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ABSENT PHENYLALANINE HYDROXYLASE ACTIVITY WITHOUT PHENYLKETONURIAYUDKOFF M; SEGAL S.1980; EUROP. J. PEDIATR.; DEU; DA. 1980; VOL. 134; NO 1; PP. 85-86; BIBL. 8 REF.Article

A MODEL FOR DETERMINATION OF TOTAL BODY PROTEIN SYNTHESIS BASED UPON COMPARTMENTAL ANALYSIS OF THE PLASMA (15N) GLYCINE DECAY CURVENISSIM I; YUDKOFF M; SEGAL S et al.1983; METABOLISM, CLINICAL AND EXPERIMENTAL; ISSN 0026-0495; USA; DA. 1983; VOL. 32; NO 7; PP. 646-653; BIBL. 28 REF.Article

EFFECTS OF CYSTEAMINE THERAPY IN NEPHROPATHIC CYSTINOSISYUDKOFF M; FOREMAN JW; SEGAL S et al.1981; N. ENGL. J. MED.; ISSN 0028-4793; USA; DA. 1981; VOL. 304; NO 3; PP. 141-145; BIBL. 35 REF.Article

ERRORS OF CARBOHYDRATE METABOLISM IN INFANTS AND CHILDREN. A SURVEYYUDKOFF M; COHN RM; SEGAL S et al.1978; CLIN. PEDIATR.; USA; DA. 1978; VOL. 17; NO 11; PP. 820-828; BIBL. 3 REF.Article

DETERMINATION OF (AMIDE-15N) GLUTAMINE IN PLASMA WITH GAS CHROMATOGRAPHY-MASS SPECTROMETRYYUDKOFF M; MISSIM I; SEGAL S et al.1982; CLIN. CHIM. ACTA; ISSN 0009-8981; NLD; DA. 1982; VOL. 118; NO 2-3; PP. 159-166; BIBL. 12 REF.Article

CIRCULATING CRYOGLOBULINS IN NEPHROPATHIC CYSTINOSISFOREMAN JW; YUDKOFF M; YANG L et al.1981; J. PEDIATR.; ISSN 0022-3476; USA; DA. 1981; VOL. 98; NO 3; PP. 432-433; BIBL. 7 REF.Article

Gas chromatographic-mass spectrometric determination of isotopic enrichment of 6-15NH2 in adenine nucleotidesLEWIS, S; YUDKOFF, M.Analytical biochemistry. 1985, Vol 145, Num 2, pp 354-361, issn 0003-2697Article

GAS CHROMATOGRAPHY-MASS SPECTROMETRY DETERMINATION OF (15N) AMMONIA ENRICHMENT IN BLOOD AND URINENISSIM I; YUDKOFF M; YANG W et al.1981; ANAL. BIOCHEM.; ISSN 0003-2697; USA; DA. 1981; VOL. 114; NO 1; PP. 125-130; BIBL. 16 REF.Article

NIEMANN-PICK DISEASE TYPE B: PRENATAL DIAGNOSIS AND ENZYMATIC AND CHEMICAL STUDIES ON FETAL BRAIN AND LIVERWENGER DA; KUDOH T; SATTLER M et al.1981; AM. J. HUM. GENET.; ISSN 0002-9297; USA; DA. 1981; VOL. 33; NO 3; PP. 337-344; BIBL. 18 REF.Article

GLYCINE THERAPY IN ISOVALERIC ACIDEMIAYUDKOFF M; COHN RM; PUSCHAK R et al.1978; J. PEDIATR.; USA; DA. 1978; VOL. 92; NO 5; PP. 813-817; BIBL. 17 REF.Article

PHENYLALANINE-TYROSINE DEFICIENCY SYNDROME AS A COMPLICATION OF THE MANAGEMENT OF HEREDITARY TYROSINEMIA.COHN RM; YUDKOFF M; YOST B et al.1977; AMER. J. CLIN. NUTRIT.; U.S.A.; DA. 1977; VOL. 30; NO 2; PP. 209-214; BIBL. 1 P. 1/2Article

ORNITHINE TRANSCARBAMYLASE DEFICIENCY IN A BOY WITH NORMAL DEVELOPMENTYUDKOFF M; YANG W; SNODGRASS PJ et al.1980; J. PEDIATR.; USA; DA. 1980; VOL. 96; NO 3 PART. 1; PP. 441-443; BIBL. 10 REF.Article

ON THE CLINICAL SIGNIFICANCE OF THE PLASMA ALPHA -AMINO-N-BUTYRIC ACID: LEUCINE RATIOYUDKOFF M; BLAZER YOST B; COHN R et al.1979; AMER. J. CLIN. NUTRIT.; USA; DA. 1979; VOL. 32; NO 2; PP. 282-285; BIBL. 15 REF.Article

THE ONTOGENY OF SUGAR TRANSPORT IN KIDNEYROTH KS; SHING MEI HWANG; YUDKOFF M et al.1978; PEDIATR. RES.; USA; DA. 1978; VOL. 12; NO 12; PP. 1127-1131; BIBL. 25 REF.Article

CYSTEAMINE INHIBITION OF (15N)-GLYCINE TURNOVER IN CYSTINOSIS AND OF THE GLYCINE CLEAVAGE SYSTEM IN VITROYUDKOFF M; NISSIM I; SCHNEIDER A et al.1981; METAB., CLIN. EXP.; ISSN 0026-0495; USA; DA. 1981; VOL. 30; NO 11; PP. 1096-1103; BIBL. 42 REF.Article

RAPID GAS CHROMATOGRAPHIC-MASS SPECTROMETRIC ANALYSIS OF (15N) UREA: APPLICATION TO HUMAN METABOLIC STUDIESNISSIM I; YUDKOFF M; YANG W et al.1981; CLIN. CHIM. ACTA; ISSN 0009-8981; NLD; DA. 1981; VOL. 109; NO 3; PP. 295-304; BIBL. 20 REF.Article

ACIDOSIS ASSOCIATED WITH DIETOTHERAPY OF MAPLE SYRUP URINE DISEASEFOREMAN JW; YUDKOFF M; BERRY G et al.1980; J. PEDIATR.; USA; DA. 1980; VOL. 96; NO 1; PP. 62-64; BIBL. 8 REF.Article

ON THE TRANSPORT OF SUGARS AND AMINO ACIDS BY NEWBORN KIDNEY: USE OF ISOLATED PROXIMAL TUBULE.ROTH KS; HWANG SM; YUDKOFF M et al.1976; LIFE SCI.; G.B.; DA. 1976; VOL. 18; NO 10; PP. 1125-1129; BIBL. 15 REF.Article

Relative role of the glutaminase, glutamate dehydrogenase, and AMP-deaminase pathways in hepatic ureagenesis : studies with 15NNISSIM, I; NISSIM, I et al.CATTANO, C; NISSIM, I; NISSIM, I et al.Archives of biochemistry and biophysics (Print). 1992, Vol 292, Num 2, pp 393-401, issn 0003-9861Article

Effects of conceptual age and dietary intake on protein metabolism in premature infantsNISSIM, I; YUDKOFF, M; PEREIRA, G et al.Journal of pediatric gastroenterology and nutrition. 1983, Vol 2, Num 3, pp 507-516, issn 0277-2116Article

Urinary excretion of dimethylarginines in premature infantsYUDKOFF, M; NISSIM, I; PEREIRA, G et al.Biochemical medicine. 1984, Vol 32, Num 2, pp 242-251, issn 0006-2944Article

Metabolic fate of glutamate carbon in rat renal tubules: studies with 13C nuclear magnetic resonance and gas chromatography-mass spectrometryNISSIM, I; YUDKOFF, M; SEGAL, S et al.Biochemical journal (London. 1906). 1987, Vol 241, Num 2, pp 361-370, issn 0006-2936Article

Nitrogen sources for renal ammoniagenesis: study with 15N amino acidITZHAK NISSIM; YUDKOFF, M; SEGAL, S et al.American journal of physiology. Renal, fluid and electrolyte physiology. 1986, Vol 20, Num 6, pp F995-F1002, issn 0363-6127Article

LATE-ONSET NONKETOTIC HYPERGLYCINEMIA AND SPINOCEREBELLAR DEGENERATIONSTEIMAN GS; YUDKOFF M; BERMAN PH et al.1979; J. PEDIATR.; USA; DA. 1979; VOL. 94; NO 6; PP. 907-911; BIBL. 19 REF.Article

Brain metabolism of branched-chain amino acidsYUDKOFF, M.Glia (New York, NY. Print). 1997, Vol 21, Num 1, pp 92-98, issn 0894-1491Article

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