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au.\*:("SENGERS RCA")

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EFFECTS OF PARENTERAL NUTRITION WITH LIPIDS ON THE HUMAN LIVER. AN ELECTRON-MICROSCOPIC STUDY.VAN HAELST UJGM; SENGERS RCA.1976; VIRCHOROS ARCH., B; DTSCH.; DA. 1976; VOL. 22; NO 4; PP. 323-332; BIBL. 21 REF.Article

PERCUTANEOUS NEEDLE BIOPSY OF SKELETAL MUSCLE IN CHILDHOODSENGERS RCA; STADHOUDERS AM; NOTERMANS SLH et al.1980; EUR. J. PEDIATR.; ISSN 0340-6199; DEU; DA. 1980; VOL. 135; NO 1; PP. 21-29; BIBL. 15 REF.Article

RECURRENT EXERTIONAL RHABDOMYOLYSIS AND STUNTED GROWTHSENGERS RCA; STADHOUDERS AM; TRIJBELS JMF et al.1978; EUROP. J. PEDIATR.; DEU; DA. 1978; VOL. 129; NO 2; PP. 133-138; BIBL. 19 REF.Article

ORGANIC ACIDURIA IN HYPOXIC PREMATURE NEWBORNS SIMULATING AN INBORN ERROR OF METABOLISMBAKKEREN JAJM; SENGERS RCA; TRIJBELS JMF et al.1977; EUROP. J. PEDIATR.; DEU; DA. 1977; VOL. 127; NO 1; PP. 41-47; BIBL. 10 REF.Article

MEASUREMENT OF CYTOCHROMES IN HUMAN SKELETAL MUSCLE MITOCHONDRIA, ISOLATED FROM FRESH AND FROZEN STORED MUSCLE SPECIMENS.BOOKELMAN H; TRIJBELS JMF; SENGERS RCA et al.1978; BIOCHEM. MED.; USA; DA. 1978; VOL. 19; NO 3; PP. 366-373; BIBL. 16 REF.Article

INFANTILE GAUCHER'S DISEASE: GLUCOCEREBROSIDASE DIFICIENCY IN PERIPHERAL BLOOD LEUKOCYTES AND CULTURED FIBROBLASTS. = LA MALADIE DE GAUCHER INFANTILE: LE DEFICIT EN GLUCOCEREBROSIDASE DANS LES LEUCOCYTES DU SANG PERIPHERIQUE ET LES FIBROBLASTES CULTIVESSENGERS RCA; LAMERS KJB; BAKKEREN JAJ et al.1975; NEUROPAEDIATRIE; DTSCH.; DA. 1975; VOL. 6; NO 4; PP. 377-382; ABS. ALLEM.; BIBL. 11 REF.Article

ESTIMATION OF ENERGY METABOLISM IN HUMAN SKELETAL MUSCLE HOMOGENATE AS A DIAGNOSTIC AIDRUITENBEEK W; SENGERS RCA; TRIJBELS JMF et al.1981; J. INHERIT. METAB. DIS.; ISSN 0141-8955; GBR; DA. 1981; VOL. 4; NO 2; PP. 91-92; BIBL. 2 REF.Article

L-ORNITHINE KETOACID-TRANSAMINASE ASSAY IN HAIR ROOTS OF HOMOZYGOTES AND HETEROZYGOTES FOR GYRATE ATROPHYJANSSEN AJM; PLAKKE T; TRIJBELS FJM et al.1981; CLIN. CHIM. ACTA; ISSN 0009-8981; NLD; DA. 1981; VOL. 113; NO 2; PP. 213-216; BIBL. 10 REF.Article

CARDIOMYOPATHY AND SHORT STATURE ASSOCIATED WITH MITOCHONDRIAL AND/OR LIPID STORAGE MYOPATHY OF SKELETAL MUSCLE.SENGERS RCA; STADHOUDERS AM; JASPAR HHJ et al.1976; NEUROPAEDIATRIE; DTSCH.; DA. 1976; VOL. 7; NO 2; PP. 196-208; BIBL. 2 P.Article

CHRONIC MILD DIARRHOEA, STUNTED GROWTH AND NEUROMUSCULAR ABNORMALITIES.SENGERS RCA; STADHOUDERS AM; JASPAR HHJ et al.1978; EUROP. J. PEDIATR.; DEU; DA. 1978; VOL. 127; NO 3; PP. 211-217; BIBL. 12 REF.Article

RHABDOMYOLYSIS BIJ KINDEREN MET PRIMAIR MYOGENE MYOPATHIEEN = RHABDOMYOLYSE CHEZ DES ENFANTS ATTEINTS DE MYOPATHIES MYOGENES PRIMAIRESHOEVENAARS F; SENGERS RCA; STADHOUDERS AM et al.1978; T. KINDERGENEESKDE; NLD; DA. 1978; VOL. 46; NO 5; PP. 153-160; ABS. ENG; BIBL. 1 P.Article

RECONSTITUTION OF MALATE-ASPARTATE AND ALPHA -GLYCEROPHOSPHATE SHUTTLE ACTIVITY IN RAT SKELETAL MUSCLE MITOCHONDRIABOOKELMAN H; TRIJBELS JMF; SENGERS RCA et al.1979; INTERNATION. J. BIOCHEM.; GBR; DA. 1979; VOL. 10; NO 5; PP. 411-414; BIBL. 17 REF.Article

OCULOCUTANEOUS ALBINISM ASSOCIATED WITH MOTOR NEURON DISEASE.HAMEL BCJ; SENGERS RCA; STADHOUDERS AM et al.1978; HELV. PAEDIATR. ACTA; SUISSE; DA. 1978; VOL. 32; NO 6; PP. 487-493; ABS. ALLEM. FR.; BIBL. 13 REF.Article

PYRUVATE OXIDATION IN RAT AND HUMAN SKELETAL MUSCLE MITOCHONDRIABOOKELMAN H; TRIJBELS JMF; SENGERS RCA et al.1978; BIOCHEM. MED.; USA; DA. 1978; VOL. 20; NO 3; PP. 395-403; BIBL. 29 REF.Article

CONGENITAL CATARACT AND MITOCHONDRIAL MYOPATHY OF SKELETAL AND HEART MUSCLE ASSOCIATED WITH LACTIC ACIDOSIS AFTER EXERCISE = CATARACTE CONGENITALE ET MYOPATHIE MITOCHONDRIALE DES MUSCLES CARDIAQUE ET SQUELETTIQUES AVEC ACIDOSE LACTIQUE A L'EFFORTSENGERS RCA; TER HAAR BGA; TRIJBELS JMF et al.1975; J. PEDIATR.; U.S.A.; DA. 1975; VOL. 86; NO 6; PP. 873-880; BIBL. 13 REF.Article

DYSMYELINATION AND DISTURBED METABOLISM OF PYRUVATE: A CASE REPORTSENGERS RCA; TRIJBELS JMF; BAKKEREN JAJM et al.1983; EUROPEAN JOURNAL OF PEDIATRICS; ISSN 0340-6199; DEU; DA. 1983; VOL. 140; NO 2; PP. 127-130; BIBL. 11 REF.Article

THE EFFECT OF EXOGENOUS CYTOCHROME C ON PYRUVATE OXIDATION BY RAT SKELETAL MUSCLE MITOCHONDRIA ISOLATED IN SUCROSE OR KCL MEDIUMBOOKELMAN H; TRIJBELS JMF; SENGERS RCA et al.1978; BIOCHEM. MED.; USA; DA. 1978; VOL. 20; NO 3; PP. 404-416; BIBL. 24 REF.Article

A PATIENT WITH NONKETOTIC HYPERGLYCINEMIA: BIOCHEMICAL FINDINGS AND THERAPEUTIC APPROACHES = SIGNES BIOCHIMIQUES ET APPROCHES THERAPEUTIQUES CHEZ UN MALADE ATTEINT D'HYPERGLYCINEMIE NON CETOSIQUETRIJBELS JMF; MONNENS LAH; VAN DER ZEE SPM et al.1974; PEDIATR. RES.; U.S.A.; DA. 1974; VOL. 8; NO 5; PP. 598-605; BIBL. 26 REF.Article

MUSCLE PHOSPHORYLASE DEFICIENCY IN CHILDHOODSENGERS RCA; STADHOUDERS AM; JASPAR HHJ et al.1980; EUROP. J. PEDIATR.; DEU; DA. 1980; VOL. 134; NO 2; PP. 161-165; BIBL. 12 REF.Article

CONGENITAL CATARACT AND MITOCHONDRIAL MYOPATHY OF SKELETAL AND HEART MUSCLE ASSOCIATED WITH LACTIC ACIDOSIS AFTER EXERCISE = CATARACTE CONGENITALE ET MYOPATHIE MITOCHONDRIALE DES MUSCLES CARDIAQUE ET SQUELETTIQUES AVEC ACIDOSE LACTIQUE A L'EFFORTSENGERS RCA; TER HAAR BGA; TRIJBELS JMF et al.1975; J. PEDIATR.; U.S.A.; DA. 1975; VOL. 86; NO 6; PP. 873-880; BIBL. 13 REF.Article

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