Pascal and Francis Bibliographic Databases

Help

Search results

Your search

kw.\*:(%22SPHINGOLIPIDOSE HEREDITAIRE GAUCHER%22)

Filter

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Document Type [dt]

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Publication Year[py]

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Discipline (document) [di]

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Language

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Author Country

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Origin

A-Z Z-A Frequency ↓ Frequency ↑
Export in CSV

Results 1 to 25 of 90473

  • Page / 3619
Export

Selection :

  • and

IDENTIFICATION OF GLUCOSYL SPHINGOSINE FROM GAUCHER'S SPLEEN BY GAS CHROMATOGRAPHY-ELECTRON IMPACT AND GC-CHEMICAL IONIZATION MASS SPECTROMETRY.OSHIMA M.1976; J. BIOCHEM.; JAP.; DA. 1976; VOL. 80; NO 1; PP. 53-59; BIBL. 20 REF.Article

INCREASED CEREBROSIDE CONCENTRATION IN PLASMA AND ERYTHROCYTES IN GAUCHER DISEASE: SIGNIFICANT DIFFERENCES BETWEEN TYPE I AND TYPE IIINILSSON O; HAKANSSON G; DREBORG S et al.1982; CLINICAL GENETICS; ISSN 0009-9163; DNK; DA. 1982; VOL. 22; NO 5; PP. 274-279; BIBL. 19 REF.Article

ISOLATION AND CHARACTERIZATION OF A TARTRATE-SENSITIVE SPLENIC ACID PHOSPHATASE IN GAUCHER'S DISEASEROBINSON DB; GLEW RH.1980; ARCH. BIOCHEM. BIOPHYS.; ISSN 0003-9861; USA; DA. 1980; VOL. 205; NO 1; PP. 156-168; BIBL. 33 REF.Article

A MODIFIED METHOD FOR THE IDENTIFICATION OF HETEROZYGOTES FOR GAUCHER'S DISEASE USING DIFFERENTIAL THERMAL INACTIVATIONGOODMAN C; O'BRIEN JS.1980; CLIN. GENET.; ISSN 0009-9163; DNK; DA. 1980; VOL. 18; NO 3; PP. 226-231; BIBL. 16 REF.Article

MORBUS GAUCHER. EINE SYNOPSIS. = MALADIE DE GAUCHER. UNE REVUERICKEN KH.1976; MED. WELT; DTSCH.; DA. 1976; VOL. 27; NO 43; PP. 2065-2069; BIBL. 15 REF.Article

THE SURFACE ULTRASTRUCTURE OF GAUCHER CELLSMEIRDJALDETTI; FISHMAN P; BESSLER H et al.1979; AMER. J. CLIN. PATHOL.; USA; DA. 1979; VOL. 71; NO 2; PP. 146-150; BIBL. 14 REF.Article

TARTRATE-RESISTANT ACID PHOSPHATASE-POSITIVE GAUCHER CELLSWOODRUFF CM; SCHUMACHER HR; BILAK MC et al.1979; AMER. J. CLIN. PATHOL.; USA; DA. 1979; VOL. 71; NO 3; PP. 361-362; BIBL. 5 REF.Article

ENHANCED MACROPHAGE UPTAKE OF SYNTHETICALLY GLYCOSYLATED HUMAN PLACENTA BETA -GLUCOCEREBROSIDASEDOEBBER TW; WU MS; BUGIANESI RL et al.1982; J. BIOL. CHEM.; ISSN 0021-9258; USA; DA. 1982; VOL. 257; NO 5; PP. 2193-2199; BIBL. 37 REF.Article

MUTATIONS OF GLUCOCEREBROSIDASE: DISCRIMINATION OF NEUROLOGIC AND NON-NEUROLOGIC PHENOTYPES OF GAUCHER DISEASEGINNS EI; BRADY RO; PIRRUCCELLO S et al.1982; PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA. BIOLOGICAL SCIENCES; ISSN 0273-1134; USA; DA. 1982; VOL. 79; NO 18; PP. 5607-5610; BIBL. 36 REF.Article

LIVER ABNORMALITIES IN PATIENTS WITH GAUCHER'S DISEASEJAMES SP; STROMEYER FW; CHANG C et al.1981; GASTROENTEROLOGY; ISSN 0016-5085; USA; DA. 1981; VOL. 80; NO 1; PP. 126-133; BIBL. 20 REF.Article

MORBO DI GAUCHER FAMILIARE DELL' ADULTO = MALADIE DE GAUCHER FAMILIALE DE L'ADULTEGIORDANO F; GIARDINI R; BUSCEMI A et al.1979; PATHOLOGICA; ITA; DA. 1979; VOL. 71; NO 1016; PP. 877-883; ABS. ENG; BIBL. 12 REF.Article

PERIPHERAL CRYOGLOBULINEMIC NEUROPATHY IN A PATIENT WITH GAUCHER'S DISEASE.BENJAMIN D; DOUER D; PICK AI et al.1978; ACTA HAEMATOL.; CHE; DA. 1978; VOL. 60; NO 2; PP. 117-121; BIBL. 21 REF.Article

ETUDES CLINIQUES ET HISTOPATHOLOGIQUES SUR UN CAS DE FORME JUVENILE DE MALADIE DE GAUCHERUENO H; UENO S; KAJITANI T et al.1977; FOLIA OPHTHALMOL. JAP.; JAP.; DA. 1977; VOL. 28; NO 1; PP. 225-232; ABS. ANGL.; BIBL. 14 REF.Article

HEPATIC CALCIFICATIONS IN A PATIENT WITH GAUCHER'S DISEASESTONE R; BENSON J; TRONIC B et al.1982; AM. J. GASTROENTEROL.; ISSN 0002-9270; USA; DA. 1982; VOL. 77; NO 2; PP. 95-98; BIBL. 9 REF.Article

ENZYME REPLACEMENT THERAPY IN GAUCHER'S AND FABRY'S DISEASE.PENTCHEV PG.1977; ANN. CLIN. LAB. SCI.; U.S.A.; DA. 1977; VOL. 7; NO 3; PP. 251-253; BIBL. 5 REF.Article

HEMATOLOGICAL FINDINGS IN THE NORRBOTTNIAN TYPE OF GAUCHER DISEASETIBBLIN E; ST DREBORG; ERIKSON A et al.1982; EUROPEAN JOURNAL OF PEDIATRICS; ISSN 0340-6199; DEU; DA. 1982; VOL. 139; NO 3; PP. 187-191; BIBL. 19 REF.Article

THE OCCURRENCE OF PSYCHOSINE AND OTHER GLYCOLIPIDS IN SPLEEN AND LIVER FROM THE THREE MAJOR TYPES OF GAUCHER'S DISEASENILSSON O; MANSSON JE; HAKANSSON G et al.1982; BIOCHIM. BIOPHYS. ACTA; ISSN 0006-3002; NLD; DA. 1982; VOL. 712; NO 3; PP. 453-463; BIBL. 33 REF.Article

ACCELERATED SKELETAL DETERIORATION AFTER SPLENECTOMY IN GAUCHER TYPE 1 DISEASEROSE JS; GRABOWSKI GA; BARNETT SH et al.1982; AMERICAN JOURNAL OF ROENTGENOLOGY; ISSN 0092-5381; USA; DA. 1982; VOL. 139; NO 6; PP. 1202-1204; BIBL. 19 REF.Article

NIEMANN-PICK DISEASE, TYPE C: EVIDENCE FOR THE DEFICIENCY OF AN ACTIVATING FACTOR STIMULATING SPHINGOMYELIN AND GLUCOCEREBROSIDE DEGRADATIONCHRISTOMANOU H.1980; HOPPE-SEYLER Z. PHYSIOL. CHEM.; ISSN 0018-4888; DEU; DA. 1980; VOL. 361; NO 10; PP. 1489-1502; ABS. GER; BIBL. 40 REF.Article

BRAIN GLYCOLIPIDS IN INFANTILE GAUCHER'S DISEASE.SUDO M.1977; J. NEUROCHEM.; G.B.; DA. 1977; VOL. 29; NO 2; PP. 379-381; BIBL. 21 REF.Article

ASSOCIATION OF HODGKIN DISEASE AND GAUCHER DISEASE = ASSOCIATION D'UNE MALADIE D'HODGKIN ET D'UNE MALADIE DE GAUCHERSHARER LR; BARONDESS JA; SILVER RT et al.1974; ARCH. PATHOL.; U.S.A.; DA. 1974; VOL. 98; NO 6; PP. 376-378; BIBL. 12REF.Article

ENZYMOLOGICAL APPROACHES TO THE LIPIDOSES.BRADY RO.1977; ANN. CLIN. LAB. SCI.; U.S.A.; DA. 1977; VOL. 7; NO 2; PP. 105-112; BIBL. 2 P.Article

SERUM FERRITIN CONCENTRATION IN GAUCHER'S DISEASEMORGAN MAM; HOFFBRAND AV; LAULICHT M et al.1983; BRITISH MEDICAL JOURNAL; ISSN 0007-1447; GBR; DA. 1983; VOL. 286; NO 6381; PP. 1864; BIBL. 5 REF.Article

ACQUIRED GAUCHER'S CELLS IN HODGKIN'S DISEASEKYUNG SHIK LEE; TOBIN MS; CHEN KTK et al.1982; AM. J. MED.; ISSN 0002-9343; USA; DA. 1982; VOL. 73; NO 2; PP. 290-294; BIBL. 18 REF.Article

GAUCHER DISEASE. III: SUBSTRATE SPECIFITY OF GLUCOCE-REBROSIDASE AND THE USE OF NONLABELED NATURAL SUBSTRATES FOR THE INVESTIGATION OF PATIENTSCHOY FYM; DAVIDSON RG.1980; AM. J. HUM. GENET.; ISSN 0002-9297; USA; DA. 1980; VOL. 32; NO 5; PP. 670-678; BIBL. 37 REF.Article

  • Page / 3619