Disturbance of cultured rat neuronal network activity depends on concentration and ratio of leucine and α-ketoisocaproate: Implication for acute encephalopathy of maple syrup urine disease
- Auteur
- GÖRTZ, Philipp1 ; KOLLER, Hubertus1 ; SCHWAHN, Bernd2 ; WENDEL, Udo2 ; SIEBLER, Mario1
[1] Department of Neurology, Heinrich-Heine-University, Düsseldorf, Germany
[2] Department of Pediatrics, Heinrich-Heine-University, Düsseldorf, Germany - Source
Pediatric research. 2003, Vol 53, Num 2, pp 320-324, 5 p ; ref : 20 ref
- CODEN
- PEREBL
- ISSN
- 0031-3998
- Domaine scientifique
- Genetics; Pediatrics
- Editeur
- Lippincott Williams & Wilkins, Hagerstown, MD
- Pays de publication
- United States
- Type de document
- Article
- Langue
- English
- Mot clé (fr)
- Activité biologique Aminoacide Animal Concentration Culture cellulaire Dépolarisation Encéphalopathie Enzymopathie GABA In vitro Leucine Leucinose Neurone Pathogénie Physiopathologie Potentiel action Rat Ratio Synapse Aminoacidopathie Maladie héréditaire Mammalia Métabolisme pathologie Neurotransmetteur Rodentia Système nerveux pathologie Vertebrata
- Mot clé (en)
- Biological activity Aminoacid Animal Concentration Cell culture Depolarization Encephalopathy Enzymopathy GABA In vitro Leucine Leucinosis Neuron Pathogenesis Pathophysiology Action potential Rat Ratio Synapse Aminoacid disorder Genetic disease Mammalia Metabolic diseases Neurotransmitter Rodentia Nervous system diseases Vertebrata
- Mot clé (es)
- Actividad biológica Aminoácido Animal Concentración Cultivo celular Despolarización Encefalopatía Enzimopatía GABA In vitro Leucina Leucinosis Neurona Patogenia Fisiopatología Potencial acción Rata Ratio Sinapsis Aminoacido alteración Enfermedad hereditaria Mammalia Metabolismo patología Neurotransmisor Rodentia Sistema nervioso patología Vertebrata
- Classification
- Pascal
- 002 Sciences biologiques et medicales / 002B Sciences medicales / 002B22 Maladies metaboliques / 002B22D Maladies métaboliques héréditaires et congénitales / 002B22D01 Aminoacidopathies
- Discipline
- Metabolic diseases
- Provenance
- Inist-CNRS
- Base de données
- PASCAL
- Identifiant INIST
- 14497664
Sauf mention contraire ci-dessus, le contenu de cette notice bibliographique peut être utilisé dans le cadre d’une licence CC BY 4.0 Inist-CNRS / Unless otherwise stated above, the content of this bibliographic record may be used under a CC BY 4.0 licence by Inist-CNRS / A menos que se haya señalado antes, el contenido de este registro bibliográfico puede ser utilizado al amparo de una licencia CC BY 4.0 Inist-CNRS
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DOI
10.1203/01.PDR.0000047521.50656.16 
https://dx.doi.org/10.1203/01.PDR.0000047521.50656.16
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