Pascal and Francis Bibliographic Databases

Help

Search results

Your search

kw.\*:("SPHINGOLIPIDOSE HEREDITAIRE KUFS")

Publication Year[py]

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Discipline (document) [di]

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Language

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Author Country

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Results 1 to 20 of 20

  • Page / 1
Export

Selection :

  • and

PEROXIDASE ACTIVITY IN THE PAROTID GLAND IN JUVENILE NEURONAL CEROID-LIPOFUSCINOSIS.PILZ H; GOEBEL HH.1977; NEUROBIOL. APPL. NEUROBIOL.; G.B.; DA. 1977; VOL. 3; NO 2; PP. 93-101; BIBL. 15 REF.Article

AN ADULT CASE OF CANINE NEURONAL CEROID-LIPOFUSCINOSIS.CUMMINGS JF; DE LAHUNTA A.1977; ACTA NEUROPATHOL.; ALLEM.; DA. 1977; VOL. 39; NO 1; PP. 43-51; BIBL. 24 REF.Article

MUSKELBIOPSIE. = BIOPSIE MUSCULAIREGOEBEL HH; SCHAAKE T.1977; MUENCH. MED. WSCHR.; DTSCH.; DA. 1977; VOL. 119; NO 27; PP. 923-925; ABS. ANGL.; BIBL. 13 REF.Article

CEROIDE-LIPOFUSCINOSE ATYPIQUE DE L'ADULTE OU DEGENERESCENCE SPINO-CEREBELLEUSE AVEC INCLUSIONS INTRACYTOPLASMIQUES.RUMBACH L; COQUILLAT G; SIMONY N et al.1981; REV. OTO-NEURO-OPHTALMOL.; ISSN 0035-2497; FRA; DA. 1981; VOL. 53; NO 2; PP. 111-120; ABS. ENG; BIBL. 33 REF.Article

AUTOFLUORESCENCE EMISSION SPECTRA OF NEURONAL LIPOPIGMENT IN A CASE OF ADULT ONSET CEROIDOSIS (KUFS' DISEASE)DOWSON JH.1983; ACTA NEUROPATHOLOGICA; ISSN 0001-6322; DEU; DA. 1983; VOL. 59; NO 4; PP. 241-245; BIBL. 21 REF.Article

A GOLGI AND ULTRASTRUCTURAL STUDY OF A DOMINANT FORM OF KUFS' DISEASEFERRER I; ARBIZU T; PENA J et al.1980; J. NEUROL.; DEU; DA. 1980; VOL. 222; NO 3; PP. 183-190; ABS. GER; BIBL. 24 REF.Article

PIGMENT VARIANT OF NEURONAL CEROID-LIPOFUSCINOSIS (KUFS'DISEASE).HOROUPIAN DS; ROSS RT.1977; CANAD. J. NEUROL. SCI.; CANADA; DA. 1977; VOL. 4; NO 1; PP. 67-75; ABS. FR.; BIBL. 20 REF.Article

HUMAN LEUKOCYTE PEROXIDASE: ACTIVITY OF A SOLUBLE AND MEMBRANE BOUND ENZYME FORM IN NORMAL PERSONS AND PATIENTS WITH NEURONAL CEROID-LIPOFUSCINOSIS.PILZ H; O'BRIEN JS; HEIPERTZ R et al.1976; METABOLISM; U.S.A.; DA. 1976; VOL. 25; NO 5; PP. 561-570; BIBL. 1 P. 1/2Article

THE INVESTIGATION OF DEMENTIA: RESULTS IN 200 CONSECUTIVE ADMISSIONSSMITH JS; KILOH LG.1981; LANCET (BR. ED.); ISSN 0140-6736; GBR; DA. 1981; NO 8224; PP. 824-827; BIBL. 9 REF.Article

PARITAL PEROXIDASE DEFICIENCY IN NEUTROPHILS AND EOSINOPHILS ASSOCIATED WITH NEUROLOGIC DISEASE. HISTOCHEMICAL, CYTOCHEMICAL AND BIOCHEMICAL STUDIESBOZDECH MJ; BAINTON DF; MUSTACCHI P et al.1980; AMER. J. CLIN. PATHOL.; USA; DA. 1980; VOL. 73; NO 3; PP. 409-416; BIBL. 22 REF.Article

SO-CALLED NEURONAL CEROID-LIPOFUSCINOSIS. HISTOCHEMICAL STUDY WITH EVIDENCE OF EXTRATIBILITY OF THE STORED MATERIAL.ELLEDER M.1977; ACTA NEUROPATHOL.; ALLEM.; DA. 1977; VOL. 38; NO 2; PP. 117-122; BIBL. 38 REF.Article

THE ULTRASTRUCTURAL CHARACTERISTICS OF THE ABNORMAL CYTOSOMES IN BATTEN-KUF'S DISEASE.CARPENTER S; KARPATI G; ANDERMANN F et al.1977; BRAIN; G.B.; DA. 1977; VOL. 100; NO 1; PP. 137-156; BIBL. 3 P.Article

ISOELECTRIC ENZYME PATTERNS OF LEUKOCYTE PEROXIDASE IN NORMAL CONTROLS AND PATIENTS WITH NEURONAL CEROID-LIPOFUSCINOSES.PILZ H; GOEBEL HH; O'BRIEN JS et al.1976; NEUROPAEDIATRIE; DTSCH.; DA. 1976; VOL. 7; NO 3; PP. 261-270; ABS. ALLEM.; BIBL. 21 REF.Article

Kuft's disease presenting as progressive dementia with late-onset generalized seizures : a clinicopathological and electrophysiologycal studyDONNET, A; HABIB, M; PELLISSIER, J. F et al.Epilepsia (Copenhagen). 1992, Vol 33, Num 1, pp 65-74, issn 0013-9580Article

Maladie de Kufs avec leucoencéphalopathie = Kufs disease presenting as a leukoencephalopathyGILLE, M; BRUCHER, J.-M; INDEKEU, P et al.Revue neurologique (Paris). 1995, Vol 151, Num 6-7, pp 392-397, issn 0035-3787Article

Kufs' disease presenting as late-onset epilepsia partialis continuaGAMBARDELLA, A; PASQUINELLI, G; CITTADELLA, R et al.Neurology. 1998, Vol 51, Num 4, pp 1180-1182, issn 0028-3878Article

Adult neuronal ceroid lipofuscinosis presenting with psychiatric symptoms: a case reportAUGUSTINE, A; FRICCHIONE, G; WOZNICKI, R et al.International journal of psychiatry in medicine. 1993, Vol 23, Num 4, pp 315-322, issn 0091-2174Article

Neuroleptic malignant syndrome in Kufs' diseaseREIF, A; SCHNEIDER, M. F; HOYER, A et al.Journal of neurology, neurosurgery and psychiatry. 2003, Vol 74, Num 3, pp 385-387, issn 0022-3050, 3 p.Article

Alz-50, ubiquitin and Tau immunoreactivity of neurofibrillary tangles, Pick bodies and Lewy bodiesLOVE, S; SAITOH, T; QUIJADA, S et al.Journal of neuropathology and experimental neurology. 1988, Vol 47, Num 4, pp 393-405, issn 0022-3069Article

A family with adult type ceroid lipofuscinosis (Kufs' disease) and heart muscle disease : Report of two autopsy casesSAKAJIRI, K.-I; MATSUBARA, N; NAKAJIMA, T et al.Internal medicine (Tokyo. 1992). 1995, Vol 34, Num 12, pp 1158-1163, issn 0918-2918Article

  • Page / 1