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HUMAN BETA -GLUCURONIDASE PINOCYTOSIS AND BINDING TO THE IMMOBILIZED PHOSPHOMANNOSYL RECEPTOR: EFFECTS OF TREATMENT OF THE ENZYME WITH ALPHA -N-ACETYLGLUCOSAMINYL PHOSPHODIESTERASEVENUGOPAL TALKAD; SLY WS.1983; JOURNAL OF BIOLOGICAL CHEMISTRY; ISSN 0021-9258; USA; DA. 1983; VOL. 258; NO 12; PP. 7345-7351; BIBL. 32 REF.Article

INTERMEDIATE GOLGI ALPHA -D-MANNOSIDOSE ACTIVITY IN FIBROBLASTS FROM PATIENTS WITH MANNOSIDOSIS AND MUCOLIPIDOSIS II AND IIANDRIA G; SLY WS.1981; PEDIATR. RES.; ISSN 0031-3998; USA; DA. 1981; VOL. 15; NO 1; PP. 70-73; BIBL. 39 REF.Article

THE ROLE OF INTERMEDIATE VESICLES IN THE ADSORPTIVE ENDOCYTOSIS AND TRANSPORT OF LIGAND TO LYSOSOMES BY HUMAN FIBROBLASTSMERION M; SLY WS.1983; JOURNAL OF CELL BIOLOGY; ISSN 0021-9525; USA; DA. 1983; VOL. 96; NO 3; PP. 644-650; BIBL. 24 REF.Article

GENETIC HETEROGENEITY IN MULTIPLE LYSOSOMAL HYDROLASE DEFICIENCY = HETEROGENEITE GENETIQUE DES DEFICITS MULTIPLES EN HYDROLASES LYSOSOMIQUESGLASER JH; MCALISTER WH; SLY WS et al.1974; J. PEDIATR.; U.S.A.; DA. 1974; VOL. 85; NO 2; PP. 192-198; BIBL. 26REF.Article

BETA -GLUCURONIDASE BINDING TO HUMAN FIBROBLAST MEMBRANE RECEPTORSFISCHER HD; GONZALEZ NORIEGA A; SLY WS et al.1980; J. BIOL. CHEM.; USA; DA. 1980; VOL. 255; NO 11; PP. 5069-5074; BIBL. 24 REF.Article

CORRELATION OF STRUCTURAL FEATURES OF PHOSPHOMANNANS WITH THEIR ABILITY TO INHIBIT PINOCYTOSIS OF HUMAN BETA -GLUCURONIDASE BY HUMAN FIBROBLASTS.KAPLAN A; FISCHER D; SLY WS et al.1978; J. BIOL. CHEM.; U.S.A.; DA. 1978; VOL. 253; NO 3; PP. 647-650; BIBL. 18 REF.Article

BETA -GLUCURONIDASE DEFICIENCY MUCOPOLYSACCHARIDOSIS. REPOSITORY IDENTIFICATION NO. GM-121SLY WS; GREENE AE; CORIELL LL et al.1975; CYTOGENET. CELL GENET.; SWITZ.; DA. 1975; VOL. 15; NO 6; PP. 410-412; BIBL. 10 REF.Article

THE REGULATION OF FATTY ACID BIOSYNTHESIS IN HUMAN SKIN FIBROBLASTSJACOBS RA; SLY WS; MAJERUS PW et al.1973; J. BIOL. CHEM.; U.S.A.; DA. 1973; VOL. 248; NO 4; PP. 1268-1276; BIBL. 42REF.Serial Issue

MICROCEPHALY, MILD MENTAL RETARDATION SHORT STATURE, AND SKELETAL ANOMALIES IN SIBLINGS = MICROCEPHALIE, RETARD MENTAL MODERE, PETITE TAILLE ET ANOMALIES SQUELETTIQUES DANS UNE FRATRIEZACKAI EH; SLY WS; MCALISTER WH et al.1972; AMER. J. DIS. CHILD.; U.S.A.; DA. 1972; VOL. 124; NO 1; PP. 111-115; BIBL. 16 REF.Serial Issue

BINDING OF PHOSPHORYLATED OLIGOSACCHARIDES TO IMMOBILIZED PHOSPHOMANNOSYL RECEPTORSFISCHER HD; CREEK KE; SLY WS et al.1982; JOURNAL OF BIOLOGICAL CHEMISTRY; ISSN 0021-9258; USA; DA. 1982; VOL. 257; NO 17; PP. 9938-9943; BIBL. 41 REF.Article

HUMAN BETA -GLUCURONIDASE. I. RECOGNITION AND UPTAKE BY ANIMAL FIBROBLASTS SUGGESTS ANIMAL MODELS FOR ENZYME REPLACEMENT STUDIES.FRANKEL HA; GLASER JH; SLY WS et al.1977; PEDIATR. RES.; U.S.A.; DA. 1977; VOL. 11; NO 7; PP. 811-816; BIBL. 23 REF.Article

HUMAN BETA -GLUCURONIDASE: IN VIVO CLEARANCE AND IN VITRO UPTAKE BY A GLYCOPROTEIN RECOGNITION SYSTEM ON RETICULOENDOTHELIAL CELLSACHORD DT; BROT FF; BELL CE et al.1978; CELL; USA; DA. 1978; VOL. 15; NO 1; PP. 269-278; BIBL. 1 P.Article

KETOTIC HYPOGLYCEMIA IN THE PENTA X AND OTHER CHROMOSOME NONS IMBALANCE SYNDROMESSRI MOEDJONO; SLY WS; MAULDIN LB et al.1978; CLIN. GENET.; DNK; DA. 1978; VOL. 14; NO 16; PP. 367-369; BIBL. 6 REF.Article

CHLOROQUINE INHIBITS LYSOSOMAL ENZYME PINOCYTOSIS AND ENHANCES LYSOSOMAL ENZYME SECRETION BY IMPAIRING RECEPTOR RECYCLINGGONZALES NORIEGA A; GRUBB JH; TALKAD V et al.1980; J. CELL BIOL.; USA; DA. 1980; VOL. 85; NO 3; PP. 839-852; BIBL. 34 REF.Article

PHOSPHOMANNOSYL-ENZYME RECEPTORS IN RAT LIVER: SUBCELLULAR DISTRIBUTION AND ROLE IN INTRACELLULAR TRANSPORT OF LYSOSOMAL ENZYMESFISCHER HD; GONZALEZ NORIEGA A; SLY WS et al.1980; J. BIOL. CHEM.; ISSN 0021-9258; USA; DA. 1980; VOL. 255; NO 20; PP. 9608-9615; BIBL. 32 REF.Article

ENZYMATIC IDENTIFICATION OF MANNOSE 6-PHOSPHATE ON THE RECOGNITION MARKER FOR RECEPTOR-MEDIATED PINOCYTOSIS OF BETA -GLUCURONIDASE BY HUMAN FIBROBLASTSNATOWICZ MR; CHI MMY; LOWRY OH et al.1979; PROC. NATION. ACAD. SCI. U.S.A.; USA; DA. 1979; VOL. 76; NO 9; PP. 4322-4326; BIBL. 35 REF.Article

MULTIPLE ISOELECTRIC AND RECOGNITION FORMS OF HUMAN BETA -GLUCURONIDASE ACTIVITYGLASER JH; ROOZEN KJ; BROT FE et al.1975; ARCH. BIOCHEM. BIOPHYS.; U.S.A.; DA. 1975; VOL. 166; NO 2; PP. 536-542; BIBL. 16REFArticle

OSTEOPETROSIS, RENAL TUBULAR ACIDOSIS AND BASAL GANGLIA CALCIFICATION IN THREE SISTERSWHYTE MP; MURPHY WA; FALLON MD et al.1980; AMER. J. MED.; USA; DA. 1980; VOL. 69; NO 1; PP. 64-74; BIBL. 41 REF.Article

PERMANENT LYMPHOID LINES FROM GENETICALLY MARKED LYMPHOCYTES: SUCCESS WITH LYMPHOCYTES RECOVERED FROM FROZEN STORAGESLY WS; GURBAX SINGH SEKHON; KENNETT R et al.1976; TISSUE ANTIGENS; DENM.; DA. 1976; VOL. 7; NO 3; PP. 165-172; BIBL. 1 P.Article

MUCOLIPIDOSIS III (PSEUDO-HURLER POLYDYSTROSPHY). CLINICAL AND LABORATORY STUDIES IN A SERIES OF 12 PATIENTS. = MUCOLIPIDOSE III (PSEUDO-POLYDYSTROPHIE DE HURLER). ETUDES CLINIQUE ET BIOLOGIQUE DANS UN GROUPE DE 12 MALADESKELLY TE; THOMAS GH; TAYLOR HA JR et al.1975; JOHNS HOPKINS MED. J.; U.S.A.; DA. 1975; VOL. 137; NO 4; PP. 156-175; BIBL. 1 P.Article

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