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TRANSAMINATIONS BETWEEN AMINO ACIDS AND KETO ACIDS ELEVATED IN PHENYLKETONURIA AND MAPLE SYRUP URINE DISEASE = TRANSAMINATIONS ENTRE LES ACIDES AMINES ET LES ACIDES CETONIQUES AUGMENTES DANS LA PHENYLCETONURIE ET LA MALADIE DU SIROP D'ERABLELEES GJ; WEINER N.1973; J. NEUROCHEM.; G.B.; DA. 1973; VOL. 20; NO 2; PP. 389-403; BIBL. 1P.Serial Issue

THE GAS-CHROMATOGRAPHIC DIAGNOSIS INTERMITTENT MAPLE SYRUP URINE DISEASE (BRANCH-CHAIN KETOACIDURIA) = DIAGNOSTIC PAR CHROMATOGRAPHIE EN PHASE GAZEUSE DE LA LEUCINOSE INTERMITTENTE (CETO-ACIDURIE A CHAINE RAMIFIEEGOMPERTZ D; DRAFFAN GH.1972; CLIN. CHIM. ACTA; PAYS-BAS; DA. 1972; VOL. 40; NO 1; PP. 5-11; BIBL. 15REF.Serial Issue

HISTORICAL OBSERVATION IN MAPLE SYRUP URINE DISEASE = OBSERVATION HISTORIQUE SUR LA MALADIE DU SIROP D'ERABLESHIH VE; MANDELL R; SCHOLL M et al.1974; J. PEDIATR.; U.S.A.; DA. 1974; VOL. 85; NO 6; PP. 868-869; BIBL. 6REF.Article

Reverse osmosis in the production of maple syrup = L'osmose inverse en production de sirop d'érableSENDAK, P. E; MORSELLI, M. F.Forest products journal. 1984, Vol 34, Num 7-8, pp 57-61, issn 0015-7473Article

ISOLEUCINE TRANSPORT BY CULTURED HUMAN FIBROBLASTS. II. SELECTION OF A CELL LINE WITH REDUCED ISOLEUCINE UPTAKEHILLMAN RE; OTTO EF.1974; BIOCHIM. BIOPHYS. ACTA; PAYS-BAS; DA. 1974; VOL. 367; NO 1; PP. 81-97; BIBL. 9REF.Article

ENZYME ACTIVITY IN CLASSICAL AND VARIANT FORMS OF MAPLE SYRUP WINE DISEASE = ACTIVITE ENZYMATIQUE DANS LES FORMES CLASSIQUES ET LES VARIANTES DE LA MALADIE DU SIROP D'ERABLEDANCIS J; HUTZLER J; SNYDERMAN SE et al.1972; J. PEDIATR.; U.S.A.; DA. 1972; VOL. 81; NO 2; PP. 312-320; BIBL. 22REF.Serial Issue

EFFECT OF OXYGEN, CARBON DIOXIDE, AND NITROGEN ON MAPLE SYRUP STORED IN PLASTIC JUGSSENDAK PE.1982; JOURNAL OF FOOD SCIENCE; ISSN 0022-1147; USA; DA. 1982; VOL. 47; NO 5; PP. 1741-1742; BIBL. 8 REF.Article

MAPLE SYRUP URINE DISEASE: REPORT OF A CASEPURSHOWTHAM RAO G; RAMANAMURTHY PSV; GHAFOORUNNISA et al.1974; INDIAN PEDIATR.; INDIA; DA. 1974; VOL. 11; NO 8; PP. 585-587; BIBL. 12REF.Article

MAPLE SYRUP URINE DISEASE: A CASE REPORT = MALADIE DU SIROP D'ERABLE: OBSERVATION D'UN CASVINODINI REDDY; REDDY YR; NARSINGA RAO BS et al.1972; INDIAN PEDIATR.; INDIA; DA. 1972; VOL. 9; NO 10; PP. 629-633; BIBL. 12REF.Serial Issue

SYNTHETIC ROUTES TO 2-HYDROXY-3-METHYLCYCLOPENT-2-EN-1-ONE AND RELATED CYCLOPENTANE-1,2-DIONES. A REVIEW. = VOIES DE SYNTHESE DE HYDROXY-2-METHYLCYCLO-3-PENTENE-2-ONE-1 ET DES CYCLOPENTANE DIONES-1,2 APPARENTEES : REVUESTRUNZ GM.1983; JOURNAL OF AGRICULTURAL AND FOOD CHEMISTRY; ISSN 0021-8561; USA; DA. 1983; VOL. 31; NO 2; PP. 185-190; BIBL. 46 REF.; 2 FIG./4 TABL.Article

MULTIPLE EXCHANGE TRANSFUSIONS AS TREATMENT DURING THE ACUTE PEROID IN MAPLE SYRUP URINE DISEASE = LES EXSANGUINO-TRANSFUSIONS MULTIPLES COMME TRAITEMENT DURANT LA PERIODE AIGUE DE LA MALADIE AVEC URINE A ODEUR DE SIROP D'ERABLESCHUCHMANN L; WITT I; SCHULZ P et al.1972; HELV. PAEDIATR. ACTA; SUISSE; DA. 1972; VOL. 27; NO 4; PP. 449-456; ABS. ALLEM.; BIBL. 15 REF.Serial Issue

DER STAND DES NEUGEBORENEN-SCREENING IN DER SCHWEIZ = L'ETAT DU DEPISTAGE CHEZ LES NOUVEAU-NES EN SUISSEGITZELMANN R.1972; BULL. ACAD. SUISSE SCI. MED.; SUISSE; DA. 1972; VOL. 28; NO 5-6; PP. 294-301; ABS. FR. ITAL. ANGL.; BIBL. 1P.Serial Issue

UN CASO DI MALATTIA CON URINE A SEIROPPO D'ACERO. STUDIO BIOCHIMICO = UN CAS DE MALADIE AVEC LES URINES SIROP D'ERABLE. ETUDE BIOCHIMIQUELAMEDICA GM; FREGONESE B; MORONI G et al.1972; MINERVA PEDIATR.; ITAL.; DA. 1972; VOL. 24; NO 43; PP. 2143-2149; ABS. ANGL.; BIBL. 32 REF.Serial Issue

DIAGNOSTIC PRECOCE DE LA PHENYLCETONURIE, DE L'HOMOCYSTINURIE ET DE LA MALADIE DU SIROP D'ERABLE A L'AIDE DU TEST D'INHIBITION MICROBIENNE DE GUTHRIEMAKHILL G; KNAPP A.1974; PEDIATRIJA; S.S.S.R.; DA. 1974; NO 12; PP. 27-30; ABS. ANGL.; BIBL. 1/2 P.Article

TREATMENT OF BRANCHED CHAIN KETOACIDURIA (BCKA) DURING ACUTE ILLNESS. APPROACHES TO THE CORRECTION OF THE ACIDOSIS = TRAITEMENT DE LA CETO-ACIDURIE A CHAINE BRANCHEE (BCKA) AU COURS DES MALADIES AIGUES. APPROCHES POUR LA CORRECTION DE L'ACIDOSE1972; CLIN. PEDIATR.; U.S.A.; DA. 1972; VOL. 11; NO 6; PP. 360-363; BIBL. 9 REF.Serial Issue

ETUDES BIOCHIMIQUES DU SYNDROME DE CETOAMINOACIDURIELYSIAK W.1972; SOC. SCI. GEDAN., ACTA BIOL. MED.; POLOGNE; DA. 1972; VOL. 17; NO 1; PP. 7-23; ABS. ANGL.; BIBL. 1 P.Serial Issue

LEUCINOSE AIGUE NEONATALEBERTHELOT J; LARGET PIET L; WILLIAMSON C et al.1975; NOUV. PRESSE MED.; FR.; DA. 1975; VOL. 4; NO 9; PP. 666Article

INHIBITION OF PYRUVATE AND BETA -HYDROXY BUTYRATE OXIDATION IN RAT BRAIN MITOCHONDRIA BY PHENYLPYRUVATE AND ALPHA -KETOISOCAPROATELAND JM; CLARK JB.1974; F.E.B.S. LETTERS; NETHERL.; DA. 1974; VOL. 44; NO 3; PP. 348-351; BIBL. 15REF.Article

METABOLIC DISEASES AND MENTAL RETARDATION. I. THE CHICK EMBRYO AS A MODEL SYSTEM IN BRANCHED-CHAIN KETOACIDURIA; THE EFFECT OF ALPHA -KETOISOCAPROIC ACID = MALADIES METABOLIQUES ET RETARD MENTAL. I. L'EMBRYON DE POULET COMME SYSTEME MODELE DANS LA CETOACIDURIE A CHAINE LATERALE; L'EFFET DE L'ACIDE ALPHA -CETOISOCAPROIQUEBOWDEN JA; MCARTHUR CL III; FRIED M et al.1974; INTERNATION. J. BIOCHEM.; G.B.; DA. 1974; VOL. 5; NO 4; PP. 391-396; BIBL. 15REF.Article

CLASSICAL MAPLE SYRUP URINE DISEASE: COFACTOR RESISTANCE = MALADIE DU SIROP D'ERABLE: UNE RESISTANCE AU COFACTEURELSAS LJ; PASK BA; WHEELER FB et al.1972; METABOLISM; U.S.A.; DA. 1972; VOL. 21; NO 10; PP. 929-944; BIBL. 1P.1/2Serial Issue

ATTEMPTED DETECTION OF HETEROZYGOTES FOR MAPLE-SYRUP-URINE DISEASE = ESSAI DE DETECTION DES HETEROZYGOTES POUR LA MALADIE DU SIROP D'ERABLEMCKNIGHT MT; SPENCE MW.1972; CLIN. GENET.; DANM.; DA. 1972; VOL. 3; NO 6; PP. 458-464; BIBL. 14REF.Serial Issue

Un sirop au goût amer : le sirop d'érable québécois, produit industriel standardisé ou produit du terroir ?MORINIAUX, V.Bulletin de l'Association de géographes français. 2007, Vol 84, Num 1, pp 81-96, issn 0004-5322, 16 p.Article

Characteristics of maple syrup processed from bleach-treated sap = Caractéristiques du sirop d'érable fabriqué à partir de sève traitée par un désinfectantMORSELLI, M. F; WHALLEN, M. L; BAGGETT, K. L et al.Journal of food protection. 1985, Vol 48, Num 3, pp 204-206, issn 0362-028XArticle

Fungi associated with pure maple syrup packed at the minimum recommended reheating temperature = Moisissures associées au sirop pur d'érable conditionné à la température minimale de réchauffement recommandéeWHALEN, M. L; MORSELLI, M. F.Journal of food protection. 1984, Vol 47, Num 9, pp 688-689, issn 0362-028XArticle

Characterization of polysaccharides isolated from maple syrup = Caractérisation des polysaccharides isolés du sirop d'érableSTORZ, G; DARVILL, A. G; ALBERSHEIM, P et al.Phytochemistry. 1986, Vol 25, Num 2, pp 437-441, issn 0031-9422Article

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