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BETA -HYDROXYISOBUTYRYL COENZYME A DEACYLASE DEFICIENCY: A DEFECT IN VALINE METABOLISM ASSOCIATED WITH PHYSICAL MALFORMATIONSBROWN GK; HUNT SM; SCHOLEM R et al.1982; PEDIATRICS (EVANSTON); ISSN 0031-4005; USA; DA. 1982; VOL. 70; NO 4; PP. 532-538; BIBL. 19 REF.Article

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