial Issue

Light-induced released of protoporphyrin, but not of zinc protoporphyrin, from erythrocytes in a patient with greatly elevated erythrocyte protoporphyrinSANDBERG, S; TALSTAD, I; HØVDING, G et al.Blood. 1983, Vol 62, Num 4, pp 846-851, issn 0006-4971Article

CHARAKTERISIERUNG DES ENZYMDEFEKTS BEI ERYTHROPOETISCHER PROTOPORPHYRIE = CARACTERISATION DU DEFICIT ENZYMATIQUE DANS LA PROTOPORPHYRIE ERYTHROPOIETIQUEDUBBELMAN TMAR; DE GEIJ AFPM; VAN STEVENINCK J et al.1978; THERAPIEWOCHE; DEU; DA. 1978; VOL. 28; NO 44; PP. 8448-8451; (2 P.); BIBL. 11 REF.Article

CHOLESTEROL HYDROPEROXIDE FORMATION IN RED CELL MEMBRANES AND PHOTOHEMOLYSIS IN ERYTHROPOIETIC PROTOPORPHYRIA = FORMATION D'HYDROPEROXYDE DE CHOLESTEROL DANS LES MEMBRANES D'ERYTHROCYTES ET PHOTOHEMOLYSE DANS LA PROTOPORPHYRIE ERYTHROPOIETIQUELAMOLA AA; YAMANE T; TROZZOLO AM et al.1973; SCIENCE; U.S.A.; DA. 1973; VOL. 179; NO 4078; PP. 1131-1133; BIBL. 20REF.Serial Issue

HEME SYNTHETASE DEFICIENCY IN HUMAN PROTOPORPHYRIA. DEMONSTRATION OF THE DEFECT IN LIVER AND CULTURED SKIN FIBROBLASTS. = DEFICIT EN HEME SYNTHETASE DANS LA PROTOPORPHYRIE HUMAINE. DEMONSTRATION DE L'ANOMALIE AU NIVEAU DU FOIE ET DANS LES FIBROBLASTES CUTANES EN CULTUREBONKOWSKY HL; BLOOMER JR; MAHONEY MJ et al.1975; J. CLIN. INVEST.; U.S.A.; DA. 1975; VOL. 56; NO 5; PP. 1139-1148; BIBL. 42 REF.Article

Genetic heterogeneity in erythropoietic protoporphyria : a study of the enzymatic defect in nine affected familiesNORRIS, P. G; NUNN, A. V; HAWK, J. L. M et al.Journal of investigative dermatology. 1990, Vol 95, Num 3, pp 260-263, issn 0022-202XArticle

Erythropoietic protoporphyria : photodynamic transfer of protoporphyrin from intact erythrocytes to other cellsBRUN, A; WESTERN, A; MALIK, Z et al.Photochemistry and photobiology. 1990, Vol 51, Num 5, pp 573-577, issn 0031-8655Article

DIE ERYTHROPOETISCHE PROTOPORPHYRIE. II. EXPERIMENTELLE UNTERSUCHUNGEN AN MODELLSYSTEMEN: PHOTOSENSIBILITAET UND HAUTVERAENDERUNGEN. = LA PROTOPORPHYRIE ERYTHROPOIETIQUE. II. ETUDES EXPERIMENTALES SUR DES SYSTEMES DE MODELE: PHOTOSENSIBILITE ET MODIFICATIONS CUTANEESHONIGSMANN H.1977; Z. HAUTKRANKH.; DTSCH.; DA. 1977; VOL. 52; NO 10; PP. 541-564Article

SIX CASES OF ERYTHROPOIETIC PROTOPORPHYRIA = SIX CAS DE PROTOPORPHYRIE ERYTHROPOIETIQUENONAKA S; NISHIMOTO K; HIROWATARI T et al.1975; J. DERMATOL.; JAP.; DA. 1975; VOL. 2; NO 2; PP. 79-85; BIBL. 10 REF.Article

SAISONALER PRURITUS ALS SYMPTOM DER ERYTHROPOETISCHEN PROTOPORPHYRINAEMISCHEN LICHTDERMATOSE. (EPL) = PRURIT SAISONNIER, SYMPTOME DE LA DERMATOSE ACTINIQUE ERYTHROPOIETIQUE PROTOPORPHYRINEMIQUEBURG G; PLEWIG G.1972; HAUTARZT; DTSCH.; DA. 1972; VOL. 23; NO 12; PP. 553-55; BIBL. 15REF.Serial Issue

HEPATISCHE REAKTIONEN BEI ERYTHROPOETISCHER PROTOPORPHYRIE = REACTIONS HEPATIQUES AU COURS D'UNE PROTOPORPHYRIE ERYTHROPOIETIQUEKLINGE O; ALEXANDRAKIS E.1981; VIRCHOWS ARCH., B; ISSN 0340-6075; DEU; DA. 1981; VOL. 37; NO 3; PP. 369-379; ABS. ENG; BIBL. 2 P.Article

HEME CONTENT OF NORMAL ANE PORPHYRIC CULTURED SKIN FIBROBLASTS.BRENNER DA; BLOOMER JR.1977; BIOCHEM. GENET.; U.S.A.; DA. 1977; VOL. 15; NO 11-12; PP. 1061-1070; BIBL. 1 P. 1/2Article

ERYTHROPOETISCHE PROTOPORPHYRIE. KLINIK UND THERAPIE. = PROTOPORPHYRIE ERYTHROPOIETIQUE. CLINIQUE ET TRAITEMENTBECKERT E; METZ J.1976; FORTSCHR. D. MED.; DTSCH.; DA. 1976; VOL. 94; NO 34; PP. 1981-1986; ABS. ANGL.; BIBL. 15 REF.Article

LA PROTOPORPHYRIE ERYTHROPOIETIQUEVERITE MOINE GUILLEMETTE.sd; FRA; DA. S.D.; 225; 74-XP.; 30 CM; BIBL. 74 REF.; TH.: MED./PARIS 6/1979Thesis

BOVINE PROTOPORPHYRIA: DOCUMENTATION OF AUTOSOMAL RECESSIVE INHERITANCE AND COMPARISON WITH THE HUMAN DISEASE THROUGH MEASUREMENT OF HEME SYNTHASE ACTIVITYBLOOMER JR; MORTON KO; REUTER RJ et al.1982; AM. J. HUM. GENET.; ISSN 0002-9297; USA; DA. 1982; VOL. 34; NO 2; PP. 322-330; BIBL. 23 REF.Article

ERYTHROPOIETIC PROTOPORPHYRIA: PHOTOACTIVATION OF THE COMPLEMENT SYSTEMGIGLI I; SCHOTHORST AA; SOTER NA et al.1980; J. CLIN. INVEST.; USA; DA. 1980; VOL. 66; NO 3; PP. 517-522; BIBL. 33 REF.Article

HEPATOERYTHROZYTAERE PORPHYRIE = PORPHYRIE HEPATOERYTHROCYTAIREHOENIGSMANN H; REICHEL K.1979; HAUTARZT; DEU; DA. 1979; VOL. 30; NO 2; PP. 95-97; ABS. ENG; BIBL. 7 REF.Article

HEPATIC FAILURE AND DEATH FROM ERYTHROPOIETIC PROTOPORPHYRA.SINGER JA; PLAUT AG; KAPLAN MM et al.1978; GASTROENTEROLOGY; U.S.A.; DA. 1978; VOL. 74; NO 3; PP. 588-591; BIBL. 18 REF.Article

RAPID QUANTITATIVE ASSAY FOR ERYTHROCYTE PORPHYRINS. RAPID QUANTITATIVE MICROFLUOROMETRIC ASSAY APPLICABLE TO THE DIAGNOSIS OF ERYTHROPOIETIC PROTOPORPHYRIA = UNE METHODE DE DOSAGE QUANTITATIVE RAPIDE POUR LES PORPHYRINES ERYTHROCYTAIRES. METHODE DE DOSAGE QUANTITATIVE MICROFLUOROMETRIQUE RAPIDE APPLIQUEE AU DIAGNOSTIC DES PROTOPORPHYRIES ERYTHROPOIETIQUESPOH FITZPATRICK MB; PIOMELLI S; YOUNG P et al.1974; ARCH. DERMATOL.; U.S.A.; DA. 1974; VOL. 110; NO 2; PP. 225-230; BIBL. 13REF.Article

MANIFESTATIONS CLINIQUES ATYPIQUES DE LA PROTOPORPHYRIE ERYTHROPOIETIQUEKRIVOSHEEV BN; NEMCHANINOV VN; ODINTSOVA NG et al.1974; VEST. DERMATOL. VENEROL.; S.S.S.R.; DA. 1974; NO 7; PP. 88-91; ABS. ANGL.; BIBL. 1/2P.Article

Protoporphyrie érythropoïétique = Erythropoietic protoporphyriaDE SELYS, R; DECROIX, J; FRANKART, M et al.Annales de dermatologie et de vénéréologie. 1988, Vol 115, Num 5, pp 555-560, issn 0151-9638Article

CAROTENOID PIGMENTS AND THE TREATMENT OF ERYTHROPOIETIC PROTOPORPHYRIAMATHEWS ROTH MM.1978; J. INFECT. DIS.; USA; DA. 1978; VOL. 138; NO 6; PP. 924-927; BIBL. 15 REF.Article

INHERITANCE IN PROTOPORPHYRIA COMPARISON OF HAEM SYNTHETASE ACTIVITY IN SKIN FIBROBLASTS WITH CLINICAL FEATURES.BLOOMER JR; BONKOWSKY HL; EBERT PS et al.1976; LANCET; G.B.; DA. 1976; NO 7979; PP. 226-228; BIBL. 25 REF.Article

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