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LIPID-PROTEIN-WECHSELWIRKUNGEN. MECHANISMEN DES ENZYMATISCHEN GLYKOLIPID-ABBAUS UND SEINE GENETISCH BEDINGTEN ENTGLEISUNGEN = INTERACTIONS LIPIDES PROTEINES. MECANISMES DE LA DEGRADATION ENZYMATIQUE DES GLYCOLIPIDES ET SES ECARTS DETERMINES GENETIQUEMENTSANDHOFF K.1980; NATURWISSENSCHAFTEN; ISSN 0028-1042; DEU; DA. 1980; VOL. 67; NO 9; PP. 431-441; ABS. ENG; BIBL. 37 REF.Article

HALOTHANE INCREASES MEMBRANE FLUIDITY AND STIMULATES SPHINGOMYELIN DEGRADATION BY MEMBRANE-BOUND NEUTRAL SPHINGOMYELINASE OF SYNAPTOSOMAL PLASMA MEMBRANES FROM CALF BRAIN ALREADY AT CLINICAL CONCENTRATIONSPELLKOFER R; SANDHOFF K.1980; J. NEUROCHEM.; GBR; DA. 1980; VOL. 34; NO 4; PP. 988-992; BIBL. 16 REF.Article

PURIFICATION AND CHARACTERIZATION OF AN ACTIVATOR PROTEIN FOR THE DEGRADATION OF GLYCOLIPIDS GM2 AND GA2 BY HEXOSAMINIDASE ACONZELMANN E; SANDHOFF K.1979; Z. (HOPPE-SEYLER'S) PHYSIOL. CHEM.; DEU; DA. 1979; VOL. 360; NO 12; PP. 1837-1849; ABS. GER; BIBL. 27 REF.Article

BIOCHEMISTRY AND GENETICS OF GANGLIOSIDOSESSANDHOFF K; CHRISTOMANOU H.1979; HUM. GENET.; DEU; DA. 1979; VOL. 50; NO 2; PP. 108-143; BIBL. 13 P.Article

VARIATION OF ARYLSULPHATASE A: COMPARATIVE OF ARYLSULPHATASE A WITH SYNTHETIC AND NATURAL SUBSTRATES IN THREE FAMILIES WITH METACHROMATIC LEUCODYSTROPHYCHRISTOMANOU H; SANDHOFF K.1978; NEUROPAEDIATRIE; DEU; DA. 1978; VOL. 9; NO 4; PP. 385-395; ABS. GER; BIBL. 25 REF.Article

A SENSITIVE FLUORESCENCE ASSAY FOR THE SIMULTANEOUS AND SEPARATE DETERMINATION OF ARYLSULPHATASES A AND B.CHRISTOMANOU H; SANDHOFF K.1977; CLIN. CHIM. ACTA; PAYS-BAS; DA. 1977; VOL. 79; NO 3; PP. 527-531; BIBL. 16 REF.Article

SPHINGOLIPIDSPEICHERKRANKHEITEN ALS BEISPIEL EINER MOLEKULAREN NEUROPATHOLOGIE. = MALADIE DE STOCKAGE DES SPHINGOLIPIDES EN TANT QU'EXEMPLE DE NEUROPATHOLOGIE MOLECULAIREJATZKEWITZ H; SANDHOFF K.1976; ARCH. PSYCHIATR. NERVENKRANKLI.; DTSCH.; DA. 1976; VOL. 221; NO 3; PP. 213-225; ABS. ANGL.; BIBL. 1 P. 1/2Article

MEMBRANE-BOUND NEURAMINIDASE FROM CALF BRAIN: REGULATION OF OLIGOSIALOGANGLIOSIDE DEGRADATION BY MEMBRANE FLUIDITY AND MEMBRANE COMPONENTS.SANDHOFF K; PALLMANN B.1978; PROC. NATION. ACAD. SCI. U.S.A.; U.S.A.; DA. 1978; VOL. 75; NO 1; PP. 122-126; BIBL. 25 REF.Article

PRENATAL DIAGNOSIS OF TAY-SACHS DISEASE IN CELL-FREE AMNIOTIC FLUIDCHRISTOMANOU H; CAP C; SANDHOFF K et al.1978; KLIN. WSCHR.; DEU; DA. 1978; VOL. 56; NO 22; PP. 1133-1135; ABS. GER; BIBL. 9 REF.Article

IMMUNOCHEMICAL AND BIOCHEMICAL INVESTIGATION OF HEXOSAMINIDASE S.GEIGER B; ARNON R; SANDHOFF K et al.1977; AMER. J. HUM. GENET.; U.S.A.; DA. 1977; VOL. 29; NO 5; PP. 508-522; BIBL. 24 REF.Article

Ganglioside metabolism : enzymology, topology, and regulationVAN ECHTEN, G; SANDHOFF, K.The Journal of biological chemistry (Print). 1993, Vol 268, Num 8, pp 5341-5344, issn 0021-9258Article

Metabolism and intracellular transport of glycosphingolipidsSCHWARZMANN, G; SANDHOFF, K.Biochemistry (Easton). 1990, Vol 29, Num 49, pp 10865-10871, issn 0006-2960, 7 p.Article

Evidence for two different active sites on human β-hexosaminidase A: interaction of GM2 activator protein with β-hexosaminidase AKYTZIA, H.-J; SANDHOFF, K.The Journal of biological chemistry (Print). 1985, Vol 260, Num 12, pp 7568-7572, issn 0021-9258Article

Identity of GD1C, GT1a and GQ1b synthase in Golgi vesicles from rat liverIBER, H; SANDHOFF, K.FEBS letters. 1989, Vol 254, Num 1-2, pp 124-128, issn 0014-5793, 5 p.Article

INCORPORATION OF LIPIDS INTO CELLULAR MEMBRANES. A SPIN LABEL ASSAYMARSH D; PELLKOFER R; HOFFMANN BLEIHAUER P et al.1982; ANAL. BIOCHEM.; ISSN 0003-2697; USA; DA. 1982; VOL. 122; NO 1; PP. 206-212; BIBL. 10 REF.Article

MELITTIN STIMULATES INCORPORATION AND DEGRADATION OF SPHINGOMYELIN IN SYNAPTOSOMAL PLASMA MEMBRANESPELLKOFER R; MARSH D; HOFFMANN BLEIHAUER P et al.1982; J. NEUROCHEM.; ISSN 0022-3042; GBR; DA. 1982; VOL. 38; NO 5; PP. 1230-1235; BIBL. 17 REF.Article

PURIFICATION BIOCHEMICAL AND IMMUNOLOGICAL CHARACTERISATION OF HEXOSAMINIDASE A FROM VARIANT AB OF INFANTILE GM2 GANGLIOSIDOSIS.CONZELMANN E; SANDHOFF K; NEHRKORN H et al.1978; EUROP. J. BIOCHEM.; GERM.; DA. 1978; VOL. 84; NO 1; PP. 27-33; BIBL. 27 REF.Article

A RADIOMETRIC ASSAY FOR SIALIDASE ACTING ON GANGLIOSIDE GD1-.SCHRAVEN J; CAP C; NOWOCZEK G et al.1977; ANAL. BIOCHEM.; U.S.A.; DA. 1977; VOL. 78; NO 2; PP. 333-339; BIBL. 22 REF.Article

LYSOSOMAL ENZYME PRECURSORS IN HUMAN FIBROBLASTS. ACTIVATION OF CATHEPSIN D PRECURSOR IN VITRO AND ACTIVITY OF BETA -HEXOSAMINIADASE A PRECURSOR TOWARDS GANGLIOSIDE GM2HASILIK A; VON FIGURA K; CONZELMANN E et al.1982; EUR. J. BIOCHEM.; ISSN 0014-2956; DEU; DA. 1982; VOL. 125; NO 2; PP. 317-321; BIBL. 31 REF.Article

Activator proteins and topology of lysosomal sphingolipid catabolismFÜRST, W; SANDHOFF, K.Biochimica et biophysica acta, L. Lipids and lipid metabolism. 1992, Vol 1126, Num 1, pp 1-16, issn 0005-2760Article

Modulation of ganglioside biosynthesis in primary cultured neuronsVAN ECHTEN, G; SANDHOFF, K.Journal of neurochemistry. 1989, Vol 52, Num 1, pp 207-214, issn 0022-3042Article

Diastereoselektive Synthese von funktionalisierten C-α- und -β-Glycosylderivaten der 2-Acetamido-2-desoxy-D-glucose = Synthèse diastéréosélective de dérivés fonctionnalisés C-α- et -β-glycosyl de l'acétamido-2 désoxy-2 D-glucose = Diastereoselective synthesis of functionalised C-α- and -β-glycosyl derivatives of 2-acetamido-2-deoxy-D-glucoseGIANNIS, A; SANDHOFF, K.Carbohydrate research. 1987, Vol 171, pp 201-210, issn 0008-6215Article

Affinity labelling of the GM2-activator proteinNEUENHOFER, S; SANDHOFF, K.FEBS letters. 1985, Vol 185, Num 1, pp 112-114, issn 0014-5793Article

CONTENT OF GANGLIOSIDES AND PROTEIN-BOUND SIALIC ACID IN POST-MORTEM BRAIN OF PATIENTS WITH MUCOLIPIDOSIS I AND II (ML I AND II)BERRA B; DI PALMA S; LINDI C et al.1979; CELL. MOLEC. BIOL.; GBR; DA. 1979; VOL. 25; NO 4; PP. 281-284; ABS. FRE; BIBL. 19 REF.Article

LiBH4(NaBH4)/Me3SiCl, ein ungewöhnlich starkes und vielseitig einsetzbares Reduktionsmittel = LiBH4(NaBH4)Me3Sill, an unusually strong and versatile reducing agentGIANNIS, A; SANDHOFF, K.Angewandte Chemie. 1989, Vol 101, Num 2, pp 220-222, issn 0044-8249, 3 p.Article

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