HPLC URINARY ORGANIC ACID PROFILING: ROLE OF THE ULTRAVIOLET AND AMPEROMETRIC DETECTORSBUCHANAN DN; THOENE JG.1981; J. LIQ. CHROMATOGR.; ISSN 0148-3919; USA; DA. 1981; VOL. 4; NO 9; PP. 1587-1600; BIBL. 16 REF.Article

CYSTINE DEPLETION OF CISTINOTIC TISSUES BY PHOSPHOCYSTEAMINE (WR 638)THOENE JG; LEMONS R.1980; J. PEDIATR.; USA; DA. 1980; VOL. 96; NO 6; PP. 1043-1044; BIBL. 9 REF.Article

MODULATION IN THE INTRACELLULAR CYSTINE CONTENT OF CYSTINOTIC FIBROBLASTS BY EXTRACELLULAR ALBUMINTHOENE JG; LEMONS R.1980; PEDIATR. RES.; USA; DA. 1980; VOL. 14; NO 6; PP. 785-787; BIBL. 18 REF.Article

COMPARISON OF EXCHANGE TRANSFUSION, PERITONEAL DIALYSIS, AND HEMODIALYSIS FOR THE TREATMENT OF HYPERAMMONEMIA IN AN ANURIC NEWBORN INFANTDONN SM; SWARTZ RD; THOENE JG et al.1979; J. PEDIATR.; USA; DA. 1979; VOL. 95; NO 1; PP. 67-70; BIBL. 10 REF.Article

IMPAIRED INTESTINAL ABSORPTION OF BIOTIN IN JUVENILE MULTIPLE CARBOXYLASE DEFICIENCYTHOENE JG; LEMONS R; BAKER H et al.1983; NEW ENGLAND JOURNAL OF MEDICINE; ISSN 0028-4793; USA; DA. 1983; VOL. 308; NO 11; PP. 639-642; BIBL. 13 REF.Article

CYSTINOSIS. INTRACELLULAR CYSTINE DEPLETION BY AMINOTHIOLS IN VITRO AND IN VIVO.THOENE JG; OSHIMA RG; CRAWHALL JC et al.1976; J. CLIN. INVEST.; U.S.A.; DA. 1976; VOL. 58; NO 1; PP. 180-189; BIBL. 38 REF.Article

A SIMPLE METHOD FOR DETERMINATION OF PLASMA AND URINARY BIOTINSANGHVI RS; LEMONS RM; BAKER H et al.1982; CLIN. CHIM. ACTA; ISSN 0009-8981; NLD; DA. 1982; VOL. 124; NO 1; PP. 85-90; BIBL. 15 REF.Article

ADVERSE REACTIONS TO ORAL CYSTEAMINE USE IN NEPHRAPATHIC CYSTINOSISCORDEN BJ; SCHULMAN JD; SCHNEIDER JA et al.1981; DEV. PHARMACOL. THER.; ISSN 0379-8305; CHE; DA. 1981; VOL. 3; NO 1; PP. 25-30; BIBL. 7 REF.Article

INEFFECTIVENESS OF ASCORBIC ACID THERAPY IN NEPHROPATHIC CYSTINOSISSCHNEIDER JA; SCHLESSELMAN JJ; MENDOZA SA et al.1979; NEW ENGL. J. MED.; USA; DA. 1979; VOL. 300; NO 14; PP. 756-759; BIBL. 24 REF.Article