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FORMATION OF MONOENOIC FATTY ACIDS BY DESATURATION IN RAT BRAIN HOMOGENATE. SOME PROPERTIES OF THE ENZYME SYSTEM OF 10-DAY-OLD BRAIN = FORMATION D'ACIDES GRAS MONOENOIQUES PAR DESATURATION DANS L'HOMOGENEISAT DE CERVEAU DE RAT. QUELQUES PROPRIETES DU SYSTEME ENZYMATIQUE DU CERVEAU AGE DE 10 JOURSCOOK HW; SPENCE MW.1973; J. BIOL. CHEM.; U.S.A.; DA. 1973; VOL. 248; NO 5; PP. 1786-1792; BIBL. 40 REF.Serial Issue

NEUTRAL AND ACID SPHINGOMYELINASES OF RAT BRAIN: SOMATOTOPOGRAPHICAL DISTRIBUTION AND ACTIVITY FOLLOWING EXPERIMENTAL MANIPULATION OF THE DOPAMINERGIC SYSTEM IN VIVOSPERKER ER; SPENCE MW.1983; JOURNAL OF NEUROCHEMISTRY; ISSN 0022-3042; GBR; DA. 1983; VOL. 40; NO 4; PP. 1182-1184; BIBL. 15 REF.Article

ACID: COENZYME A LIGASE IN BRAIN: FATTY ACID SPECIFICITY IN CELLULAR AND SUBCELLULAR FRACTIONSMURPHY MG; SPENCE MW.1982; J. NEUROCHEM.; ISSN 0022-3042; GBR; DA. 1982; VOL. 38; NO 3; PP. 675-679; BIBL. 26 REF.Article

SPHINGOMYELINASE ACTIVITY AT PH 7.4 IN HUMAN BRAIN AND A COMPARISON TO ACTIVITY AT PH 5.0.RAO BG; SPENCE MW.1976; J. LIPID RES.; U.S.A.; DA. 1976; VOL. 17; NO 5; PP. 506-515; BIBL. 30 REF.Article

EFFECT OF FATHY-ACID DOUBLE-BOND POSITION ON THE SELECTIVITY OF RAT-BRAIN ENZYMES: THE INCORPORATION OF OLEIC AND CIS-VACCINIC ACIDS INTO LYSOLECITHIN IN VITRO.MURPHY MG; SPENCE MW.1977; J. NEUROCHEM.; G.B.; DA. 1977; VOL. 29; NO 2; PP. 251-259; BIBL. 42 REF.Article

NIEMANN-PICK DISEASE TYPE D: LIPID ANALYSES AND STUDIES ON SPHINGOMYELINASES.RAO BG; SPENCE MW.1977; ANN. NEUROL.; U.S.A.; DA. 1977; VOL. 1; NO 4; PP. 385-392; BIBL. 1 P.Article

INBORN ERRORS OF METABOLISM IN THE MARITIMES, WITH SPECIAL REFERENCE TO MAPLE-SYRUP-URINE DISEASE AND FABRY'S DISEASE.SPENCE MW; DEWOLFE MS.1976; CLIN. BIOCHEM.; CANADA; DA. 1976; VOL. 9; NO 3; PP. 173-177; BIBL. 21 REF.Article

ATTEMPTED DETECTION OF HETEROZYGOTES FOR MAPLE-SYRUP-URINE DISEASE = ESSAI DE DETECTION DES HETEROZYGOTES POUR LA MALADIE DU SIROP D'ERABLEMCKNIGHT MT; SPENCE MW.1972; CLIN. GENET.; DANM.; DA. 1972; VOL. 3; NO 6; PP. 458-464; BIBL. 14REF.Serial Issue

INABILITY OF RABBIT PERITONEAL POLYMORPHONUCLEAR LEUKOCYTES TO SYNTHESIZE ARACHIDONIC ACID FROM LINOLEIC ACIDCOOK HW; CLARKE JTR; SPENCE MW et al.1983; PROSTAGLANDINS, LEUKOTRIENES AND MEDICINE; ISSN 0262-1746; GBR; DA. 1983; VOL. 10; NO I; PP. 39-52; BIBL. 3 P.Article

CONCERTED STIMULATION AND INHIBITION OF DESATURATION, CHAIN ELONGATION, AND ESTERIFICATION OF ESSENTIAL FATTY ACIDS BY CULTURED NEUROBLASTOMA CELLSCOOK HW; CLARKE JTR; SPENCE MW et al.1983; JOURNAL OF BIOLOGICAL CHEMISTRY; ISSN 0021-9258; USA; DA. 1983; VOL. 258; NO 12; PP. 7586-7591; BIBL. 21 REF.Article

A NEW VARIANT OF SANDHOFF'S DISEASE = UNE NOUVELLE VARIANTE DE LA MALADIE DE SANDHOFFSPENCE MW; RIPLEY BA; EMBIL JA et al.1974; PEDIATR. RES.; U.S.A.; DA. 1974; VOL. 8; NO 6; PP. 628-637; BIBL. 1P.1/2Article

STUDIES ON THE TURNOVER OF ENDOGENOUS CHOLINE-CONTAINING PHOSPHOLIPIDS OF CULTURED NEUROBLASTOMA CELLSD'SOUZA CJM; CLARKE JTR; COOK HW et al.1983; BIOCHIMICA ET BIOPHYSICA ACTA; ISSN 0006-3002; NLD; DA. 1983; VOL. 752; NO 3; PP. 467-473; BIBL. 13 REF.Article

ANGIOKERATOMA CORPORIS DIFFUSUM (ANDERSON-FABRY DISEASE) IN A SINGLE LARGE FAMILY IN NOVA SCOTIASPENCE MW; CLARKE JTR; D'ENTREMONT DM et al.1978; J. MED. GENET.; GBR; DA. 1978; VOL. 15; NO 6; PP. 428-434; BIBL. 19 REF.Article

FAILURE TO CORRECT THE METABOLIC DEFECT BY RENAL ALLOTRANSPLANTATION IN FABRY'S DISEASE = ECHEC DANS LA CORRECTION DU TROUBLE METABOLIQUE PAR ALLOTRANSPLANTATION RENALE DANS LA MALADIE DE FABRYSPENCE MW; MACKINNON KE; BURGESS JK et al.1976; ANN. INTERN. MED.; U.S.A.; DA. 1976; VOL. 84; NO 1; PP. 13-16; BIBL. 23 REF.Article

HETEROZYGOTE DETECTION IN ANGIOKERATOMA CORPORIS DIFFUSUM (ANDERSON-FABRY DISEASE). STUDIES ON PLASMA, LEUCOCYTES, AND HAIR FOLLICLES.SPENCE MW; GOLDBLOOM AL; BURGESS JK et al.1977; J. MED. GENET.; G.B.; DA. 1977; VOL. 14; NO 2; PP. 91-99; BIBL. 1 P.Article

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